Peripheral nervous system manifestations in a Sandhoff disease mouse model: Nerve conduction, myelin structure, lipid analysis

Journal of Negative Results in BioMedicine

Volumn 6, Issue , 2007, Pages

  McNally, Melanie A ^a   Baek, Rena C ^a   Avila, Robin L ^a   Seyfried, Thomas N ^a   Strichartz, Gary R ^b   Kirschner, Daniel A ^a  

^a BOSTON COLLEGE   (United States)

^b BRIGHAM AND WOMEN S HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BETA N ACETYLHEXOSAMINIDASE B; GANGLIOSIDE GM2 ACTIVATOR PROTEIN; LIPID;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; ELECTROPHYSIOLOGY; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; LIPID ANALYSIS; LIPID COMPOSITION; MOUSE; MYELIN DEFICIENCY; MYELIN SHEATH; NERVE CONDUCTION; NONHUMAN; PERIPHERAL NERVOUS SYSTEM; PERIPHERAL NEUROPATHY; PROTEIN DEGRADATION; PROTEIN FUNCTION; PROTEIN STRUCTURE; SANDHOFF DISEASE; X RAY DIFFRACTION; ANIMAL; CHEMICAL STRUCTURE; CHEMISTRY; DISEASE MODEL; MOUSE MUTANT; PATHOPHYSIOLOGY; TRANSGENIC MOUSE;

ANIMALS; DISEASE MODELS, ANIMAL; LIPIDS; MICE; MICE, KNOCKOUT; MICE, TRANSGENIC; MOLECULAR STRUCTURE; MYELIN SHEATH; NEURAL CONDUCTION; PERIPHERAL NERVOUS SYSTEM; SANDHOFF DISEASE; X-RAY DIFFRACTION;

EID: 34548694515     PISSN: None     EISSN: 14775751     Source Type: Journal    
DOI: 10.1186/1477-5751-6-8     Document Type: Article

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