A new evidence for the maintenance of the sarcoglycan complex in muscle sarcolemma in spite of the primary absence of δ-SG protein

Journal of Molecular Medicine

Volumn 85, Issue 4, 2007, Pages 415-420

  Gouveia, Telma L F ^a   Kossugue, Patrícia M ^a   Paim, Julia F ^b   Zatz, Mayana ^a   Anderson, Louise V B ^c   Nigro, Vincenzo ^d   Vainzof, Mariz ^a  

^a UNIVERSITY OF SÃO PAULO   (Brazil)

^b SARAH NETWORK OF REHABILITATION HOSPITALS   (Brazil)

^c NEWCASTLE GENERAL HOSPITAL   (United Kingdom)

^d SECOND UNIVERSITY OF NAPLES   (Italy)

Author keywords

DGC; Limb girdle muscular dystrophies; Sarcoglycanopathies

Indexed keywords

DELTA SARCOGLYCAN; SARCOGLYCAN; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; ARTICLE; CLINICAL ARTICLE; CLINICAL FEATURE; DISEASE COURSE; DISEASE SEVERITY; FALLING; GENE DELETION; HOMOZYGOSITY; HUMAN; HUMAN TISSUE; LIMB GIRDLE MUSCULAR DYSTROPHY; MALE; MUSCLE BIOPSY; PROTEIN ANALYSIS; PROTEIN DEFICIENCY; SARCOLEMMA; SCHOOL CHILD; WALKING;

HUMANS; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES, LIMB-GIRDLE; SARCOGLYCANS; SARCOLEMMA;

EID: 33947423351     PISSN: 09462716     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00109-007-0163-8     Document Type: Article

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