Vestibular and auditory deficits in Fabry disease and their response to enzyme replacement therapy

Journal of Neurology

Volumn 254, Issue 10, 2007, Pages 1433-1442

  Palla, A ^a   Hegemann, S ^a   Widmer, U ^a   Straumann, D ^a  

^a UNIVERSITY HOSPITAL ZURICH   (Switzerland)

Author keywords

Caloric irrigation; Fabry disease; Head impulse test; Lysosomal disease; Pure tone audiogram

Indexed keywords

AGALSIDASE ALFA; ALPHA GALACTOSIDASE;

ADULT; AGED; ARTICLE; DRUG EFFECT; ENZYME REPLACEMENT; FABRY DISEASE; FEMALE; HEARING IMPAIRMENT; HUMAN; MAJOR CLINICAL STUDY; MALE; PREVALENCE; PRIORITY JOURNAL; PURE TONE AUDIOMETRY; SEMICIRCULAR CANAL; TREATMENT RESPONSE; VESTIBULAR DISORDER; VESTIBULOCOCHLEAR NERVE;

ADOLESCENT; ADULT; AGED; ALPHA-GALACTOSIDASE; ANALYSIS OF VARIANCE; FABRY DISEASE; FEMALE; FOLLOW-UP STUDIES; HEARING DISORDERS; HEARING TESTS; HUMANS; ISOENZYMES; MALE; MIDDLE AGED; SEX FACTORS; VESTIBULAR DISEASES;

EID: 36148983806     PISSN: 03405354     EISSN: 14321459     Source Type: Journal    
DOI: 10.1007/s00415-007-0575-y     Document Type: Article

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