-
1
-
-
0842281643
-
Mammalian prion biology: one century of evolving concepts
-
Aguzzi A., and Polymenidou M. Mammalian prion biology: one century of evolving concepts. Cell 116 (2004) 313-327
-
(2004)
Cell
, vol.116
, pp. 313-327
-
-
Aguzzi, A.1
Polymenidou, M.2
-
2
-
-
0025304678
-
Scrapie and cellular prion proteins differ in their kinetics of synthesis and topology in cultured cells
-
Borchelt D.R., Scott M., Taraboulos A., Stahl N., and Prusiner S.B. Scrapie and cellular prion proteins differ in their kinetics of synthesis and topology in cultured cells. J. Cell Biol. 110 (1990) 743-752
-
(1990)
J. Cell Biol.
, vol.110
, pp. 743-752
-
-
Borchelt, D.R.1
Scott, M.2
Taraboulos, A.3
Stahl, N.4
Prusiner, S.B.5
-
3
-
-
0035914410
-
Prion protein protects human neurons against bax-mediated apoptosis
-
Bounhar Y., Zhang Y., Goodyer C., and LeBlanc A. Prion protein protects human neurons against bax-mediated apoptosis. J. Biol. Chem. 276 (2001) 39145-39149
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 39145-39149
-
-
Bounhar, Y.1
Zhang, Y.2
Goodyer, C.3
LeBlanc, A.4
-
4
-
-
0030054010
-
Normal host prion protein necessary for scrapie-induced neurotoxicity
-
Brandner S., Isenmann S., Raeber A., Fischer M., Sailer A., Kobayashi Y., Marino S., Weissmann C., and Aguzzi A. Normal host prion protein necessary for scrapie-induced neurotoxicity. Nature 379 (1996) 339-343
-
(1996)
Nature
, vol.379
, pp. 339-343
-
-
Brandner, S.1
Isenmann, S.2
Raeber, A.3
Fischer, M.4
Sailer, A.5
Kobayashi, Y.6
Marino, S.7
Weissmann, C.8
Aguzzi, A.9
-
5
-
-
0037080043
-
Lack of prion protein expression results in a neuronal phenotype sensitive to stress
-
Brown D., Nicholas R., and Canevari L. Lack of prion protein expression results in a neuronal phenotype sensitive to stress. J. Neurosci. Res. 67 (2002) 211-224
-
(2002)
J. Neurosci. Res.
, vol.67
, pp. 211-224
-
-
Brown, D.1
Nicholas, R.2
Canevari, L.3
-
6
-
-
0024545093
-
Prion protein biosynthesis in scrapie-infected and uninfected neuroblastoma cells
-
Caughey B., Race R.E., Ernst D., Buchmeier M.J., and Chesebro B. Prion protein biosynthesis in scrapie-infected and uninfected neuroblastoma cells. J. Virol. 63 (1989) 175-181
-
(1989)
J. Virol.
, vol.63
, pp. 175-181
-
-
Caughey, B.1
Race, R.E.2
Ernst, D.3
Buchmeier, M.J.4
Chesebro, B.5
-
7
-
-
20344394154
-
Anchorless prion protein results in infectious amyloid disease without clinical scrapie
-
Chesebro B., Trifilo M., Race R., Meade-White K., Teng C., LaCasse R., Raymond L., Favara C., Baron G., Priola S., Caughey B., Masliah E., and Oldstone M. Anchorless prion protein results in infectious amyloid disease without clinical scrapie. Science 308 (2005) 1435-1439
-
(2005)
Science
, vol.308
, pp. 1435-1439
-
-
Chesebro, B.1
Trifilo, M.2
Race, R.3
Meade-White, K.4
Teng, C.5
LaCasse, R.6
Raymond, L.7
Favara, C.8
Baron, G.9
Priola, S.10
Caughey, B.11
Masliah, E.12
Oldstone, M.13
-
8
-
-
11844296730
-
Bax deletion prevents neuronal loss but not neurological symptoms in a transgenic model of inherited prion disease
-
Chiesa R., Piccardo P., Dossena S., Nowoslawski L., Roth K.A., Ghetti B., and Harris D.A. Bax deletion prevents neuronal loss but not neurological symptoms in a transgenic model of inherited prion disease. Proc. Natl Acad. Sci. USA 102 (2005) 238-243
-
(2005)
Proc. Natl Acad. Sci. USA
, vol.102
, pp. 238-243
-
-
Chiesa, R.1
Piccardo, P.2
Dossena, S.3
Nowoslawski, L.4
Roth, K.A.5
Ghetti, B.6
Harris, D.A.7
-
9
-
-
0028338441
-
Structural clues to prion replication
-
Cohen F.E., Huang Z., Fletterick R.J., Baldwin M., and Prusiner S.B. Structural clues to prion replication. Science 264 (1994) 530-531
-
(1994)
Science
, vol.264
, pp. 530-531
-
-
Cohen, F.E.1
Huang, Z.2
Fletterick, R.J.3
Baldwin, M.4
Prusiner, S.B.5
-
10
-
-
8844247180
-
Mechanism of prion propagation: amyloid growth occurs by monomer addition
-
Collins S., Douglass A., Vale R., and Weissman J. Mechanism of prion propagation: amyloid growth occurs by monomer addition. PLOSBio 2 (2004) 1582-1590
-
(2004)
PLOSBio
, vol.2
, pp. 1582-1590
-
-
Collins, S.1
Douglass, A.2
Vale, R.3
Weissman, J.4
-
11
-
-
0030579560
-
Prionics or the kinetic basis of prion diseases
-
Eigen M. Prionics or the kinetic basis of prion diseases. Biophys. Chem. 63 (1996) 11-18
-
(1996)
Biophys. Chem.
, vol.63
, pp. 11-18
-
-
Eigen, M.1
-
12
-
-
33747891073
-
-
Engler, H., Prüss, J., Webb, G.F., 2006. Analysis of a model for the dynamics of prions II, in press.
-
-
-
-
13
-
-
0042709768
-
Stochastic modeling approach to the incubation time of prionic diseases
-
Ferreira A.S., da Silva M.A., and Cressoni J.C. Stochastic modeling approach to the incubation time of prionic diseases. Phys. Rev. Lett. 90 (2003) 198101-198104
-
(2003)
Phys. Rev. Lett.
, vol.90
, pp. 198101-198104
-
-
Ferreira, A.S.1
da Silva, M.A.2
Cressoni, J.C.3
-
14
-
-
2942616602
-
Evidence for assembly of prions with left-handed β-helices into trimers
-
Govaerts C., Wille H., Prusiner S.B., and Cohen F.E. Evidence for assembly of prions with left-handed β-helices into trimers. Proc. Natl Acad. Sci. 101 (2004) 8342-8347
-
(2004)
Proc. Natl Acad. Sci.
, vol.101
, pp. 8342-8347
-
-
Govaerts, C.1
Wille, H.2
Prusiner, S.B.3
Cohen, F.E.4
-
15
-
-
33747886557
-
-
Greer, M.L., 2002. A population model of prion dynamics. Ph.D. Thesis, Vanderbilt University.
-
-
-
-
16
-
-
0014190760
-
Nature of the scrapie agent
-
Griffith J.S. Nature of the scrapie agent. Nature 215 (1967) 1043-1044
-
(1967)
Nature
, vol.215
, pp. 1043-1044
-
-
Griffith, J.S.1
-
18
-
-
0030908095
-
Models of amyloid seeding in Alzheimer's disease and scrapie: mechanistic truths and physiological consequences of the time-dependent solubility of amyloid proteins
-
Harper J.D., and Lansbury P.T. Models of amyloid seeding in Alzheimer's disease and scrapie: mechanistic truths and physiological consequences of the time-dependent solubility of amyloid proteins. Ann. Rev. Biochem. 66 (1997) 385-407
-
(1997)
Ann. Rev. Biochem.
, vol.66
, pp. 385-407
-
-
Harper, J.D.1
Lansbury, P.T.2
-
19
-
-
0030728039
-
Deadly conformations: protein misfolding in prion disease
-
Horwich A.L., and Weissman J.S. Deadly conformations: protein misfolding in prion disease. Cell 89 (1997) 499-510
-
(1997)
Cell
, vol.89
, pp. 499-510
-
-
Horwich, A.L.1
Weissman, J.S.2
-
20
-
-
33747878116
-
Proposed three-dimensional structure for the cellular prion protein
-
Huang Z.W., Gabriel J.M., Baldwin M.A., Fletterick R.J., Prusiner S.B., and ECohen F. Proposed three-dimensional structure for the cellular prion protein. Proc. Natl Acad. Sci. USA 47 (1984) 71-79
-
(1984)
Proc. Natl Acad. Sci. USA
, vol.47
, pp. 71-79
-
-
Huang, Z.W.1
Gabriel, J.M.2
Baldwin, M.A.3
Fletterick, R.J.4
Prusiner, S.B.5
ECohen, F.6
-
21
-
-
0027195933
-
Seeding "one-dimensional crystallization" of smyloid: a pathogenic mechanism in Alzheimer's disease and scrapie?
-
Jarrett J.T., and Lansbury P.T. Seeding "one-dimensional crystallization" of smyloid: a pathogenic mechanism in Alzheimer's disease and scrapie?. Cell 73 (1993) 1055-1058
-
(1993)
Cell
, vol.73
, pp. 1055-1058
-
-
Jarrett, J.T.1
Lansbury, P.T.2
-
22
-
-
1942485480
-
The cellular prion protein (prpc) prevents apoptotic neuronal cell death and mitochondrial dysfunction induced by serum deprivation
-
Kim B.H., Lee H.G., Choi J.K., Kim J.I., Choi E.K., Carp R.I., and Kim Y.S. The cellular prion protein (prpc) prevents apoptotic neuronal cell death and mitochondrial dysfunction induced by serum deprivation. Mol. Brain Res. 124 (2004) 40-50
-
(2004)
Mol. Brain Res.
, vol.124
, pp. 40-50
-
-
Kim, B.H.1
Lee, H.G.2
Choi, J.K.3
Kim, J.I.4
Choi, E.K.5
Carp, R.I.6
Kim, Y.S.7
-
23
-
-
0041343119
-
Theoretical modeling of prion disease incubation
-
Kulkarni R.V., Slepoy A., Singh R.R.P., Cox D.L., and Pázmándi F. Theoretical modeling of prion disease incubation. Biophys. J. 85 (2003) 707-718
-
(2003)
Biophys. J.
, vol.85
, pp. 707-718
-
-
Kulkarni, R.V.1
Slepoy, A.2
Singh, R.R.P.3
Cox, D.L.4
Pázmándi, F.5
-
24
-
-
0029110883
-
The chemistry of scrapie infection: implication of the "ice 9" metaphor
-
Lansbury P., and Caughey B. The chemistry of scrapie infection: implication of the "ice 9" metaphor. Chem. Biol. 2 (1981) 1-5
-
(1981)
Chem. Biol.
, vol.2
, pp. 1-5
-
-
Lansbury, P.1
Caughey, B.2
-
25
-
-
0031582232
-
Autocatalytic processes in cooperative mechanisms of prion diseases
-
Laurent M. Autocatalytic processes in cooperative mechanisms of prion diseases. FEBS Lett. 407 (1997) 1-6
-
(1997)
FEBS Lett.
, vol.407
, pp. 1-6
-
-
Laurent, M.1
-
26
-
-
20444454586
-
Mammalian prion protein suppresses bax-induced cell death in yeast
-
Li A., and Harris D.A. Mammalian prion protein suppresses bax-induced cell death in yeast. J. Biol. Chem. 280 (2005) 17430-17434
-
(2005)
J. Biol. Chem.
, vol.280
, pp. 17430-17434
-
-
Li, A.1
Harris, D.A.2
-
28
-
-
0032968132
-
Quantifying the kinetic parameters of prion replication
-
Masel J., Jansen V.A.A., and Nowak M.S. Quantifying the kinetic parameters of prion replication. Biophys. Chem. 77 (1999) 139-152
-
(1999)
Biophys. Chem.
, vol.77
, pp. 139-152
-
-
Masel, J.1
Jansen, V.A.A.2
Nowak, M.S.3
-
30
-
-
0141530993
-
Simulations of oligomeric intermediates in prion diseases
-
Mobley D.L., Cox D.L., Singh R.R., Kulkarni R.V., and Slepoy A. Simulations of oligomeric intermediates in prion diseases. Biophys. J. 85 (2003) 2213-2223
-
(2003)
Biophys. J.
, vol.85
, pp. 2213-2223
-
-
Mobley, D.L.1
Cox, D.L.2
Singh, R.R.3
Kulkarni, R.V.4
Slepoy, A.5
-
32
-
-
0022005315
-
A cellular gene encodes scrapie prp 27-30 protein
-
Oesch B., Westaway D., Walchli M., McKinley M.P., Kent S.B.H., Aebersold R., Barry R.A., Tempst P., Teplow D.B., Hood L.E., Prusiner S.B., and Weissmann C. A cellular gene encodes scrapie prp 27-30 protein. Cell 40 (1985) 735-746
-
(1985)
Cell
, vol.40
, pp. 735-746
-
-
Oesch, B.1
Westaway, D.2
Walchli, M.3
McKinley, M.P.4
Kent, S.B.H.5
Aebersold, R.6
Barry, R.A.7
Tempst, P.8
Teplow, D.B.9
Hood, L.E.10
Prusiner, S.B.11
Weissmann, C.12
-
33
-
-
0027332116
-
Conversion of α-helices into β-sheets features in the formation of the scrapie prion proteins
-
Pan K.M., Baldwin M., Nguyen J., Gasset M., Serban A., Groth D., IlMelhorn S., Huang Z., Fletterick R.J., Cohen F.E., and Prusiner S.B. Conversion of α-helices into β-sheets features in the formation of the scrapie prion proteins. Proc. Natl Acad. Sci. USA 90 (1993) 10962-10966
-
(1993)
Proc. Natl Acad. Sci. USA
, vol.90
, pp. 10962-10966
-
-
Pan, K.M.1
Baldwin, M.2
Nguyen, J.3
Gasset, M.4
Serban, A.5
Groth, D.6
IlMelhorn, S.7
Huang, Z.8
Fletterick, R.J.9
Cohen, F.E.10
Prusiner, S.B.11
-
35
-
-
0020321767
-
Novel proteinaceous infectious particles cause scrapie
-
Prusiner S.B. Novel proteinaceous infectious particles cause scrapie. Science 216 (1982) 136-144
-
(1982)
Science
, vol.216
, pp. 136-144
-
-
Prusiner, S.B.1
-
36
-
-
85036438709
-
Prions
-
Prusiner S.B. Prions. Sci. Am. 4 (1986) 50-59
-
(1986)
Sci. Am.
, vol.4
, pp. 50-59
-
-
Prusiner, S.B.1
-
37
-
-
0025910229
-
Molecular biology of prion diseases
-
Prusiner S.B. Molecular biology of prion diseases. Science 252 (1991) 1515-1522
-
(1991)
Science
, vol.252
, pp. 1515-1522
-
-
Prusiner, S.B.1
-
39
-
-
2442490085
-
Scrapie agent contains a hydrophobic protein
-
Prusiner S.B., McKinley M.P., Groth D.F., Bowman K.A., Mock N.I., Cochran S.P., and Masiarz F.R. Scrapie agent contains a hydrophobic protein. Proc. Natl Acad. Sci. USA 78 (1981) 6675-6679
-
(1981)
Proc. Natl Acad. Sci. USA
, vol.78
, pp. 6675-6679
-
-
Prusiner, S.B.1
McKinley, M.P.2
Groth, D.F.3
Bowman, K.A.4
Mock, N.I.5
Cochran, S.P.6
Masiarz, F.R.7
-
40
-
-
0021752457
-
Purification and structural studies of a major scrapie prion protein
-
Prusiner S.B., Groth D.F., Bolton D.C., Kent S.B., and Hood L.E. Purification and structural studies of a major scrapie prion protein. Cell 38 (1984) 127-134
-
(1984)
Cell
, vol.38
, pp. 127-134
-
-
Prusiner, S.B.1
Groth, D.F.2
Bolton, D.C.3
Kent, S.B.4
Hood, L.E.5
-
41
-
-
33644529127
-
Analysis of a model for the dynamics of prions
-
Prüss J., Pujo-Menjouet L., Webb G.F., and Zacher R. Analysis of a model for the dynamics of prions. Discrete Control Dyn. Syst. Ser. B 6 1 (2006) 215-225
-
(2006)
Discrete Control Dyn. Syst. Ser. B
, vol.6
, Issue.1
, pp. 215-225
-
-
Prüss, J.1
Pujo-Menjouet, L.2
Webb, G.F.3
Zacher, R.4
-
42
-
-
0142135128
-
Cytosolic prion protein is not toxic and protects against bax-mediated cell death in human primary neurons
-
Roucou X., Guo Q., Zhang Y., Goodyer C.G., and Leblanc A. Cytosolic prion protein is not toxic and protects against bax-mediated cell death in human primary neurons. J. Biol. Chem. 278 (2003) 40877-40881
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 40877-40881
-
-
Roucou, X.1
Guo, Q.2
Zhang, Y.3
Goodyer, C.G.4
Leblanc, A.5
-
44
-
-
0026094433
-
Scrapie-infected spleens: analysis of infectivity, scrapie-associated fibrils, and protease-resistant proteins
-
Rubenstein R., Merz P.A., Kascsak R.J., Scalici C.L., Papini M.C., Carp R.I., and Kimberlin R.H. Scrapie-infected spleens: analysis of infectivity, scrapie-associated fibrils, and protease-resistant proteins. J. Infect. Dis. 164 (1991) 29-35
-
(1991)
J. Infect. Dis.
, vol.164
, pp. 29-35
-
-
Rubenstein, R.1
Merz, P.A.2
Kascsak, R.J.3
Scalici, C.L.4
Papini, M.C.5
Carp, R.I.6
Kimberlin, R.H.7
-
45
-
-
0035814918
-
Bidirectional amyloid fiber growth for a yeast prion determinant
-
Scheibel T., Kowal A.S., Bloom J.D., and Lindquist S.L. Bidirectional amyloid fiber growth for a yeast prion determinant. Curr. Biol. 11 (2001) 366-369
-
(2001)
Curr. Biol.
, vol.11
, pp. 366-369
-
-
Scheibel, T.1
Kowal, A.S.2
Bloom, J.D.3
Lindquist, S.L.4
-
46
-
-
33747874816
-
On the statistical mechanics of prion proteins
-
Slepoy A., Kulkarni R.V., Singh R.R.P., Pázmándi F., and Cox D.L. On the statistical mechanics of prion proteins. Phys. Rev. Lett. 87 (2001) 8101-8104
-
(2001)
Phys. Rev. Lett.
, vol.87
, pp. 8101-8104
-
-
Slepoy, A.1
Kulkarni, R.V.2
Singh, R.R.P.3
Pázmándi, F.4
Cox, D.L.5
-
47
-
-
0037133587
-
Structural studies of the scrapie prion protein by electron crystallography
-
Wille H., Michelitsch M.D., Guenebaut V., Supattapone S., Serban A., Cohen F.E., Agard D.A., and Prusiner S.B. Structural studies of the scrapie prion protein by electron crystallography. Proc. Natl Acad. Sci. USA 99 (2002) 3563-3568
-
(2002)
Proc. Natl Acad. Sci. USA
, vol.99
, pp. 3563-3568
-
-
Wille, H.1
Michelitsch, M.D.2
Guenebaut, V.3
Supattapone, S.4
Serban, A.5
Cohen, F.E.6
Agard, D.A.7
Prusiner, S.B.8
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