Effects of arginine treatment on nutrition, growth and urea cycle function in seven Japanese boys with late-onset ornithine transcarbamylase deficiency

European Journal of Pediatrics

Volumn 165, Issue 9, 2006, Pages 618-624

  Nagasaka, Hironori ^a   Yorifuji, Tohru ^b   Murayama, Kei ^a   Kubota, Mitsuru ^c   Kurokawa, Keiji ^b   Murakami, Tomoko ^a   Kanazawa, Masaki ^d   Takatani, Tomozumi ^a   Ogawa, Atsushi ^d   Ogawa, Emi ^d   Yamamoto, Shigenori ^d   Adachi, Masanori ^e   Kobayashi, Kunihiko ^c   Takayanagi, Masaki ^a  

^a CHIBA CHILDREN'S HOSPITAL   (Japan)

^b KYOTO UNIVERSITY   (Japan)

^c HOKKAIDO UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^d CHIBA UNIVERSITY   (Japan)

^e KANAGAWA CHILDREN'S MEDICAL CENTER   (Japan)

Author keywords

Arginine deficiency; Growth hormone; Nutrition and growth; Ornithine transcarbamylase deficiency; Orotate; Plasma glutamine and alanine

Indexed keywords

ALANINE; AMINO ACID; ARGININE; BIOLOGICAL MARKER; GLUTAMINE; GROWTH HORMONE; HIGH DENSITY LIPOPROTEIN CHOLESTEROL; LIPID; OROTIC ACID; PROTEIN; SOMATOMEDIN BINDING PROTEIN 3; SOMATOMEDIN C;

AMINO ACID BLOOD LEVEL; ARTICLE; BODY GROWTH; BODY HEIGHT; BODY WEIGHT; CHILD GROWTH; CHILD NUTRITION; CHOLESTEROL BLOOD LEVEL; CHRONOLOGY; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; DRUG EFFECT; GROWTH HORMONE BLOOD LEVEL; GROWTH HORMONE RELEASE; HUMAN; HYPERAMMONEMIA; LIPID BLOOD LEVEL; MALE; ONSET AGE; PATIENT MONITORING; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTEIN SYNTHESIS; TREATMENT OUTCOME; UNCONSCIOUSNESS; UREA CYCLE; URINARY EXCRETION; VOMITING; WEIGHT CHANGE;

AGE OF ONSET; AMINO ACIDS; AMMONIA; ANALYSIS OF VARIANCE; ARGININE; BIOLOGICAL MARKERS; BLOOD PROTEINS; BODY HEIGHT; BODY WEIGHT; CHILD, PRESCHOOL; CHOLESTEROL, HDL; CHOLESTEROL, LDL; DIET, PROTEIN-RESTRICTED; GROWTH; GROWTH HORMONE; HUMANS; HYPERAMMONEMIA; INSULIN-LIKE GROWTH FACTOR BINDING PROTEIN 3; INSULIN-LIKE GROWTH FACTOR I; JAPAN; MALE; NUTRITION PHYSIOLOGY; NUTRITIONAL PHYSIOLOGICAL PHENOMENA; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; OROTIC ACID; THYROTROPIN; TIME FACTORS; TREATMENT OUTCOME; TRIGLYCERIDES; UREA;

EID: 33746518542     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-006-0143-y     Document Type: Article

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