Congenital thrombotic thrombocytopenic purpura associated with unilateral moyamoya disease

Pediatric Nephrology

Volumn 23, Issue 9, 2008, Pages 1555-1558

  Park, Hye Won ^a   Oh, Doyeon ^a   Kim, Namkeun ^a   Cho, Hee Yeon ^b   Moon, Kyung Chul ^c   Chae, Jong Hee ^b   Ahn, Hyo Seop ^b   Choi, Yong ^b   Cheong II, Hae ^b  

^a CHA University   (South Korea)

^b Seoul National University Children's Hospital   (South Korea)

^c Seoul National University Hospital   (South Korea)

Author keywords

ADAMTS13 gene; Congenital thrombotic thrombocytopenic purpura; Moyamoya disease; Von Willebrand factor cleaving protease

Indexed keywords

ANTIHYPERTENSIVE AGENT; CREATININE; FRESH FROZEN PLASMA; HEMOGLOBIN; IMMUNOGLOBULIN; PREDNISONE; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ARM WEAKNESS; ARTICLE; AUTOIMMUNE HEMOLYTIC ANEMIA; BRAIN ANGIOGRAPHY; BRAIN INFARCTION; CASE REPORT; CEREBROVASCULAR ACCIDENT; COMPUTER ASSISTED TOMOGRAPHY; CONGESTIVE CARDIOMYOPATHY; CREATININE BLOOD LEVEL; DIFFERENTIAL DIAGNOSIS; DISEASE ASSOCIATION; DISEASE EXACERBATION; DYSARTHRIA; ERYTHROCYTE TRANSFUSION; EXCHANGE BLOOD TRANSFUSION; FACIAL NERVE PARALYSIS; HEMATURIA; HEMIPARESIS; HEMOLYTIC ANEMIA; HUMAN; HYPERTENSION; KIDNEY BIOPSY; KIDNEY DYSFUNCTION; KOREA; MALE; MIDDLE CEREBRAL ARTERY OCCLUSION; MISSENSE MUTATION; MOYAMOYA DISEASE; MUTATIONAL ANALYSIS; NEWBORN JAUNDICE; NUCLEAR MAGNETIC RESONANCE IMAGING; PLASMA TRANSFUSION; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; PROTEINURIA; SCHOOL CHILD; THROMBOCYTE COUNT; THROMBOCYTE TRANSFUSION; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA;

ADAM PROTEINS; CHILD; HUMANS; MALE; MOYAMOYA DISEASE; MUTATION; PURPURA, THROMBOTIC THROMBOCYTOPENIC;

EID: 47749153345     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-008-0847-5     Document Type: Article

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