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Volumn 26, Issue 6, 2006, Pages 445-449

Pulmonary fibrosis in Hermansky-Pudlak syndrome is not fully usual;La fibrose pulmonaire du syndrome de Hermansky Pudlak n'est pas totalement commune

Author keywords

Hermansky Pudlak syndrome; Interstitial pneumonia; Pulmonary fibrosis

Indexed keywords

ADULT; ARTICLE; CASE REPORT; CLINICAL FEATURE; DISEASE ASSOCIATION; DISEASE COURSE; FEMALE; HISTOPATHOLOGY; HUMAN; LUNG FIBROSIS; LUNG TRANSPLANTATION; OCULAR ALBINISM; TREATMENT OUTCOME;

EID: 33846257577     PISSN: 02426498     EISSN: None     Source Type: Journal    
DOI: 10.1016/s0242-6498(06)70753-2     Document Type: Article
Times cited : (8)

References (9)
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    • Pulmonary function and high-resolution CT findings in patients with an inherited form of pulmonary fibrosis, Hermansky-Pudlak syndrome, due to mutations in HPS-1
    • Brantly M, Avila NA, Shotelersuk V, Lucero C, Huizing M, Gahl WA. Pulmonary function and high-resolution CT findings in patients with an inherited form of pulmonary fibrosis, Hermansky-Pudlak syndrome, due to mutations in HPS-1. Chest 2000 ; 117 : 129-36.
    • (2000) Chest , vol.117 , pp. 129-136
    • Brantly, M.1    Avila, N.A.2    Shotelersuk, V.3    Lucero, C.4    Huizing, M.5    Gahl, W.A.6
  • 3
    • 0033829367 scopus 로고    scopus 로고
    • Interstitial pneumonia in Hermansky-Pudlak syndrome: Significance of florid foamy swelling/degeneration (giant lamellar body degeneration) of type-2 pneumocytes
    • Nakatani Y, Nakamura N, Sano J, Inayama Y, Kawano N, Yamanaka S et al. Interstitial pneumonia in Hermansky-Pudlak syndrome: significance of florid foamy swelling/degeneration (giant lamellar body degeneration) of type-2 pneumocytes. Virchows Arch 2000 ; 437 : 304-13.
    • (2000) Virchows Arch , vol.437 , pp. 304-313
    • Nakatani, Y.1    Nakamura, N.2    Sano, J.3    Inayama, Y.4    Kawano, N.5    Yamanaka, S.6
  • 4
    • 0036783758 scopus 로고    scopus 로고
    • Hermansky-Pudlak syndrome: Radiography and CT of the chest compared with pulmonary function tests and genetic studies
    • Avila NA, Brantly M, Premkumar A, Huizing M, Dwyer A, Galh WA. Hermansky-Pudlak syndrome: radiography and CT of the chest compared with pulmonary function tests and genetic studies. Am J Roentgenol 2002 ; 179 : 887-92.
    • (2002) Am J Roentgenol , vol.179 , pp. 887-892
    • Avila, N.A.1    Brantly, M.2    Premkumar, A.3    Huizing, M.4    Dwyer, A.5    Galh, W.A.6
  • 5
    • 21044448584 scopus 로고    scopus 로고
    • The cell biology of Hermansky-Pudlak syndrome: Recent advances
    • Di Pietro SM, Dell'Angelica EC. The cell biology of Hermansky-Pudlak syndrome: recent advances. Traffic 2005 ; 6 : 525-33.
    • (2005) Traffic , vol.6 , pp. 525-533
    • Di Pietro, S.M.1    Dell'Angelica, E.C.2
  • 6
    • 0029563692 scopus 로고
    • Hermansky-Pudlak syndrome; a case report with analysis of auto-fluorescent ceroid-like pigments
    • Ohbayashi C, Kanomata N, Imai Y, Ito H, Shimasaki H. Hermansky-Pudlak syndrome; a case report with analysis of auto-fluorescent ceroid-like pigments. Gerontology 1995 ; 41 : 297-303.
    • (1995) Gerontology , vol.41 , pp. 297-303
    • Ohbayashi, C.1    Kanomata, N.2    Imai, Y.3    Ito, H.4    Shimasaki, H.5
  • 7
    • 0021256435 scopus 로고
    • Hermansky-Pudlak syndrome and interstitial lung disease: Report of a case with lavage findings
    • White DA, Smith GJW, Cooper JAD, Glickstein M, Rankin JA. Hermansky-Pudlak syndrome and interstitial lung disease: report of a case with lavage findings. Am Rev Resp Dis 1984 ; 130 : 138-41.
    • (1984) Am Rev Resp Dis , vol.130 , pp. 138-141
    • White, D.A.1    Smith, G.J.W.2    Cooper, J.A.D.3    Glickstein, M.4    Rankin, J.A.5
  • 9
    • 21644432169 scopus 로고    scopus 로고
    • Shared mechanisms of lung injury and subsequent fibrosis: Role of surfactant proteins in the pathogenesis of interstitial pneumonia in Hermansky-Pudlak syndrome
    • Azuma A. Shared mechanisms of lung injury and subsequent fibrosis: role of surfactant proteins in the pathogenesis of interstitial pneumonia in Hermansky-Pudlak syndrome. Intern Med 2005 ; 44 : 529-30.
    • (2005) Intern Med , vol.44 , pp. 529-530
    • Azuma, A.1


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.