Phenotypic identification of platelet-type von Willebrand disease and its discrimination from type 2B von Willebrand disease: A question of 2B or not 2B? A story of nonidentical twins? Or two sides of a multidenominational or multifaceted primary-hemostasis coin?

Seminars in Thrombosis and Hemostasis

Volumn 34, Issue 1, 2008, Pages 113-127

  Favaloro, Emmanuel J ^a  

^a WESTMEAD HOSPITAL   (Australia)

Author keywords

GP1BA; GPIBA; Platelet type VWD; Pseudo VWD; PT VWD; RIPA; Type 2B VWD; von Willebrand disease; von Willebrand factor; VWD; VWF

Indexed keywords

DESMOPRESSIN; GLYCOPROTEIN IB ALPHA; THROMBOCYTE RECEPTOR; VON WILLEBRAND FACTOR;

BLEEDING; DISEASE CLASSIFICATION; DIZYGOTIC TWINS; GENE IDENTIFICATION; GENE INTERACTION; GENE LOCUS; GENE MUTATION; GENETIC COUNSELING; GENETIC DISORDER; GENETIC IDENTIFICATION; GENETIC VARIABILITY; HEMOSTASIS; HUMAN; LABORATORY TEST; PEDIGREE ANALYSIS; PHENOTYPE; PLASMA TRANSFUSION; PLATELET TYPE VON WILLEBRAND DISEASE; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN PROTEIN INTERACTION; REVIEW; THROMBOCYTE; THROMBOCYTE TRANSFUSION; VON WILLEBRAND DISEASE; VON WILLEBRAND DISEASE TYPE 2B;

BLOOD PLATELETS; DIAGNOSIS, DIFFERENTIAL; HEMOSTASIS; HUMANS; MEMBRANE PROTEINS; MUTATION; PHENOTYPE; PLATELET FUNCTION TESTS; PROTEIN BINDING; TERMINOLOGY AS TOPIC; VON WILLEBRAND DISEASE; VON WILLEBRAND FACTOR;

EID: 43149092271     PISSN: 00946176     EISSN: 10989064     Source Type: Journal    
DOI: 10.1055/s-2008-1066019     Document Type: Review

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