Combination of cardiac conduction disease and long QT syndrome caused by mutation T1620K in the cardiac sodium channel

Cardiovascular Research

Volumn 77, Issue 4, 2008, Pages 740-748

  Surber, Ralf ^a   Hensellek, Sabine ^a   Prochnau, Dirk ^a   Werner, Gerald S ^a   Benndorf, Klaus ^a   Figulla, Hans R ^a   Zimmer, Thomas ^a  

^a FRIEDRICH SCHILLER UNIVERSITY JENA   (Germany)

Author keywords

Conduction block; Ion channels; Long QT syndrome; Na+ channels

Indexed keywords

LIDOCAINE; LYSINE; SODIUM CHANNEL; THREONINE; VOLTAGE GATED SODIUM CHANNEL;

ADOLESCENT; ADULT; ARTICLE; BRUGADA SYNDROME; CAUCASIAN; CELL STRAIN HEK293; COMORBIDITY; CONTROLLED STUDY; EMBRYO; EXON; FEMALE; GENE MUTATION; HEART BUNDLE BRANCH BLOCK; HEART MUSCLE CONDUCTION DISTURBANCE; HUMAN; HUMAN CELL; HYPERPOLARIZATION; LONG QT SYNDROME; MALE; MEMBRANE STEADY POTENTIAL; MOLECULAR DYNAMICS; MUTANT; MUTATIONAL ANALYSIS; OOCYTE; PRIORITY JOURNAL; PROTEIN FUNCTION; SCHOOL CHILD; SODIUM CHANNELOPATHY; SODIUM CURRENT; STEADY STATE; SUDDEN DEATH; SYNCOPE; WILD TYPE; XENOPUS;

ACTION POTENTIALS; ADOLESCENT; ADULT; AJMALINE; ANIMALS; ANTI-ARRHYTHMIA AGENTS; BUNDLE-BRANCH BLOCK; CELL LINE; CHILD; DEATH, SUDDEN, CARDIAC; DNA MUTATIONAL ANALYSIS; ELECTROCARDIOGRAPHY; FEMALE; GENE TRANSFER TECHNIQUES; GENETIC PREDISPOSITION TO DISEASE; HUMANS; KINETICS; LIDOCAINE; LONG QT SYNDROME; LYSINE; MALE; MUSCLE PROTEINS; MUTATION; MYOCARDIUM; PATCH-CLAMP TECHNIQUES; PEDIGREE; SODIUM; SODIUM CHANNELS; SYNCOPE; THREONINE; XENOPUS LAEVIS;

EID: 39749187283     PISSN: 00086363     EISSN: 17553245     Source Type: Journal    
DOI: 10.1093/cvr/cvm096     Document Type: Article

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