Deficient activity of von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura in the setting of adult-onset Still's disease [5]

Rheumatology

Volumn 45, Issue 8, 2006, Pages 1046-1047

  Hirata, S ^a   Okamoto, H ^a   Ohta, S ^a   Kobashigawa, T ^a   Uesato, M ^a   Kawaguchi, Y ^a   Tateishi, M ^a   Hara, M ^a   Kamatani, N ^a   Tsai, H M ^b  

^a TOKYO WOMEN'S MEDICAL UNIVERSITY   (Japan)

^b ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYLSALICYLIC ACID; CORTICOSTEROID; CYCLOSPORIN A; METHOTREXATE; METHYLPREDNISOLONE; PENICILLAMINE; PREDNISOLONE; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ADULT; ADULT ONSET STILL DISEASE; CASE REPORT; DISEASE ASSOCIATION; DISEASE CONTROL; DISEASE EXACERBATION; DRUG MEGADOSE; DRUG WITHDRAWAL; ENZYME ACTIVITY; FEMALE; FEVER; FOLLOW UP; HEMATURIA; HEMOLYTIC ANEMIA; HOSPITAL ADMISSION; HOSPITAL DISCHARGE; HUMAN; LETTER; LOW DRUG DOSE; NAUSEA; PETECHIA; PLASMAPHERESIS; PRIORITY JOURNAL; THROMBOTIC THROMBOCYTOPENIC PURPURA; UNSPECIFIED SIDE EFFECT; VOMITING;

ADAM PROTEINS; ADULT; AUTOIMMUNE DISEASES; FEMALE; HUMANS; PURPURA, THROMBOTIC THROMBOCYTOPENIC; STILL'S DISEASE, ADULT-ONSET;

EID: 33747835305     PISSN: 14620324     EISSN: 14620332     Source Type: Journal    
DOI: 10.1093/rheumatology/kel176     Document Type: Letter

References (8)

1. Wakai K, Ohta A, Tamakoshi A et al. Estimated prevalence and incidence of adult Still's disease: Findings by a nationwide epidemio-logical survey in Japan. J Epidemiol 1997;7:221-5.
2. Tsai HM, Lian EC. Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura. N Engl J Med 1998;339:1585-94.
3. Furlan M, Robles R, Galbusera M et al. von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome. N Engl J Med 1998;339:1578-84.
4. Levy GG, Nichols WC, Lian EC et al. Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura. Nature 2001;413:488-94.
5. Musio F, Bohen EM, Yuan CM, Welch PG. Review of thrombotic thrombocytopenic purpura in the setting of systemic lupus erythematosus. Semin Arthritis Rheum 1998;28:1-19.
6. Manadan AM, Harris C, Block JA. Thrombotic thrombocytopenic purpura in the setting of systemic sclerosis. Semin Arthritis Rheum 2005;34:683-8.
7. Tsai HM, Li A, Rock G. Inhibitors of von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura. Clin Lab 2001;47:387-92.
8. Mannucci PM, Vanoli M, Forza I, Canciani MT, Scorza R. Von Willebrand factor-cleaving protease (ADAMTS-13) in 123 patients with connective tissue diseases (systemic lupus erythematosus and systemic sclerosis). Haematologica 2003;88:914-8.