Hexacosanoic and docosanoic acids plasma levels in patients with cerebral childhood and asymptomatic X-linked adrenoleukodystrophy: Lorenzo's oil effect

Metabolic Brain Disease

Volumn 23, Issue 1, 2008, Pages 43-49

  Deon, Marion ^c   Garcia, Mariana Pires ^a   Sitta, Angela ^c   Barschak, Alethéa G ^c   Coelho, Daniella M ^b   Schimit, Graziela O ^b   Pigatto, Maiara ^a   Jardim, Laura B ^b   Wajner, Moacir ^b,c   Giugliani, Roberto ^b,c   Vargas, Carmen R ^a,b,c  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

^c Instituto de Ciencias Biologicas e da Saude Pontifical Catholic University of Minas Gerais   (Brazil)

Author keywords

Adrenoleukodystrophy; Hexacosanoic acid; Lorenzo's Oil; Peroxisomes; Tetracosanoic acid; Very long chain fatty acids

Indexed keywords

BEHENIC ACID; HEXACOSANOIC ACID; LONG CHAIN FATTY ACID; LORENZO OIL; UNCLASSIFIED DRUG; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ARTICLE; CHILD; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; DIET RESTRICTION; DISEASE COURSE; FATTY ACID BLOOD LEVEL; HUMAN; THERAPY EFFECT; TREATMENT OUTCOME; TREATMENT RESPONSE; X CHROMOSOME LINKED DISORDER;

EID: 39149135565     PISSN: 08857490     EISSN: None     Source Type: Journal    
DOI: 10.1007/s11011-007-9079-9     Document Type: Article

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