Malignant triton tumor in a patient with Li-Fraumeni syndrome and a novel TP53 mutation

Pediatric Blood and Cancer

Volumn 49, Issue 7, 2007, Pages 1000-1004

  Chao, Mwe Mwe ^a   Levine, John E ^a   Ruiz, Robert E ^a   Kohlmann, Wendy K ^a   Bower, Matthew A ^b   Petty, Elizabeth M ^a   Mody, Rajen J ^a  

^a UNIVERSITY OF MICHIGAN HEALTH SYSTEM   (United States)

^b UNIVERSITY OF MINNESOTA MEDICAL CENTER   (United States)

Author keywords

Li Fraumeni syndrome; Malignant peripheral nerve sheath tumor; Malignant triton tumor; TP53

Indexed keywords

CARBOPLATIN; CYCLOPHOSPHAMIDE; DOXORUBICIN; ETOPOSIDE; IFOSFAMIDE; RAZOXANE; THIOTEPA; VINCRISTINE;

ARTICLE; AUTOLOGOUS STEM CELL TRANSPLANTATION; BIOPSY; CANCER SURGERY; CASE REPORT; CHEMOTHERAPY; DISEASE ASSOCIATION; DRUG MEGADOSE; DRUG TOLERABILITY; FAMILIAL CANCER; FAMILY HISTORY; GENE MUTATION; GERM LINE; HISTOLOGY; HUMAN; HUMAN TISSUE; IMMUNOHISTOLOGY; LYMPH NODE METASTASIS; MALE; MALIGNANT TRITON TUMOR; MASTICATORY MUSCLE; MULTIPLE CYCLE TREATMENT; NERVE SHEATH TUMOR; PATHOGENESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; SOMATIC MUTATION; TP53 GENE; TREATMENT OUTCOME; TREATMENT RESPONSE; TUMOR SUPPRESSOR GENE;

ANTINEOPLASTIC COMBINED CHEMOTHERAPY PROTOCOLS; CHILD, PRESCHOOL; COMBINED MODALITY THERAPY; FOLLOW-UP STUDIES; GERM-LINE MUTATION; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMANS; LI-FRAUMENI SYNDROME; MALE; NERVE SHEATH NEOPLASMS; NOSE NEOPLASMS; PEDIGREE; TOMOGRAPHY, X-RAY COMPUTED; TRANSPLANTATION, AUTOLOGOUS; TREATMENT OUTCOME; TUMOR SUPPRESSOR PROTEIN P53;

EID: 35649016560     PISSN: 15455009     EISSN: 15455017     Source Type: Journal    
DOI: 10.1002/pbc.20700     Document Type: Article

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