Perioperative management of MYH9 hereditary macrothrombocytopenia (Fechtner syndrome)

European Journal of Haematology

Volumn 79, Issue 3, 2007, Pages 263-268

  Selleng, Kathleen ^b   Lubenow, Lena E ^b   Greinacher, Andreas ^b   Warkentin, Theodore E ^a,c  

^a HAMILTON REGIONAL LABORATORY MEDICINE PROGRAM   (Canada)

^b UNIVERSITY OF GREIFSWALD   (Germany)

^c MCMASTER UNIVERSITY   (Canada)

Author keywords

Fechtner syndrome; Hereditary macrothrombocytopenia; MYH9 related disorder; Pulmonary embolism; Thromboprophylaxis

Indexed keywords

ANTICOAGULANT AGENT; CORTICOSTEROID DERIVATIVE; MYOSIN HEAVY CHAIN ALPHA; WARFARIN;

ADULT; ANAMNESIS; ARTICLE; BRAIN ARTERIOVENOUS MALFORMATION; CASE REPORT; CLINICAL FEATURE; COMPUTED TOMOGRAPHIC ANGIOGRAPHY; DIAGNOSTIC ERROR; FECHTNER SYNDROME; GENE MUTATION; GENE SEQUENCE; GENETIC DISORDER; HUMAN; IMMUNOFLUORESCENCE TEST; LABORATORY TEST; LUNG EMBOLISM; MALE; NEUROSURGERY; NON MUSCLE MYOSIN HEAVY CHAIN IIA GENE; PERIOPERATIVE PERIOD; PHYSICAL EXAMINATION; POSTOPERATIVE THROMBOSIS; PRIORITY JOURNAL; REGULATOR GENE; RISK ASSESSMENT; SPLENECTOMY; THROMBOCYTOPENIA;

ADULT; HUMANS; MALE; MOLECULAR MOTOR PROTEINS; MUTATION; MYOSIN HEAVY CHAINS; PERIOPERATIVE CARE; PREMEDICATION; PULMONARY EMBOLISM; SYNDROME; THROMBOCYTOPENIA;

EID: 34547742070     PISSN: 09024441     EISSN: 16000609     Source Type: Journal    
DOI: 10.1111/j.1600-0609.2007.00913.x     Document Type: Article

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