Acquired factor VIII deficiency associated with a novel primary immunodeficiency suggestive of autosomal recessive hyper IgE syndrome

Journal of Pediatric Hematology/Oncology

Volumn 29, Issue 5, 2007, Pages 327-329

  Ozgur, Tuba Turul ^a   Asal, Gulten Turkkan ^a   Gurgey, Aytemiz ^a   Tezcan, Ilhan ^a   Ersoy, Fugen ^a   Sanal, Ozden ^a  

^a HACETTEPE UNIVERSITY   (Turkey)

Author keywords

Acquired hemophilia; Factor VIII inhibitor; Hyper IgE syndrome; T cell immunodeficiency

Indexed keywords

BLOOD CLOTTING FACTOR 8; BLOOD CLOTTING FACTOR 8 INHIBITOR; COTRIMOXAZOLE; FLUCONAZOLE; PREDNISOLONE;

ANAMNESIS; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BLEEDING; BRONCHIECTASIS; CASE REPORT; CLINICAL FEATURE; DISEASE COURSE; HEMATOMA; HEMOPHILIA A; HERPES ZOSTER; HUMAN; HYPERIMMUNOGLOBULINEMIA E; IMMUNE DEFICIENCY; LABORATORY TEST; MALE; PHYSICAL EXAMINATION; PRIORITY JOURNAL; SCHOOL CHILD; TOMOGRAPHY;

ADMINISTRATION, ORAL; BLOOD COAGULATION FACTOR INHIBITORS; CHILD; FOLLOW-UP STUDIES; GENES, RECESSIVE; HEMOPHILIA A; HUMANS; JOB'S SYNDROME; MALE; PREDICTIVE VALUE OF TESTS; PREDNISOLONE; PROGNOSIS; TREATMENT OUTCOME;

EID: 34248218677     PISSN: 10774114     EISSN: 15363678     Source Type: Journal    
DOI: 10.1097/MPH.0b013e318059c236     Document Type: Article

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