Short PR interval in the absence of preexcitation: A characteristic finding in a patient with Fabry disease

PACE - Pacing and Clinical Electrophysiology

Volumn 31, Issue 6, 2008, Pages 782-783

  Aryana, Arash ^a   Fifer, Michael A ^a   Ruskin, Jeremy N ^a   Mela, Theofanie ^a  

^a MASSACHUSETTS GENERAL HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

GLYCOSPHINGOLIPID;

ADULT; ARTICLE; CASE REPORT; ECG ABNORMALITY; ELECTROPHYSIOLOGY; FABRY DISEASE; FEMALE; HEART ATRIOVENTRICULAR NODE; HEART CONDUCTION; HEART LEFT VENTRICLE HYPERTROPHY; HEART PREEXCITATION; HIS BUNDLE; HUMAN; PR INTERVAL; PURKINJE CELL; RARE DISEASE; RECURRENT DISEASE; SYNCOPE;

ADULT; ARRHYTHMIAS, CARDIAC; ELECTROCARDIOGRAPHY; FABRY DISEASE; FEMALE; HUMANS;

EID: 44349115553     PISSN: 01478389     EISSN: 15408159     Source Type: Journal    
DOI: 10.1111/j.1540-8159.2008.01088.x     Document Type: Article

References (5)

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2. Frustaci A, Chimenti C, Ricci R, Natale L, Russo MA, Pieroni M, Eng CM, et al. Improvement in cardiac function in the cardiac variant of Fabry's disease with galactose-infusion therapy. N Engl J Med 2001 345 : 25 32.
3. Frustaci A, Chimenti C. Images in cardiovascular medicine. Cryptogenic ventricular arrhythmias and sudden death by Fabry disease: Prominent infiltration of cardiac conduction tissue. Circulation 2007 116 : e350 e351.
4. Pochis WT, Litzow JT, King BG, Kenny D. Electrophysiologic findings in Fabry's disease with a short PR interval. Am J Cardiol 1994 74 : 203 204.
5. Jastrzebski M, Bacior B, Dimitrow PP, Kawecka-Jaszcz K. Electrophysiological study in a patient with Fabry disease and a short PQ interval. Europace 2006 8 : 1045 1047.