CLN3p impacts galactosylceramide transport, raft morphology, and lipid content

Pediatric Research

Volumn 63, Issue 6, 2008, Pages 625-631

  Rusyn, Elena ^a   Mousallem, Talal ^a   Persaud Sawin, Dixie Ann ^a   Miller, Sara ^a   Boustany, Rose Mary N ^b  

^a DUKE UNIVERSITY MEDICAL CENTER   (United States)

^b AMERICAN UNIVERSITY OF BEIRUT   (Lebanon)

Author keywords

[No Author keywords available]

Indexed keywords

GALACTOSYLCERAMIDE; GALACTOSYLCERAMIDE SYNTHASE; LIPID TRANSFER PROTEIN; LYSOPHOSPHATIDIC ACID; MUTANT PROTEIN; PROTEIN CLN1; PROTEIN CLN2; PROTEIN CLN3P; PROTEIN CLN6; PROTEIN CLN8; PROTEIN CLN9; SMALL INTERFERING RNA; SPHINGOLIPID; SULFATIDE; SYNTHETASE; UNCLASSIFIED DRUG; CHAPERONE; CLN3 PROTEIN, HUMAN; CLN3 PROTEIN, MOUSE; CLN8 PROTEIN, MOUSE; MEMBRANE LIPID; MEMBRANE PROTEIN;

APOPTOSIS; ARTICLE; CELL GROWTH; CELL VACUOLE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; GOLGI COMPLEX; HUMAN; HUMAN CELL; LIPID COMPOSITION; LIPID RAFT; LIPID TRANSPORT; MORPHOLOGY; NEURONAL CEROID LIPOFUSCINOSIS; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN FUNCTION; PROTEIN LOCALIZATION; STOICHIOMETRY; TRANSMISSION ELECTRON MICROSCOPY; WILD TYPE; ANIMAL; CELL CULTURE; CELL FRACTIONATION; CELL LINE; CELL MEMBRANE; CELL PROLIFERATION; FIBROBLAST; GENETICS; METABOLISM; MOUSE; MOUSE MUTANT; MUTATION; PATHOLOGY; PROTEIN TRANSPORT; ULTRASTRUCTURE;

ANIMALS; APOPTOSIS; CELL LINE; CELL PROLIFERATION; CELLS, CULTURED; ENDOPLASMIC RETICULUM; FIBROBLASTS; GALACTOSYLCERAMIDES; GOLGI APPARATUS; HUMANS; MEMBRANE GLYCOPROTEINS; MEMBRANE LIPIDS; MEMBRANE MICRODOMAINS; MEMBRANE PROTEINS; MICE; MICE, KNOCKOUT; MOLECULAR CHAPERONES; MUTATION; NEURONAL CEROID-LIPOFUSCINOSES; PROTEIN BINDING; PROTEIN TRANSPORT; SUBCELLULAR FRACTIONS; SULFOGLYCOSPHINGOLIPIDS;

EID: 45849149313     PISSN: 00313998     EISSN: 15300447     Source Type: Journal    
DOI: 10.1203/PDR.0b013e31816fdc17     Document Type: Article

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