An evaluation of tests used for the diagnosis and monitoring of C1 inhibitor deficiency: Normal serum C4 does not exclude hereditary angio-oedema

Clinical and Experimental Immunology

Volumn 149, Issue 3, 2007, Pages 513-516

  Tarzi, M D ^a,c   Hickey, A ^a   Forster T ^b   Mohammadi, M ^a   Longhurst, H J ^a  

^a BARTS HEALTH NHS TRUST   (United Kingdom)

^b UNIVERSITY OF WÜRZBURG   (Germany)

^c ROYAL LONDON HOSPITAL   (United Kingdom)

Author keywords

Angio oedema; C1 inhibitor deficiency; HAE

Indexed keywords

ANTIGEN; C1 INHIBITOR ANTIGEN; COMPLEMENT COMPONENT C1S INHIBITOR; COMPLEMENT COMPONENT C4; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; AGED; ANGIONEUROTIC EDEMA; ARTICLE; C1 INHIBITOR DEFICIENCY; CHILD; CLINICAL ARTICLE; COMPLEMENT BLOOD LEVEL; COMPLEMENT DEFICIENCY; CONTROLLED STUDY; DIAGNOSTIC TEST; EMBRYO; ENZYME LINKED IMMUNOSORBENT ASSAY; FEMALE; GENE MUTATION; HUMAN; HUMAN CELL; LABORATORY DIAGNOSIS; MALE; MOLECULAR GENETICS; MONITORING; NORMAL VALUE; PRIORITY JOURNAL; RECEIVER OPERATING CHARACTERISTIC; REFERENCE VALUE; SENSITIVITY ANALYSIS; SENSITIVITY AND SPECIFICITY;

ADULT; AGED; ANGIONEUROTIC EDEMA; BIOLOGICAL MARKERS; CHILD; COMPLEMENT C1 INHIBITOR PROTEIN; COMPLEMENT C4; FALSE NEGATIVE REACTIONS; FEMALE; HUMANS; MALE; MUTATION; REFERENCE VALUES; SENSITIVITY AND SPECIFICITY;

EID: 34547895872     PISSN: 00099104     EISSN: 13652249     Source Type: Journal    
DOI: 10.1111/j.1365-2249.2007.03438.x     Document Type: Article

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