Pulmonary arterial hypertension of congenital heart diseases: From reversible pulmonary hypertension to Eisenmenger syndrome

Korean Circulation Journal

Volumn 37, Issue 7, 2007, Pages 287-297

  Jo, Won Jung ^a  

^a Ajou University School of Medicine   (South Korea)

Author keywords

Congenital heart defects; Eisenmenger syndrome; Hypertension, pulmonary

Indexed keywords

ADENOSINE; ANTIARRHYTHMIC AGENT; ANTICOAGULANT AGENT; ANTIINFLAMMATORY AGENT; ANTITHROMBOCYTIC AGENT; BERAPROST; BOSENTAN; CALCIUM CHANNEL BLOCKING AGENT; DIGITALIS; DIURETIC AGENT; ENDOTHELIN 1; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE INHIBITOR; ILOPROST; LIPOXYGENASE INHIBITOR; NITRIC OXIDE; PROSTACYCLIN; SILDENAFIL; WARFARIN;

CATHETERIZATION; CLINICAL FEATURE; CLINICAL TRIAL; CONGENITAL HEART DISEASE; DISEASE ASSOCIATION; DISEASE CLASSIFICATION; DRUG DOSE INCREASE; DRUG HALF LIFE; DRUG MECHANISM; DRUG WITHDRAWAL; ECHOCARDIOGRAPHY; EISENMENGER COMPLEX; ELECTROCARDIOGRAM; EXERCISE TEST; HEART LUNG TRANSPLANTATION; HIGH RESOLUTION COMPUTER TOMOGRAPHY; HUMAN; LUNG HEMODYNAMICS; LUNG TRANSPLANTATION; MULTIDETECTOR COMPUTED TOMOGRAPHY; OXYGEN THERAPY; PHLEBOTOMY; PHYSICAL EXAMINATION; PULMONARY HYPERTENSION; REVIEW; RISK FACTOR; SUDDEN DEATH; SURVIVAL TIME; THORAX RADIOGRAPHY; THREE DIMENSIONAL IMAGING;

EID: 34548239220     PISSN: 17385520     EISSN: 17385555     Source Type: Journal    
DOI: 10.4070/kcj.2007.37.7.287     Document Type: Review

References (34)

1. Wood P. The Eisenmenger syndrome or pulmonary hypertension with reversed central shunt. BMJ 1958;2:755-62.
2. McGoon M, Gutterman D, Steen V, et al. Screening, early detection, and diagnosis of pulmonary arterial hypertension: ACCP evidence-based clinical practice guidelines. Chest 2004;126 (1 Suppl):14S-34S.
3. Diller GP, Gatzoulis MA. Pulmonary vascular disease in adults with congenital heart disease. Circulation 2007;115-1039-50.
4. Barst RJ, McGoon M, Torbicki A, et al. Diagnosis and differential assessment of pulmonary arterial hypertension. J Am Coll Cardiol 2004;43 (Suppl S):40S-7S.
5. Farber HW, Loscalzo J. Pulmonary arterial hypertension. N Engl J Med 2004;351-1655-65.
6. Barst RJ. Recent advances in the treatment of pediatric pulmonary artery hypertension. Pediatr Clin North Am 1999;46-331-45.
7. Berman EB, Barst RJ. Eisenmenger's syndrome: current management. Prog Cardiovasc Dis 2002;45:129-38.
8. Kaemmerer H, Fratz S, Bauer U, et al. Emergency hospital admissions and three-year survival of adults with and without cardiovascular surgery for congenital cardiac disease. J Thorac Cardiovasc Surg 2003;126:1048-52.
9. Keck BM, Bennett LE, Rosendale J, Daily OP, Novick RJ, Hosenpud JD. Worldwide thoracic organ transplantation: a report from the UNOS/ISHLT International Registry for Thoracic Organ Transplantation. Clin Transpl; 1999. p.35-49.
10. Hopkins WE, Ochoa LL, Richardson GW, Trulock EP. Comparison of the hemodynamics and survival of adults with severe primary pulmonary hypertension or Eisenmenger syndrome. J Heart Lung Transplant 1996;15:100-5.
11. Hong SK, Han KR, Kim HS, et al. Eisenmenger syndrome in adult. Korean Circ J 1992;22:563-72.
12. Kim KH, Park JC, Lee S, et al. Clinical features and long-term clinical outcomes of adult atrial septal defects. Korean Circ J 2006;36:695-700.
13. Steele PM, Fuster V, Cohen M, Ritter DG, McGoon DC. Isolated atrial septal defect with pulmonary vascular obstructive disease-long-term follow-up and prediction of outcome after surgical correction. Circulation 1987;76:1037-42.
14. Silversides CK, Granton JT, Konen E, Hart MA, Webb GD, Therrien J. Pulmonary thrombosis in adults with Eisenmenger syndrome. J Am Coll Cardiol 2003;42:1982-7.
15. Daliento L, Somerville J, Presbitero P, et al. Eisenmenger syndrome: factors relating to deterioration and death. Eur Heart J 1998;19:1845-55.
16. Galie N, Torbicki A, Barst R, et al. Guidelines on diagnosis and treatment of pulmonary arterial hypertension. Eur Heart J 2004; 25:2243-78.
17. Rubin LJ, Badesch DB. Evaluation and management of the patient with pulmonary arterial hypertension. Ann Intern Med 2005;143:282-92.
18. Heath D, Edwards JE. The pathology of hypertensive pulmonary vascular disease: a description of six grades of structural changes in the pulmonary arteries with special reference to congenital cardiac septal defects. Circulation 1958;18:533-47.
19. Ito T, Ozawa K, Shimada K. Current drug targets and future therapy of pulmonary arterial hypertension. Curr Med Chem 2007;14:719-33.
20. Benisty JL, Landzberg MJ. Eisenmenger's syndrome. Curr Trea Options Cardiovasc Med 1999;1:355-62
21. Perloff JK, Rosove MH, Child JS, Wright GB. Adults with cyanotic congenital heart disease: hematologic management. Ann Intern Med 1988;109:406-13.
22. Kim HY. A case of Eisenmenger syndrome with brain abscess. Korean Circ J 1999;29:79-83.
23. Chung SM, Kim SH, Ryu KH, Kim HJ, Han SW, Lee Y. Impact of pulmonary hypertension on the regional right ventricular strain. Korean Circ J 2006;36:578-82.
24. Badesch DB, Abman SH, Ahearn GS, et al. Medical therapy for pulmonary aArterial hypertension: ACCP evidence-based clinical practice guidelines. Chest 2004;126:35S-62S.
25. Therrien J, Warnes C, Daliento L, et al. Canadian Cardiovascular Society Consensus Conference 2001 update: recommendations for the management of adults with congenital heart disease part III. Can J Cardiol 2001;17:1135-58.
26. Diller GP, Dimopoulos K, Broberg CS, et al. Presentation, survival prospects, and predictors of death in Eisenmenger syndrome: a combined retrospective and case-control study. Eur Heart J 2006;27:1737-42.
27. Warnes CA. Pregnancy and pulmonary hypertension. Int J Cardiol 2004;97:11-3.
28. Sreeram N. Eisenmenger syndrome: towards identifying the risk factors for death. Eur Heart J 2006;27:1644-5.
29. Broberg CS, Uebing A, Cuomo L, Thein SL, Papdopoulous MG, Gatzoulis MA. Adult patients with Eisenmenger syndrome report flying safely on commercial airlines. Heart 2006 Available from: URL: http://heart.bmj.com/cgi/rapidpdf/hrt; 2006.
30. Waddell TK, Bennett L, Kennedy R, Todd TR, Keshavjee SH. Heart-lung or lung transplantation for Eisenmenger syndrome. J Heart Lung Transplant 2002;21:731-7.
31. Humpl T, Reyes JT, Holtby H, Stephens D, Adatia I. Beneficial effect of oral sildenafil therapy on childhood pulmonary arterial hypertension: twelve-month clinical trial of a single-drug, open-label, pilot study. Circulation 2005;111:3274-80.
32. Galie N, Beghetti M, Gatzoulis MA, et al. Bosentan therapy in patients with Eisenmenger syndrome: a multicenter, double-blind, randomized, placebo-controlled study. Circulation 2006;114:48-54.
33. McLaughlin VV, Presberg KW, Doyle RL, et al. Prognosis of pulmonary arterial hypertension: ACCP evidence-based clinical practice guidelines. Chest 2004;126 (1 Suppl):78S-92S.
34. Cantor WJ, Harrison DA, Moussadji JS, et al. Determinants of survival and length of survival in adults with Eisenmenger syndrome. Am J Cardiol 1999;84:677-81.