Copper- and iron-rich matrices in hepatocellular lipofuscin particles of a young male patient: Diagnostic ultrastructures for Wilson disease

Ultrastructural Pathology

Volumn 30, Issue 6, 2006, Pages 409-414

  Motonishi, Satoshi ^a   Hayashi, Hisao ^b,e   Fujita, Yoshikazu ^c   Okada, Hidetoshi ^a   Kusakabe, Atsuhiko ^d   Ito, Masafumi ^d   Miyamoto, Kenichi ^a   Ueno, Toshio ^b  

^a KANAZAWA UNIVERSITY   (Japan)

^b Asanogawa General Hospital   (Japan)

^c NAGOYA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^d JAPANESE RED CROSS NAGOYA FIRST HOSPITAL   (Japan)

^e Asanogawa General Hospital   (Japan)

Author keywords

ATP7B; Ceruloplasmin; Hemosiderin; HFE; Lysosome; Metallothionein

Indexed keywords

CERULOPLASMIN; COPPER; EPOXY RESIN; IRON; LIPOFUSCIN; OSMIUM TETRAOXIDE; PHOSPHORUS; SULFUR;

ADULT; ARTICLE; CASE REPORT; DETOXIFICATION; GENE MUTATION; GENETIC ANALYSIS; HETEROZYGOSITY; HISTOCHEMISTRY; HUMAN; HUMAN CELL; HUMAN TISSUE; INTOXICATION; IRON OVERLOAD; LIVER CELL; LIVER INJURY; MALE; PRIORITY JOURNAL; STAINING; ULTRASTRUCTURE; WILSON DISEASE; X RAY MICROANALYSIS;

ADENOSINE TRIPHOSPHATASES; ADOLESCENT; CATION TRANSPORT PROTEINS; CERULOPLASMIN; COPPER; ELECTRON PROBE MICROANALYSIS; HEPATOCYTES; HEPATOLENTICULAR DEGENERATION; HISTOCOMPATIBILITY ANTIGENS CLASS I; HISTOCYTOCHEMISTRY; HUMANS; IMMUNOHISTOCHEMISTRY; INCLUSION BODIES; IRON; LIPOFUSCIN; MALE; MEMBRANE PROTEINS; MICROSCOPY, ELECTRON, TRANSMISSION; MUTATION;

EID: 33845871698     PISSN: 01913123     EISSN: 15210758     Source Type: Journal    
DOI: 10.1080/01913120600854327     Document Type: Article

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