Choice of oils for essential fat supplements can enhance production of abnormal metabolites in fat oxidation disorders

Molecular Genetics and Metabolism

Volumn 92, Issue 4, 2007, Pages 346-350

  Roe, Charles R ^a   Roe, Diane S ^a   Wallace, Mary ^a   Garritson, Brenda ^a  

^a BAYLOR UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

Diet supplements; Essential fats; Fatty acid oxidation disorders; Methylketones

Indexed keywords

ACETONE; ACETYL COENZYME A; ACYLCARNITINE; CARNITINE PALMITOYLTRANSFERASE; ESSENTIAL FATTY ACID; FAT; FATTY ACID; LEVO 3 HYDROXY ACYL COENZYME A DEHYDROGENASE; LINOLEIC ACID; LINOLENIC ACID; OIL; OLEIC ACID; PALMITIC ACID; UNCLASSIFIED DRUG; VERY LONG CHAIN ACYL COENZYME A DEHYDROGENASE;

ARTICLE; CASE REPORT; CONTROLLED STUDY; DECARBOXYLATION; ENZYME ACTIVITY; FATTY ACID OXIDATION; FIBROBLAST; FLAX; HUMAN; HUMAN CELL; HUMAN TISSUE; INCUBATION TIME; METABOLITE; PERIPHERAL NEUROPATHY; PRIORITY JOURNAL; PROTEIN DEFICIENCY; RAPESEED; SUPPLEMENTATION; WALNUT;

ACYL-COA DEHYDROGENASE, LONG-CHAIN; CARNITINE; CELL LINE; DIET THERAPY; DIETARY FATS; ENERGY INTAKE; FIBROBLASTS; LIPID METABOLISM, INBORN ERRORS; MULTIENZYME COMPLEXES; OILS; OXIDATION-REDUCTION; POLYNEUROPATHIES;

BRASSICA NAPUS VAR. NAPUS; PYRONIA TITHONUS;

EID: 36148997325     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2007.07.012     Document Type: Article

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