Unfolded protein response and aggresome formation in hereditary reducing-body myopathy

Muscle and Nerve

Volumn 35, Issue 3, 2007, Pages 322-326

  Liewluck, Teerin ^a   Hayashi, Yukiko K ^a   Ohsawa, Maki ^b   Kurokawa, Rumi ^a   Fujita, Masako ^a   Noguchi, Satoru ^a   Nonaka, Ikuya ^a   Nishino, Ichizo ^a  

^a NATIONAL INSTITUTE OF NEUROSCIENCE   (Japan)

^b NATIONAL INSTITUTE OF MENTAL HEALTH   (Japan)

Author keywords

Aggresome; Endoplasmic reticulum stress; Endoplasmic reticulum stress associated degradation (EDRA); Reducing body myopathy; Unfolded protein response

Indexed keywords

CHAPERONE; GAMMA TUBULIN; GLUCOSE RELATED PROTEIN 78; MEMBRANE PROTEIN; MESSENGER RNA; UBIQUITIN; UNCLASSIFIED DRUG;

AGGRESOME; ARTICLE; CASE REPORT; CLINICAL FEATURE; HEREDITARY REDUCING BODY MYOPATHY; HUMAN; IMMUNOHISTOCHEMISTRY; MALE; MYOPATHY; PRIORITY JOURNAL; PROTEIN FOLDING; QUANTITATIVE ANALYSIS; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; SARCOPLASMIC RETICULUM; SCHOOL CHILD; WESTERN BLOTTING;

ADENOSINE TRIPHOSPHATASES; ADULT; BIOLOGICAL MARKERS; CELL CYCLE PROTEINS; CHILD; ENDOPLASMIC RETICULUM; FEMALE; GENETIC DISEASES, INBORN; HEAT-SHOCK PROTEINS; HUMANS; INCLUSION BODIES; MALE; MEMBRANE PROTEINS; MOLECULAR CHAPERONES; MUSCLE PROTEINS; MUSCLE, SKELETAL; MUSCULAR DISEASES; PROTEIN FOLDING; RARE DISEASES; RNA, MESSENGER; TUBULIN; UBIQUITIN;

EID: 33847690682     PISSN: 0148639X     EISSN: 10974598     Source Type: Journal    
DOI: 10.1002/mus.20691     Document Type: Article

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