Efficacy of plasma therapy in atypical hemolytic uremic syndrome with complement factor H mutations

Pediatric Nephrology

Volumn 23, Issue 8, 2008, Pages 1363-1366

  Lapeyraque, Anne Laure ^a   Wagner, Eric ^a   Phan, Véronique ^a   Clermont, Marie José ^a   Merouani, Aïcha ^a   Frémeaux Bacchi, Véronique ^b   Goodship, Timothy H J ^c   Robitaille, Pierre ^a  

^a UNIVERSITY OF MONTREAL   (Canada)

^b HÔPITAL EUROPÉEN GEORGES POMPIDOU   (France)

^c NEWCASTLE UNIVERSITY   (United Kingdom)

Author keywords

Complement factor H genetics; Complement system proteins; Hemolytic uremic syndrome genetics therapy; Humans; Liver transplantation; Mutation; Plasma therapy

Indexed keywords

ALANINE; COMPLEMENT COMPONENT C3; COMPLEMENT COMPONENT C4; COMPLEMENT FACTOR H; LYSINE; SERINE; VALINE;

ACUTE HEART FAILURE; ARTICLE; BACTEREMIA; CASE REPORT; CATHETER INFECTION; COMPLEMENT BLOOD LEVEL; FEMALE; FEVER; GENE MUTATION; HEMODIALYSIS; HEMOLYTIC UREMIC SYNDROME; HUMAN; INFANT; LONG TERM CARE; PALLOR; PLASMA TRANSFUSION; PLASMAPHERESIS; PRIORITY JOURNAL; RECURRENCE RISK; THERAPY EFFECT; TREATMENT FAILURE; TREATMENT RESPONSE; VOMITING;

COMPLEMENT FACTOR H; FEMALE; HEMOLYTIC-UREMIC SYNDROME; HETEROZYGOTE; HUMANS; INFANT; PLASMA EXCHANGE; POINT MUTATION;

EID: 46949105006     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-008-0803-4     Document Type: Article

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