Thrombocytopenia and severe hyperbilirubinemia in the neonatal period secondary to congenital thrombotic thrombocytopenic purpura and ADAMTS13 deficiency

Journal of Pediatric Hematology/Oncology

Volumn 26, Issue 8, 2004, Pages 535-538

  Schiff, Deborah E ^a   Roberts, William D ^a   Willert, Jennifer ^a   Tsai, Han Mou ^b  

^a RADY CHILDREN'S HOSPITAL   (United States)

^b ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

Author keywords

ADAMTS13 deficiency; Congenital hemolytic anemia; Congenital thrombotic thrombocytopenic purpura; Hyperbilirubinemia; Thrombocytopenia

Indexed keywords

FRESH FROZEN PLASMA; IMMUNOGLOBULIN; LACTATE DEHYDROGENASE; PREDNISONE; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ADAMTS13 DEFICIENCY; ARTICLE; AUTOIMMUNE HEMOLYTIC ANEMIA; BLOOD SMEAR; CASE REPORT; CLINICAL FEATURE; COOMBS TEST; DIFFERENTIAL DIAGNOSIS; DISEASE COURSE; ENZYME DEFICIENCY; FEMALE; HEMOLYTIC ANEMIA; HUMAN; HYPERBILIRUBINEMIA; LACTATE DEHYDROGENASE BLOOD LEVEL; MALE; NEWBORN PERIOD; PLASMA TRANSFUSION; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA;

ADAM PROTEINS; ANEMIA; CHILD, PRESCHOOL; DIAGNOSIS, DIFFERENTIAL; FEMALE; HUMANS; HYPERBILIRUBINEMIA; INFANT; INFANT, NEWBORN; MALE; METALLOENDOPEPTIDASES; PEDIGREE; PURPURA, THROMBOTIC THROMBOCYTOPENIC; THROMBOCYTOPENIA;

EID: 3843152878     PISSN: 10774114     EISSN: None     Source Type: Journal    
DOI: 10.1097/01.mph.0000135284.85292.2c     Document Type: Article

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