-
2
-
-
0027332116
-
Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins
-
Pan K.M., Baldwin M., Nguyen J., Gasset M., Serban A., Groth D., Mehlhorn I., Huang Z., Fletterick R.J., Cohen F.E., et al. Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins. Proc. Natl. Acad. Sci. USA 90 (1993) 10962-10966
-
(1993)
Proc. Natl. Acad. Sci. USA
, vol.90
, pp. 10962-10966
-
-
Pan, K.M.1
Baldwin, M.2
Nguyen, J.3
Gasset, M.4
Serban, A.5
Groth, D.6
Mehlhorn, I.7
Huang, Z.8
Fletterick, R.J.9
Cohen, F.E.10
-
3
-
-
2342472104
-
Prion protein (PrPc) immunocytochemistry and expression of the green fluorescent protein reporter gene under control of the bovine PrP gene promoter in the mouse brain
-
Bailly Y., Haeberle A.M., Blanquet-Grossard F., Chasserot-Golaz S., Grant N., Schulze T., Bombarde G., Grassi J., Cesbron J.Y., and Lemaire-Vieille C. Prion protein (PrPc) immunocytochemistry and expression of the green fluorescent protein reporter gene under control of the bovine PrP gene promoter in the mouse brain. J. Comp. Neurol. 473 (2004) 244-269
-
(2004)
J. Comp. Neurol.
, vol.473
, pp. 244-269
-
-
Bailly, Y.1
Haeberle, A.M.2
Blanquet-Grossard, F.3
Chasserot-Golaz, S.4
Grant, N.5
Schulze, T.6
Bombarde, G.7
Grassi, J.8
Cesbron, J.Y.9
Lemaire-Vieille, C.10
-
4
-
-
34249936265
-
The cellular prion protein (PrP(C)): its physiological function and role in disease
-
Westergard L., Christensen H.M., and Harris D.A. The cellular prion protein (PrP(C)): its physiological function and role in disease. Biochim. Biophys. Acta 1772 (2007) 629-644
-
(2007)
Biochim. Biophys. Acta
, vol.1772
, pp. 629-644
-
-
Westergard, L.1
Christensen, H.M.2
Harris, D.A.3
-
5
-
-
0026600865
-
Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein
-
Bueler H., Fischer M., Lang Y., Bluethmann H., Lipp H.P., DeArmond S.J., Prusiner S.B., Aguet M., and Weissmann C. Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein. Nature 356 (1992) 577-582
-
(1992)
Nature
, vol.356
, pp. 577-582
-
-
Bueler, H.1
Fischer, M.2
Lang, Y.3
Bluethmann, H.4
Lipp, H.P.5
DeArmond, S.J.6
Prusiner, S.B.7
Aguet, M.8
Weissmann, C.9
-
6
-
-
15844421385
-
Altered circadian activity rhythms and sleep in mice devoid of prion protein
-
Tobler I., Gaus S.E., Deboer T., Achermann P., Fischer M., Rulicke T., Moser M., Oesch B., McBride P.A., and Manson J.C. Altered circadian activity rhythms and sleep in mice devoid of prion protein. Nature 380 (1996) 639-642
-
(1996)
Nature
, vol.380
, pp. 639-642
-
-
Tobler, I.1
Gaus, S.E.2
Deboer, T.3
Achermann, P.4
Fischer, M.5
Rulicke, T.6
Moser, M.7
Oesch, B.8
McBride, P.A.9
Manson, J.C.10
-
7
-
-
13344282734
-
Loss of cerebellar Purkinje cells in aged mice homozygous for a disrupted PrP gene
-
Sakaguchi S., Katamine S., Nishida N., Moriuchi R., Shigematsu K., Sugimoto T., Nakatani A., Kataoka Y., Houtani T., Shirabe S., Okada H., Hasegawa S., Miyamoto T., and Noda T. Loss of cerebellar Purkinje cells in aged mice homozygous for a disrupted PrP gene. Nature 380 (1996) 528-531
-
(1996)
Nature
, vol.380
, pp. 528-531
-
-
Sakaguchi, S.1
Katamine, S.2
Nishida, N.3
Moriuchi, R.4
Shigematsu, K.5
Sugimoto, T.6
Nakatani, A.7
Kataoka, Y.8
Houtani, T.9
Shirabe, S.10
Okada, H.11
Hasegawa, S.12
Miyamoto, T.13
Noda, T.14
-
8
-
-
0035865398
-
Onset of ataxia and Purkinje cell loss in PrP null mice inversely correlated with Dpl level in brain
-
Rossi D., Cozzio A., Flechsig E., Klein M.A., Rulicke T., Aguzzi A., and Weissmann C. Onset of ataxia and Purkinje cell loss in PrP null mice inversely correlated with Dpl level in brain. EMBO J. 20 (2001) 694-702
-
(2001)
EMBO J.
, vol.20
, pp. 694-702
-
-
Rossi, D.1
Cozzio, A.2
Flechsig, E.3
Klein, M.A.4
Rulicke, T.5
Aguzzi, A.6
Weissmann, C.7
-
9
-
-
0033215478
-
Ataxia in prion protein (PrP)-deficient mice is associated with upregulation of the novel PrP-like protein doppel
-
Moore R.C., Lee I.Y., Silverman G.L., Harrison P.M., Strome R., Heinrich C., Karunaratne A., Pasternak S.H., Chishti M.A., Liang Y., Mastrangelo P., Wang K., Smit A.F., Katamine S., Carlson G.A., Cohen F.E., Prusiner S.B., Melton D.W., Tremblay P., Hood L.E., and Westaway D. Ataxia in prion protein (PrP)-deficient mice is associated with upregulation of the novel PrP-like protein doppel. J. Mol. Biol. 292 (1999) 797-817
-
(1999)
J. Mol. Biol.
, vol.292
, pp. 797-817
-
-
Moore, R.C.1
Lee, I.Y.2
Silverman, G.L.3
Harrison, P.M.4
Strome, R.5
Heinrich, C.6
Karunaratne, A.7
Pasternak, S.H.8
Chishti, M.A.9
Liang, Y.10
Mastrangelo, P.11
Wang, K.12
Smit, A.F.13
Katamine, S.14
Carlson, G.A.15
Cohen, F.E.16
Prusiner, S.B.17
Melton, D.W.18
Tremblay, P.19
Hood, L.E.20
Westaway, D.21
more..
-
10
-
-
0141738255
-
PrP knock-out and PrP transgenic mice in prion research
-
Weissmann C., and Flechsig E. PrP knock-out and PrP transgenic mice in prion research. Br. Med. Bull. 66 (2003) 43-60
-
(2003)
Br. Med. Bull.
, vol.66
, pp. 43-60
-
-
Weissmann, C.1
Flechsig, E.2
-
11
-
-
0141849873
-
Physiological and pathological functions of the prion protein homologue Dpl
-
Behrens A. Physiological and pathological functions of the prion protein homologue Dpl. Br. Med. Bull. 66 (2003) 35-42
-
(2003)
Br. Med. Bull.
, vol.66
, pp. 35-42
-
-
Behrens, A.1
-
12
-
-
0036184716
-
Expression of doppel in the CNS of mice does not modulate transmissible spongiform encephalopathy disease
-
Tuzi N.L., Gall E., Melton D., and Manson J.C. Expression of doppel in the CNS of mice does not modulate transmissible spongiform encephalopathy disease. J. Gen. Virol. 83 (2002) 705-711
-
(2002)
J. Gen. Virol.
, vol.83
, pp. 705-711
-
-
Tuzi, N.L.1
Gall, E.2
Melton, D.3
Manson, J.C.4
-
13
-
-
0036498430
-
Small is not beautiful: antagonizing functions for the prion protein PrP(C) and its homologue Dpl
-
Behrens A., and Aguzzi A. Small is not beautiful: antagonizing functions for the prion protein PrP(C) and its homologue Dpl. Trends Neurosci. 25 (2002) 150-154
-
(2002)
Trends Neurosci.
, vol.25
, pp. 150-154
-
-
Behrens, A.1
Aguzzi, A.2
-
14
-
-
23644449548
-
Influence of the N-terminal domain on the aggregation properties of the prion protein
-
Frankenfield K.N., Powers E.T., and Kelly J.W. Influence of the N-terminal domain on the aggregation properties of the prion protein. Protein Sci. 14 (2005) 2154-2166
-
(2005)
Protein Sci.
, vol.14
, pp. 2154-2166
-
-
Frankenfield, K.N.1
Powers, E.T.2
Kelly, J.W.3
-
15
-
-
33646342768
-
Role of N-terminal familial mutations in prion protein fibrillization and prion amyloid propagation in vitro
-
Jones E.M., Surewicz K., and Surewicz W.K. Role of N-terminal familial mutations in prion protein fibrillization and prion amyloid propagation in vitro. J. Biol. Chem. 281 (2006) 8190-8196
-
(2006)
J. Biol. Chem.
, vol.281
, pp. 8190-8196
-
-
Jones, E.M.1
Surewicz, K.2
Surewicz, W.K.3
-
16
-
-
35948932203
-
Activation of classical pathway of complement cascade by soluble oligomers of prion
-
Dumestre-Perard C., Osmundson J., Lemaire-Vieille C., Thielens N., Grives A., Favier B., Csopaki F., Jamin M., Gagnon J., and Cesbron J.Y. Activation of classical pathway of complement cascade by soluble oligomers of prion. Cell. Microbiol. 9 (2007) 2870-2879
-
(2007)
Cell. Microbiol.
, vol.9
, pp. 2870-2879
-
-
Dumestre-Perard, C.1
Osmundson, J.2
Lemaire-Vieille, C.3
Thielens, N.4
Grives, A.5
Favier, B.6
Csopaki, F.7
Jamin, M.8
Gagnon, J.9
Cesbron, J.Y.10
-
17
-
-
33644540192
-
Octapeptide repeat insertions increase the rate of protease-resistant prion protein formation
-
Moore R.A., Herzog C., Errett J., Kocisko D.A., Arnold K.M., Hayes S.F., and Priola S.A. Octapeptide repeat insertions increase the rate of protease-resistant prion protein formation. Protein Sci. 15 (2006) 609-619
-
(2006)
Protein Sci.
, vol.15
, pp. 609-619
-
-
Moore, R.A.1
Herzog, C.2
Errett, J.3
Kocisko, D.A.4
Arnold, K.M.5
Hayes, S.F.6
Priola, S.A.7
-
18
-
-
0029863648
-
Prion protein (PrP) with amino-proximal deletions restoring susceptibility of PrP knockout mice to scrapie
-
Fischer M., Rulicke T., Raeber A., Sailer A., Moser M., Oesch B., Brandner S., Aguzzi A., and Weissmann C. Prion protein (PrP) with amino-proximal deletions restoring susceptibility of PrP knockout mice to scrapie. EMBO J. 15 (1996) 1255-1264
-
(1996)
EMBO J.
, vol.15
, pp. 1255-1264
-
-
Fischer, M.1
Rulicke, T.2
Raeber, A.3
Sailer, A.4
Moser, M.5
Oesch, B.6
Brandner, S.7
Aguzzi, A.8
Weissmann, C.9
-
19
-
-
33645064267
-
Fusion of doppel to octapeptide repeat and N-terminal half of hydrophobic region of prion protein confers resistance to serum deprivation
-
Lee D.C., Sakudo A., Kim C.K., Nishimura T., Saeki K., Matsumoto Y., Yokoyama T., Chen S.G., Itohara S., and Onodera T. Fusion of doppel to octapeptide repeat and N-terminal half of hydrophobic region of prion protein confers resistance to serum deprivation. Microbiol. Immunol. 50 (2006) 203-209
-
(2006)
Microbiol. Immunol.
, vol.50
, pp. 203-209
-
-
Lee, D.C.1
Sakudo, A.2
Kim, C.K.3
Nishimura, T.4
Saeki, K.5
Matsumoto, Y.6
Yokoyama, T.7
Chen, S.G.8
Itohara, S.9
Onodera, T.10
-
20
-
-
23144463784
-
Assembly of the full-length recombinant mouse prion protein I. Formation of soluble oligomers
-
Vendrely C., Valadie H., Bednarova L., Cardin L., Pasdeloup M., Cappadoro J., Bednar J., Rinaudo M., and Jamin M. Assembly of the full-length recombinant mouse prion protein I. Formation of soluble oligomers. Biochim. Biophys. Acta 1724 (2005) 355-366
-
(2005)
Biochim. Biophys. Acta
, vol.1724
, pp. 355-366
-
-
Vendrely, C.1
Valadie, H.2
Bednarova, L.3
Cardin, L.4
Pasdeloup, M.5
Cappadoro, J.6
Bednar, J.7
Rinaudo, M.8
Jamin, M.9
-
21
-
-
0037077234
-
Pathway complexity of prion protein assembly into amyloid
-
Baskakov I.V., Legname G., Baldwin M.A., Prusiner S.B., and Cohen F.E. Pathway complexity of prion protein assembly into amyloid. J. Biol. Chem. 277 (2002) 21140-21148
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 21140-21148
-
-
Baskakov, I.V.1
Legname, G.2
Baldwin, M.A.3
Prusiner, S.B.4
Cohen, F.E.5
-
22
-
-
14744284214
-
Sequential generation of two structurally distinct ovine prion protein soluble oligomers displaying different biochemical reactivities
-
Rezaei H., Eghiaian F., Perez J., Doublet B., Choiset Y., Haertle T., and Grosclaude J. Sequential generation of two structurally distinct ovine prion protein soluble oligomers displaying different biochemical reactivities. J. Mol. Biol. 347 (2005) 665-679
-
(2005)
J. Mol. Biol.
, vol.347
, pp. 665-679
-
-
Rezaei, H.1
Eghiaian, F.2
Perez, J.3
Doublet, B.4
Choiset, Y.5
Haertle, T.6
Grosclaude, J.7
-
23
-
-
0035957003
-
Two different neurodegenerative diseases caused by proteins with similar structures
-
Mo H., Moore R.C., Cohen F.E., Westaway D., Prusiner S.B., Wright P.E., and Dyson H.J. Two different neurodegenerative diseases caused by proteins with similar structures. Proc. Natl. Acad. Sci. USA 98 (2001) 2352-2357
-
(2001)
Proc. Natl. Acad. Sci. USA
, vol.98
, pp. 2352-2357
-
-
Mo, H.1
Moore, R.C.2
Cohen, F.E.3
Westaway, D.4
Prusiner, S.B.5
Wright, P.E.6
Dyson, H.J.7
-
24
-
-
0033695126
-
Prion protein devoid of the octapeptide repeat region restores susceptibility to scrapie in PrP knockout mice
-
Flechsig E., Shmerling D., Hegyi I., Raeber A.J., Fischer M., Cozzio A., von Mering C., Aguzzi A., and Weissmann C. Prion protein devoid of the octapeptide repeat region restores susceptibility to scrapie in PrP knockout mice. Neuron 27 (2000) 399-408
-
(2000)
Neuron
, vol.27
, pp. 399-408
-
-
Flechsig, E.1
Shmerling, D.2
Hegyi, I.3
Raeber, A.J.4
Fischer, M.5
Cozzio, A.6
von Mering, C.7
Aguzzi, A.8
Weissmann, C.9
-
25
-
-
0036713563
-
Unusual property of prion protein unfolding in neutral salt solution
-
Nandi P.K., Leclerc E., and Marc D. Unusual property of prion protein unfolding in neutral salt solution. Biochemistry 41 (2002) 11017-11024
-
(2002)
Biochemistry
, vol.41
, pp. 11017-11024
-
-
Nandi, P.K.1
Leclerc, E.2
Marc, D.3
|