Revised King's College score for liver transplantation in adult patients with Wilson's disease

Liver Transplantation

Volumn 13, Issue 1, 2007, Pages 55-61

  Petrasek, Jan ^a   Jirsa, Milan ^a,b   Sperl, Jan ^a   Kozak, Libor ^c   Taimr, Pavel ^a   Spicak, Julius ^a   Filip, Karel ^a   Trunecka, Pavel ^a  

^a INSTITUTE FOR CLINICAL AND EXPERIMENTAL MEDICINE   (Czech Republic)

^b CHARLES UNIVERSITY   (Czech Republic)

^c Center of Molecular Biology and Gene Therapy   (Czech Republic)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER; PENICILLAMINE;

ACCURACY; ADULT; AGED; ARTICLE; CALCULATION; CHELATION THERAPY; CHRONIC DISEASE; CLINICAL ARTICLE; CLINICAL PROTOCOL; CONTROLLED STUDY; DIAGNOSTIC PROCEDURE; FEMALE; GENE MUTATION; HUMAN; LIVER FAILURE; LIVER TRANSPLANTATION; MALE; PREDICTION; PRIORITY JOURNAL; PROGNOSIS; SCORING SYSTEM; URINARY EXCRETION; WILSON DISEASE;

ADOLESCENT; ADULT; AGED; COPPER; DNA MUTATIONAL ANALYSIS; FEMALE; GENOTYPE; HEPATOLENTICULAR DEGENERATION; HUMANS; LIVER; LIVER FAILURE; LIVER TRANSPLANTATION; MALE; MIDDLE AGED; MUTATION; PROGNOSIS; RETROSPECTIVE STUDIES; TREATMENT OUTCOME;

EID: 33846234693     PISSN: 15276465     EISSN: 15276473     Source Type: Journal    
DOI: 10.1002/lt.20920     Document Type: Article

References (22)

1. Roberts EA. Schilsky ML. A practice guideline on Wilson disease. Hepatology. 2003;37:1475-1492.
2. Steindl P. Ferenci P. Dienes HP, Grimm G, Pabinger I, Madl C, et al. Wilson's disease in patients presenting with liver disease: a diagnostic challenge. Gastroenterology 1997; 113:212-218.
3. Gow PJ, Smallwood RA, Angus PW, Smith AL, Wall AJ, Sewell RB. Diagnosis of Wilson's disease: an experience over three decades. Gut 2000;46:415-419.
4. Durand F, Bernuau J, Giostra. E. Mentha G, Shouval D, Degott C, et al. Wilson's disease with severe hepatic insufficiency: beneficial effects of early administration of D-penicillamine. Gut 2001;48:849-852.
5. Berman DH, Leventhal RI, Gavaler JS, Cadoff EM, Van Thiel DH. Clinical differentiation of fulminant Wilsonian hepatitis from other causes of hepatic failure. Gastroenterology 1991;100:1129-1134.
6. Sallie R, Katsiyiannakis L, Baldwin D, Davis S. O'Grady J, Mowat A. et al. Failure of simple biochemical indexes to reliably differentiate fulminant Wilson's disease from other causes of fulminant liver failure. Hepatology 1992:16: 1206-1211.
7. Nazer H, Ede RJ, Mowat AP, Williams R. Wilson's disease: clinical presentation and use of prognostic index. Gut 1986;27:1377-1381.
8. Dhawan A, Taylor RM, Cheeseman P, De Silva P, Katsiyiannakis L, Mieli-Vergani G. Wilson's disease in children: 37-year experience and revised King's score for liver transplantation. Liver Transpl 2005; 11:441-448.
9. Kamath PS, Wiesner RH, Malinchoc M, Kremers W, Therneau TM, Kosberg CL, et al. A model to predict survival in patients with end-stage liver disease. Hepatology 2001;33: 464-470.
10. Yantorno SET, Trentadue JJ, Ruf AE. The model for endstage liver disease (MELD): a useful tool to assess prognosis in fulminant hepatic failure. Liver Transpl 2004; 10(suppl):C36.
11. Wiesner RH. MELD/PELD and the allocation of deceased donor livers for status 1 recipients with acute fulminant hepatic failure, primary nonfunction. hepatic artery thrombosis, and acute Wilson's disease. Liver Transpl 2004;10(suppl 2):S17-S22.
12. Vrabelova S, Letocha O, Borsky M, Kozak L. Mutation analysis of the ATP7B gene and genotype/phenotype correlation in 227 patients with Wilson disease. Mol Genet Metab 2005;86:277-285.
13. O'Grady JG, Alexander GJ, Hayllar KM, Williams R. Early indicators of prognosis in fulminant hepatic failure. Gastroenterology 1989;97:439-445.
14. Schilsky ML. Identification of the Wilson's disease gene: clues for disease pathogenesis and the potential for molecular diagnosis. Hepatology 1994;20:529-533.
15. Kasai N, Miyoshi I. Osanai T. Yamashita T. Kamimura E, Yoshida MC. Effects of sex hormones on fulminant hepatitis in LEC rats: a model of Wilson's disease. Lab Anim Sci 1992;42:363-368.
16. Schilsky ML, Scheinberg IH, Sternlieb I. Liver tunsplantation for Wilson's disease: indications and outcome. Hepatology 1994; 19:583-587.
17. Schilsky ML, Scheinberg IH, Sternlieb I. Prognosis of Wilsonian chronic active hepatitis. Gastroenterology 1991; 100:762-767.
18. McCullough AJ, Fleming CR, Thistle JL, Baldus WP, Ludwing J, McCall JT, Dickson ER. Diagnosis of Wilson's disease presenting as fulminant hepatic failure. Gastroenterology 1983:84:161-167.
19. Brewer GJ. Diagnosis of Wilson's disease: an experience over three decades. Gut 2002;50:136.
20. Case records of the Massachusetts General Hospital. Weekly clinicopathological exercises. Case I-1997. A 23-year-old man with fulminant hepatorenal failure of uncertain cause. N Engl J Med 1997;336:118-125.
21. Shaver WA, Bhatt H, Combes B. Low serum alkaline phosphatase activity in Wilson's disease. Hepatology 1986;6: 859-863.
22. Schilsky ML. Diagnosis and treatment of Wilson's disease. Pediatr Transplant 2002;6:15-19.