Documented transient third-degree atrioventricular block and asystole in a child with familial dysautonomia

Pediatric Cardiology

Volumn 29, Issue 1, 2008, Pages 202-204

  Rotstein, Amichay ^a,b   Charrow, Joel ^c   Deal, Barbara J ^c  

^a SCHNEIDER CHILDREN S MEDICAL CENTER OF ISRAEL   (Israel)

^b TEL AVIV UNIVERSITY   (Israel)

^c NORTHWESTERN UNIVERSITY   (United States)

Author keywords

Arrhythmia; Familial dysautonomia; Pacemaker

Indexed keywords

ALPHA TOCOTRIENOL; CHLORAL HYDRATE; CLONIDINE; DIAZEPAM; FAMOTIDINE; FLUDROCORTISONE ACETATE; FLUTICASONE PROPIONATE; VALPROIC ACID;

ANAMNESIS; ARTICLE; ARTIFICIAL HEART PACEMAKER; ASYSTOLE; ATRIOVENTRICULAR BLOCK; AUTONOMIC NEUROPATHY; CARDIOVASCULAR RISK; CASE REPORT; COMPLETE HEART BLOCK; CUTIS MARMORATA TELANGIECTATICA CONGENITA; DISEASE COURSE; DISEASE PREDISPOSITION; DYSAUTONOMIA; ELECTROCARDIOGRAM; HEART PALPITATION; HOLTER MONITORING; HUMAN; HYPERTENSION; LABORATORY TEST; MALE; PHYSICAL EXAMINATION; SALIVATION; SCHOOL CHILD; SWEATING; SYMPTOM; TREATMENT OUTCOME; VOMITING;

ATRIOVENTRICULAR BLOCK; CHILD; DYSAUTONOMIA, FAMILIAL; ELECTROCARDIOGRAPHY; ELECTROCARDIOGRAPHY, AMBULATORY; HEART ARREST; HUMANS; MALE;

EID: 38349143929     PISSN: 01720643     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00246-007-9057-3     Document Type: Article

References (12)

1. Axelrod FB (2004) Familial dysautonomia. Muscle Nerve 29:352-363
2. Axelrod FB, Goldberg JD, Ye XY, Maayan CH (2002) Survival in familial dysautonomia:impact of early intervention. J Pediatr 141:518-523
3. Axelrod FB, Putman D, Berlin D, Rutkowski M (1977) Electrocardiographic measures and heart rate variability in patients with familial dysautonomia. Cardiology 88:133-140
4. Bartoletti A (2005) Cardiac pacing in patients with familial dysautonomia-there is nothing simple about sudden death. Clin Auton Res 15:6-9
5. Glickstein JS, Axelrod FB, Friedman D (1999) Electrocardiographic abnormalities in familial dysautonomia: an indicator of cardiac autonomic dysfunction. Clin Auton Res 9:109-112
6. Glickstein JS, Schwartzman D, Friedman D, Rutkowski M, Axelrod FB (1993) Abnormalities of the corrected QT interval in familial dysautonomia: an indicator of autonomic dysfunction. J Pediatr 122:925-928
7. Gold-Von Simson G, Rutkowski M, Berlin D, Axelrod FB (2005) Pacemakers in patients with familial dysautonomia-a review of experience with 20 patients. Clin Auton Res 15:15-20
8. Hillz MJ, Kolodny E, Neuner E, Stemper B, Axelrod FB (1998) Highly abnormal thermotests in familial dysautonomia suggest increased cardiac autonomic risk. J Neurol Neurosurg Psychiatry 65:338-343
9. Michaelsson M, Jonzon A, Riesenfeld T (1995) Isolated congenital complete atrioventricular block in adult life: a prospective study. Circulation 92:442-449
10. Rutkowski M, Axelrod FB, Danilowitcz D (1992) Transient third-degree atrioventricular block in a 4-year old child with familial dysautonomia. Pediatr Cardiol 13:184-186
11. Ziegler MG, Lake CR, Kopin IJ (1976) Deficient sympathetic nervous response in familial dysautonomia. N Engl J Med 294:630-634
12. ACC/AHA/NASPE (2002) 2002 guideline update for implantation of cardiac pacemakers and antiarrhythmia devices:summary article: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (ACC/AHA/NASPE Committee to Update the 1998 Pacemaker Guidelines). Circulation 106:2145-2161