-
1
-
-
0032554898
-
Elastin is an essential determinant of arterial morphogenesis
-
Li, D. Y., Brooke, B., Davis, E. C., Mecham, R. P., Sorensen, L. K., Boak, B. B., Eichwald, E. and Keating, M. T. (1998) Elastin is an essential determinant of arterial morphogenesis. Nature 393, 276-280
-
(1998)
Nature
, vol.393
, pp. 276-280
-
-
Li, D.Y.1
Brooke, B.2
Davis, E.C.3
Mecham, R.P.4
Sorensen, L.K.5
Boak, B.B.6
Eichwald, E.7
Keating, M.T.8
-
2
-
-
0032533870
-
Novel arterial pathology in mice and humans hemizygous for elastin
-
Li, D. Y., Faury, G., Taylor, D. G., Davis, E. C., Boyle, W. A., Mecham, R. P., Stenzel, P., Boak, B. and Keating, M. T. (1998) Novel arterial pathology in mice and humans hemizygous for elastin. J. Clin. Invest. 102, 1783-1787
-
(1998)
J. Clin. Invest
, vol.102
, pp. 1783-1787
-
-
Li, D.Y.1
Faury, G.2
Taylor, D.G.3
Davis, E.C.4
Boyle, W.A.5
Mecham, R.P.6
Stenzel, P.7
Boak, B.8
Keating, M.T.9
-
3
-
-
0030809954
-
Coacervation characteristics of recombinant human tropoelastin
-
Vrhovski, B., Jensen, S. and Weiss, A. S. (1997) Coacervation characteristics of recombinant human tropoelastin. Eur. J. Biochem. 250, 92-98
-
(1997)
Eur. J. Biochem
, vol.250
, pp. 92-98
-
-
Vrhovski, B.1
Jensen, S.2
Weiss, A.S.3
-
4
-
-
0027471980
-
Characterization of lamprin, an unusual matrix protein from lamprey cartilage: Implications for evolution, structure, and assembly of elastin and other fibrillar proteins
-
Robson, P., Wright, G. M., Sitarz, E., Maiti, A., Rawat, M., Youson, J. H. and Keeley, F. W. (1993) Characterization of lamprin, an unusual matrix protein from lamprey cartilage: implications for evolution, structure, and assembly of elastin and other fibrillar proteins. J. Biol. Chem. 268, 1440-1447
-
(1993)
J. Biol. Chem
, vol.268
, pp. 1440-1447
-
-
Robson, P.1
Wright, G.M.2
Sitarz, E.3
Maiti, A.4
Rawat, M.5
Youson, J.H.6
Keeley, F.W.7
-
5
-
-
0036678028
-
The molecular structure of spider dragline silk: Folding and orientation of the protein backbone
-
van Beek, J. D., Hess, S., Vollrath, F. and Meier, B. H. (2002) The molecular structure of spider dragline silk: folding and orientation of the protein backbone. Proc. Natl. Acad. Sci. U.S.A. 99, 10266-10271
-
(2002)
Proc. Natl. Acad. Sci. U.S.A
, vol.99
, pp. 10266-10271
-
-
van Beek, J.D.1
Hess, S.2
Vollrath, F.3
Meier, B.H.4
-
6
-
-
1542281813
-
Sequence and structure determinants for the self-aggregation of recombinant polypeptides modeled after human elastin
-
Miao, M., Bellingham, C. M., Stahl, R. J., Sitarz, E. E., Lane, C. J. and Keeley, F. W. (2003) Sequence and structure determinants for the self-aggregation of recombinant polypeptides modeled after human elastin. J. Biol. Chem. 278, 48553-48562
-
(2003)
J. Biol. Chem
, vol.278
, pp. 48553-48562
-
-
Miao, M.1
Bellingham, C.M.2
Stahl, R.J.3
Sitarz, E.E.4
Lane, C.J.5
Keeley, F.W.6
-
7
-
-
0037705394
-
Domains in tropoelastin that mediate elastin deposition in vitro and in vivo
-
Kozel, B. A., Wachi, H., Davis, E. C. and Mecham, R. P. (2003) Domains in tropoelastin that mediate elastin deposition in vitro and in vivo. J. Biol. Chem. 278, 18491-18498
-
(2003)
J. Biol. Chem
, vol.278
, pp. 18491-18498
-
-
Kozel, B.A.1
Wachi, H.2
Davis, E.C.3
Mecham, R.P.4
-
8
-
-
0346850628
-
Recombinant human elastin polypeptides self-assemble into biomaterials with elastin-like properties
-
Bellingham, C. M., Lillie, M. A., Gosline, J. M., Wright, G. M., Starcher, B. C., Bailey, A. J., Woodhouse, K. A. and Keeley, F. W. (2003) Recombinant human elastin polypeptides self-assemble into biomaterials with elastin-like properties. Biopolymers 70, 445-455
-
(2003)
Biopolymers
, vol.70
, pp. 445-455
-
-
Bellingham, C.M.1
Lillie, M.A.2
Gosline, J.M.3
Wright, G.M.4
Starcher, B.C.5
Bailey, A.J.6
Woodhouse, K.A.7
Keeley, F.W.8
-
9
-
-
0034637534
-
Interaction of tropoelastin with the amino-terminal domains of fibrillin-1 and fibrillin-2 suggests a role for the fibrillins in elastic fiber assembly
-
Trask, T. M., Trask, B. C., Ritty, T. M., Abrams, W. R., Rosenbloom, J. and Mecham, R. P. (2000) Interaction of tropoelastin with the amino-terminal domains of fibrillin-1 and fibrillin-2 suggests a role for the fibrillins in elastic fiber assembly. J. Biol. Chem. 275, 24400-24406
-
(2000)
J. Biol. Chem
, vol.275
, pp. 24400-24406
-
-
Trask, T.M.1
Trask, B.C.2
Ritty, T.M.3
Abrams, W.R.4
Rosenbloom, J.5
Mecham, R.P.6
-
10
-
-
2142850468
-
Molecular basis of elastic fiber formation: Critical interactions and a tropoelastin-fibrillin-1 cross-link
-
Rock, M. J., Cain, S. A., Freeman, L. J., Morgan, A., Mellody, K., Marson, A., Shuttleworth, C. A., Weiss, A. S. and Kielty, C. M. (2004) Molecular basis of elastic fiber formation: critical interactions and a tropoelastin-fibrillin-1 cross-link. J. Biol. Chem. 279, 23748-23758.
-
(2004)
J. Biol. Chem
, vol.279
, pp. 23748-23758
-
-
Rock, M.J.1
Cain, S.A.2
Freeman, L.J.3
Morgan, A.4
Mellody, K.5
Marson, A.6
Shuttleworth, C.A.7
Weiss, A.S.8
Kielty, C.M.9
-
11
-
-
0035955677
-
Protein interaction studies of MAGP-1 with tropoelastin and fibrillin-1
-
Jensen, S. A., Reinhardt, D. P., Gibson, M. A. and Weiss, A. S. (2001) Protein interaction studies of MAGP-1 with tropoelastin and fibrillin-1. J. Biol. Chem. 276, 39661-39666
-
(2001)
J. Biol. Chem
, vol.276
, pp. 39661-39666
-
-
Jensen, S.A.1
Reinhardt, D.P.2
Gibson, M.A.3
Weiss, A.S.4
-
12
-
-
19544386091
-
Fibulin-5 interacts with fibrillin-1 molecules and microfibrils
-
Freeman, L. J., Lomas, A., Hodson, N., Sherratt, M. J., Mellody, K. T., Weiss, A. S., Shuttleworth, C. A. and Kielty, C. M. (2005) Fibulin-5 interacts with fibrillin-1 molecules and microfibrils. Biochem. J. 388, 1-5
-
(2005)
Biochem. J
, vol.388
, pp. 1-5
-
-
Freeman, L.J.1
Lomas, A.2
Hodson, N.3
Sherratt, M.J.4
Mellody, K.T.5
Weiss, A.S.6
Shuttleworth, C.A.7
Kielty, C.M.8
-
13
-
-
0026641004
-
The cysteine residues in the carboxy terminal domain of tropoelastin form an intrachain disulfide bond that stabilizes a loop structure and positively charged pocket
-
Brown, P. L., Mecham, L., Tisdale, C. and Mecham, R. P. (1992) The cysteine residues in the carboxy terminal domain of tropoelastin form an intrachain disulfide bond that stabilizes a loop structure and positively charged pocket. Biochem. Biophys. Res. Commun. 186, 549-555
-
(1992)
Biochem. Biophys. Res. Commun
, vol.186
, pp. 549-555
-
-
Brown, P.L.1
Mecham, L.2
Tisdale, C.3
Mecham, R.P.4
-
14
-
-
0033061145
-
The role of the carboxy terminus of tropoelastin in its assembly into the elastic fiber
-
Hsiao, H., Stone, P. J., Toselli, P., Rosenbloom, J., Franzblau, C. and Schreiber, B. M. (1999) The role of the carboxy terminus of tropoelastin in its assembly into the elastic fiber. Connect. Tissue Res. 40, 83-95
-
(1999)
Connect. Tissue Res
, vol.40
, pp. 83-95
-
-
Hsiao, H.1
Stone, P.J.2
Toselli, P.3
Rosenbloom, J.4
Franzblau, C.5
Schreiber, B.M.6
-
15
-
-
0037144515
-
Microfibril-associated glycoprotein-2 interacts with fibrillin-1 and fibrillin-2 suggesting a role for MAGP-2 in elastic fiber assembly
-
Penner, A. S., Rock, M. J., Kielty, C. M. and Shipley, J. M. (2002) Microfibril-associated glycoprotein-2 interacts with fibrillin-1 and fibrillin-2 suggesting a role for MAGP-2 in elastic fiber assembly. J. Biol. Chem. 277, 35044-35049
-
(2002)
J. Biol. Chem
, vol.277
, pp. 35044-35049
-
-
Penner, A.S.1
Rock, M.J.2
Kielty, C.M.3
Shipley, J.M.4
-
16
-
-
23044517305
-
Coacervation is promoted by molecular interactions between the PF2 segment of fibrillin-1 and the domain 4 region of tropoelastin
-
Clarke, A. W., Wise, S. G., Cain, S. A., Kielty, C. M. and Weiss, A. S. (2005) Coacervation is promoted by molecular interactions between the PF2 segment of fibrillin-1 and the domain 4 region of tropoelastin. Biochemistry 44, 10271-10281
-
(2005)
Biochemistry
, vol.44
, pp. 10271-10281
-
-
Clarke, A.W.1
Wise, S.G.2
Cain, S.A.3
Kielty, C.M.4
Weiss, A.S.5
-
17
-
-
0036308551
-
Connection between elastin haploinsufficiency and increased cell proliferation in patients with supravalvular aortic stenosis and Williams-Beuren syndrome
-
Urban, Z., Riazi, S., Seidl, T. L., Katahira, J., Smoot, L. B., Chitayat, D., Boyd, C. D. and Hinek, A. (2002) Connection between elastin haploinsufficiency and increased cell proliferation in patients with supravalvular aortic stenosis and Williams-Beuren syndrome. Am. J. Hum. Genet. 71, 30-44
-
(2002)
Am. J. Hum. Genet
, vol.71
, pp. 30-44
-
-
Urban, Z.1
Riazi, S.2
Seidl, T.L.3
Katahira, J.4
Smoot, L.B.5
Chitayat, D.6
Boyd, C.D.7
Hinek, A.8
-
18
-
-
0033783405
-
Genetic disorders of the elastic fiber system
-
Milewicz, D. M., Urban, Z. and Boyd, C. (2000) Genetic disorders of the elastic fiber system. Matrix Biol. 19, 471-480
-
(2000)
Matrix Biol
, vol.19
, pp. 471-480
-
-
Milewicz, D.M.1
Urban, Z.2
Boyd, C.3
-
19
-
-
21844459996
-
Development of a new in vitro model of elastic fiber assembly in human pigmented epithelial cells
-
Wachi, H., Sato, F., Murata, H., Nakazawa, J., Starcher, B. C. and Seyama, Y. (2005) Development of a new in vitro model of elastic fiber assembly in human pigmented epithelial cells. Clin. Biochem. 38, 643-653
-
(2005)
Clin. Biochem
, vol.38
, pp. 643-653
-
-
Wachi, H.1
Sato, F.2
Murata, H.3
Nakazawa, J.4
Starcher, B.C.5
Seyama, Y.6
-
20
-
-
0032694642
-
Characterization of an in vitro model of elastic fiber assembly
-
Robb, B. W., Wachi, H., Schaub, T., Mecham, R. P. and Davis, E. C. (1999) Characterization of an in vitro model of elastic fiber assembly. Mol. Biol. Cell 10, 3595-3605
-
(1999)
Mol. Biol. Cell
, vol.10
, pp. 3595-3605
-
-
Robb, B.W.1
Wachi, H.2
Schaub, T.3
Mecham, R.P.4
Davis, E.C.5
-
21
-
-
0032973922
-
Supravalvular aortic stenosis: A splice site mutation within the elastin gene results in reduced expression of two aberrantly spliced transcripts
-
Urban, Z., Michels, V. V., Thibodeau, S. N., Donis-Keller, H., Csiszar, K. and Boyd, C. D. (1999) Supravalvular aortic stenosis: a splice site mutation within the elastin gene results in reduced expression of two aberrantly spliced transcripts. Hum. Genet. 104, 135-142
-
(1999)
Hum. Genet
, vol.104
, pp. 135-142
-
-
Urban, Z.1
Michels, V.V.2
Thibodeau, S.N.3
Donis-Keller, H.4
Csiszar, K.5
Boyd, C.D.6
-
22
-
-
0033605750
-
Processing of the fibrillin-1 carboxyl-terminal domain
-
Ritty, T. M., Broekelmann, T., Tisdale, C., Milewicz, D. M. and Mecham, R. P. (1999) Processing of the fibrillin-1 carboxyl-terminal domain. J. Biol. Chem. 274, 8933-8940
-
(1999)
J. Biol. Chem
, vol.274
, pp. 8933-8940
-
-
Ritty, T.M.1
Broekelmann, T.2
Tisdale, C.3
Milewicz, D.M.4
Mecham, R.P.5
-
23
-
-
0019469264
-
Desmosine radioimmunoassay as a means of studying elastogenesis in cell culture
-
Starcher, B. C. and Mecham, R. P. (1981)Desmosine radioimmunoassay as a means of studying elastogenesis in cell culture. Connect. Tissue Res. 8, 255-258
-
(1981)
Connect. Tissue Res
, vol.8
, pp. 255-258
-
-
Starcher, B.C.1
Mecham, R.P.2
-
24
-
-
33745821612
-
The characteristics of elastic fiber assembled with recombinant tropoelastin isoform
-
Sato, F., Wachi, H., Starcher, B. C., Murata, H., Amano, S., Tajima, S. and Seyama, Y. (2006) The characteristics of elastic fiber assembled with recombinant tropoelastin isoform. Clin. Biochem. 39, 746-753
-
(2006)
Clin. Biochem
, vol.39
, pp. 746-753
-
-
Sato, F.1
Wachi, H.2
Starcher, B.C.3
Murata, H.4
Amano, S.5
Tajima, S.6
Seyama, Y.7
-
25
-
-
0037049996
-
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
-
Yanagisawa, H., Davis, E. C., Starcher, B. C., Ouchi, T., Yanagisawa, M., Richardson, J. A. and Olson, E. N. (2002) Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo. Nature 415, 168-171
-
(2002)
Nature
, vol.415
, pp. 168-171
-
-
Yanagisawa, H.1
Davis, E.C.2
Starcher, B.C.3
Ouchi, T.4
Yanagisawa, M.5
Richardson, J.A.6
Olson, E.N.7
-
26
-
-
0037050030
-
Fibulin-5/DANCE is essential for elastogenesis in vivo
-
Nakamura, T., Lozano, P. R., Ikeda, Y., Iwanaga, Y., Hinek, A., Minamisawa, S., Cheng, C. F., Kobuke, K., Dalton, N., Takada, Y. et al. (2002) Fibulin-5/DANCE is essential for elastogenesis in vivo. Nature 415, 171-175
-
(2002)
Nature
, vol.415
, pp. 171-175
-
-
Nakamura, T.1
Lozano, P.R.2
Ikeda, Y.3
Iwanaga, Y.4
Hinek, A.5
Minamisawa, S.6
Cheng, C.F.7
Kobuke, K.8
Dalton, N.9
Takada, Y.10
-
27
-
-
0028961103
-
The association of human fibulin-1 with elastic fibers: An immunohistological, ultrastructural, and RNA study
-
Roark, E. F., Keene, D. R., Haudenschild, C. C., Godyna, S., Little, C. D. and Argraves, W. S. (1995) The association of human fibulin-1 with elastic fibers: an immunohistological, ultrastructural, and RNA study. J. Histochem. Cytochem. 43, 401-411
-
(1995)
J. Histochem. Cytochem
, vol.43
, pp. 401-411
-
-
Roark, E.F.1
Keene, D.R.2
Haudenschild, C.C.3
Godyna, S.4
Little, C.D.5
Argraves, W.S.6
-
28
-
-
0023696859
-
Cloning of full-length elastin cDNAs from a human skin fibroblast recombinant cDNA library: Further elucidation of alternative splicing utilizing exon-specific oligonucleotides
-
Fazio, M. J., Olsen, D. R., Kauh, E. A., Baldwin, C. T., Indik, Z., Ornstein-Goldstein, N., Yeh, H., Rosenbloom, J. and Uitto, J. (1988) Cloning of full-length elastin cDNAs from a human skin fibroblast recombinant cDNA library: further elucidation of alternative splicing utilizing exon-specific oligonucleotides. J. Invest. Dermatol. 91, 458-464
-
(1988)
J. Invest. Dermatol
, vol.91
, pp. 458-464
-
-
Fazio, M.J.1
Olsen, D.R.2
Kauh, E.A.3
Baldwin, C.T.4
Indik, Z.5
Ornstein-Goldstein, N.6
Yeh, H.7
Rosenbloom, J.8
Uitto, J.9
-
29
-
-
0000263731
-
Alternative splicing of human elastin mRNA indicated by sequence analysis of cloned genomic and complementary DNA
-
Indik, Z., Yeh, H., Ornstein-Goldstein, N., Sheppard, P., Anderson, N., Rosenbloom, J. C., Peltonen, L. and Rosenbloom, J. (1987) Alternative splicing of human elastin mRNA indicated by sequence analysis of cloned genomic and complementary DNA. Proc. Natl. Acad. Sci. U.S.A. 84, 5680-5684
-
(1987)
Proc. Natl. Acad. Sci. U.S.A
, vol.84
, pp. 5680-5684
-
-
Indik, Z.1
Yeh, H.2
Ornstein-Goldstein, N.3
Sheppard, P.4
Anderson, N.5
Rosenbloom, J.C.6
Peltonen, L.7
Rosenbloom, J.8
-
30
-
-
0036713921
-
Homozygosity for a missense mutation in fibulin-5 (FBLN5) results in a severe form of cutis laxa
-
Loeys, B., Van Maldergem, L., Mortier, G., Coucke, P., Gerniers, S., Naeyaert, J. M. and De Paepe, A. (2002) Homozygosity for a missense mutation in fibulin-5 (FBLN5) results in a severe form of cutis laxa. Hum. Mol. Genet 11, 2113-2118
-
(2002)
Hum. Mol. Genet
, vol.11
, pp. 2113-2118
-
-
Loeys, B.1
Van Maldergem, L.2
Mortier, G.3
Coucke, P.4
Gerniers, S.5
Naeyaert, J.M.6
De Paepe, A.7
-
31
-
-
0037185946
-
Elastin as a self-organizing biomaterial: Use of recombinantly expressed human elastin polypeptides as a model for investigations of structure and self-assembly of elastin
-
Keeley, F. W., Bellingham, C. M. and Woodhouse, K. A. (2002) Elastin as a self-organizing biomaterial: use of recombinantly expressed human elastin polypeptides as a model for investigations of structure and self-assembly of elastin. Philos. Trans. R. Soc. London Ser. B 357, 185-189
-
(2002)
Philos. Trans. R. Soc. London Ser. B
, vol.357
, pp. 185-189
-
-
Keeley, F.W.1
Bellingham, C.M.2
Woodhouse, K.A.3
-
32
-
-
27444442269
-
Structural determinants of cross-linking and hydrophobic domains for self-assembly of elastin-like polypeptides
-
Miao, M., Cirulis, J. T., Lee, S. and Keeley, F. W. (2005) Structural determinants of cross-linking and hydrophobic domains for self-assembly of elastin-like polypeptides. Biochemistry 44, 14367-14375
-
(2005)
Biochemistry
, vol.44
, pp. 14367-14375
-
-
Miao, M.1
Cirulis, J.T.2
Lee, S.3
Keeley, F.W.4
-
33
-
-
0022965882
-
Relevance of aggregation properties of tropoelastin to the assembly and structure of elastic fibers
-
Bressan, G. M., Pasquali-Ronchetti, I., Fornieri, C., Mattioli, F., Castellani, I. and Volpin, D. (1986) Relevance of aggregation properties of tropoelastin to the assembly and structure of elastic fibers. J. Ultrastruct. Mol. Struct. Res. 94, 209-216
-
(1986)
J. Ultrastruct. Mol. Struct. Res
, vol.94
, pp. 209-216
-
-
Bressan, G.M.1
Pasquali-Ronchetti, I.2
Fornieri, C.3
Mattioli, F.4
Castellani, I.5
Volpin, D.6
-
34
-
-
0035977033
-
Hydrophobic domains of human tropoelastin interact in a context-dependent manner
-
Toonkool, P., Jensen, S. A., Maxwell, A. L. and Weiss, A. S. (2001) Hydrophobic domains of human tropoelastin interact in a context-dependent manner. J. Biol. Chem. 276, 44575-44580
-
(2001)
J. Biol. Chem
, vol.276
, pp. 44575-44580
-
-
Toonkool, P.1
Jensen, S.A.2
Maxwell, A.L.3
Weiss, A.S.4
-
35
-
-
0033571740
-
Deficient coacervation of two forms of human tropoelastin associated with supravalvular aortic stenosis
-
Wu, W. J. and Weiss, A. S. (1999) Deficient coacervation of two forms of human tropoelastin associated with supravalvular aortic stenosis. Eur. J. Biochem. 266, 308-314
-
(1999)
Eur. J. Biochem
, vol.266
, pp. 308-314
-
-
Wu, W.J.1
Weiss, A.S.2
-
36
-
-
0035176745
-
Supravalvular aortic stenosis: Genetic and molecular dissection of a complex mutation in the elastin gene
-
Urban, Z., Zhang, J., Davis, E. C., Maeda, G. K., Kumar, A., Stalker, H., Belmont, J. W., Boyd, C. D. and Wallace, M. R. (2001) Supravalvular aortic stenosis: genetic and molecular dissection of a complex mutation in the elastin gene. Hum. Genet. 109, 512-520
-
(2001)
Hum. Genet
, vol.109
, pp. 512-520
-
-
Urban, Z.1
Zhang, J.2
Davis, E.C.3
Maeda, G.K.4
Kumar, A.5
Stalker, H.6
Belmont, J.W.7
Boyd, C.D.8
Wallace, M.R.9
-
37
-
-
0033946498
-
Isolated supravalvular aortic stenosis: Functional haploinsufficiency of the elastin gene as a result of nonsense-mediated decay
-
Urban, Z., Michels, V. V., Thibodeau, S. N., Davis, E. C., Bonnefont, J. P., Munnich, A., Eyskens, B., Gewillig, M., Devriendt, K. and Boyd, C. D. (2000) Isolated supravalvular aortic stenosis: functional haploinsufficiency of the elastin gene as a result of nonsense-mediated decay. Hum. Genet. 106, 577-588
-
(2000)
Hum. Genet
, vol.106
, pp. 577-588
-
-
Urban, Z.1
Michels, V.V.2
Thibodeau, S.N.3
Davis, E.C.4
Bonnefont, J.P.5
Munnich, A.6
Eyskens, B.7
Gewillig, M.8
Devriendt, K.9
Boyd, C.D.10
|