Effects of OPA1 mutations on mitochondrial morphology and apoptosis: Relevance to ADOA pathogenesis

Journal of Cellular Physiology

Volumn 211, Issue 2, 2007, Pages 423-430

  Olichon, Aurélien ^a   Landes, Thomas ^a   Arnauné Pelloquin, Laetitia ^a   Emorine, Laurent J ^a   Mils, Valérie ^a   Guichet, Agnès ^b   Delettre, Cécile ^c   Hamel, Christian ^c   Amati Bonneau, Patrizia ^b,d   Bonneau, Dominique ^b,d   Reynier, Pascal ^b,d   Lenaers, Guy ^a,c   Belenguer, Pascale ^a  

^a Université de Toulouse Paul Sabatier   (France)

^b ANGERS UNIVERSITY HOSPITAL   (France)

^c Montpellier University Medical Center   (France)

^d INSERM   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ARGININE; GLUTAMIC ACID; GLUTAMINE; GLYCINE; GUANOSINE TRIPHOSPHATASE; MITOCHONDRIAL PROTEIN; MUTANT PROTEIN; PROTEIN OPA1; PROTEIN SUBUNIT; UNCLASSIFIED DRUG;

ALLELE; AMINO ACID SUBSTITUTION; APOPTOSIS; ARTICLE; AUTOSOMAL DOMINANT OPTIC ATROPHY; CARBOXY TERMINAL SEQUENCE; CELL FUNCTION; COMPLEX FORMATION; CONTROLLED STUDY; DRUG SENSITIVITY; FIBROBLAST; GENE DELETION; GENE FUSION; GENETIC ASSOCIATION; GENETIC TRANSFECTION; HELA CELL; HUMAN; HUMAN CELL; MISSENSE MUTATION; MITOCHONDRION; MUTATIONAL ANALYSIS; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN FUNCTION; RETINA GANGLION CELL;

APOPTOSIS; BLOTTING, WESTERN; FIBROBLASTS; GENE DELETION; GTP PHOSPHOHYDROLASES; HELA CELLS; HUMANS; MICROSCOPY, FLUORESCENCE; MITOCHONDRIA; MUTATION; MUTATION, MISSENSE; OPTIC ATROPHY, AUTOSOMAL DOMINANT; PHENOTYPE; SKIN; STAUROSPORINE; TRANSFECTION;

EID: 34147223220     PISSN: 00219541     EISSN: None     Source Type: Journal    
DOI: 10.1002/jcp.20950     Document Type: Article

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