Dysfunction of dysferlin-deficient hearts

Journal of Molecular Medicine

Volumn 85, Issue 11, 2007, Pages 1203-1214

  Wenzel, Katrin ^a   Geier, Christian ^a   Qadri, Fatimunnisa ^a   Hubner, Norbert ^b   Schulz, Herbert ^b   Erdmann, Bettina ^b   Gross, Volkmar ^b   Bauer, David ^c   Dechend, Ralf ^a   Dietz, Rainer ^a   Osterziel, Karl Josef ^a   Spuler, Simone ^b,d   Özcelik, Cemil ^a  

^a FRANZ VOLHARD CLINIC   (Germany)

^b MAX DELBRÜCK CENTER FOR MOLECULAR MEDICINE   (Germany)

^c BAYER PHARMA AG   (Germany)

^d CHARITÉ UNIVERSITÄTSMEDIZIN BERLIN   (Germany)

Author keywords

Cardiomyopathy; Contractile function; Dysferlin; Gene expression; Isoproterenol; Muscular dystrophy

Indexed keywords

CARDIAC ANKYRIN REPEATED PROTEIN; DESMIN; DYSFERLIN; EVANS BLUE; ISOPRENALINE; LIM PROTEIN; MEMBRANE PROTEIN; METALLOPROTEINASE; METALLOPROTEINASE 2; PROTEIN CAPZ; TRANSCRIPTION FACTOR LHX3; UNCLASSIFIED DRUG; ZASP PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONGESTIVE CARDIOMYOPATHY; CONTROLLED STUDY; DEATH; ELECTRON MICROSCOPY; ENZYME REGULATION; FEMALE; GENE EXPRESSION PROFILING; GENE MUTATION; GENETIC ASSOCIATION; HEART MUSCLE BIOPSY; HEART MUSCLE CONTRACTILITY; HEART MUSCLE FIBER MEMBRANE; HEART MUSCLE FIBROSIS; HEART MUSCLE INJURY; HISTOPATHOLOGY; IMMUNOHISTOCHEMISTRY; MECHANICAL STRESS; MOUSE; NONHUMAN; NUCLEOTIDE SEQUENCE; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; SIGNAL TRANSDUCTION; SYSTOLIC BLOOD PRESSURE; WESTERN BLOTTING;

ADOLESCENT; ADULT; ANIMALS; BLOTTING, WESTERN; ECHOCARDIOGRAPHY; FEMALE; GENE EXPRESSION PROFILING; GENE EXPRESSION REGULATION; HEART; HEART FUNCTION TESTS; HUMANS; ISOPROTERENOL; MALE; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; MIDDLE AGED; MUSCLE PROTEINS; MUSCULAR DYSTROPHIES, LIMB-GIRDLE; MUTATION; MYOCARDIUM;

EID: 35448939656     PISSN: 09462716     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00109-007-0253-7     Document Type: Article

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