Auto-immune hemolytic anemia and dyserythropoïesis as the presenting signs of Fas-deficient condition in 3 children;Anémie hémolytique auto-immune et dysérythropoïèse révélatrices d'un déficit de l'apoptose Fas chez 3 enfants

Archives de Pediatrie

Volumn 13, Issue 4, 2006, Pages 367-370

  Guitton, C ^a   Ledeist, F ^b   Tchernia, G ^a   Bader Meunier, B ^a  

^a BICÊTRE HOSPITAL   (France)

^b HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

Anemia; Apoptosis; Autoimmune diseases; Child; genetics; hemolytic; Lymphoproliferative disorders; Mutation

Indexed keywords

FAS ANTIGEN; MONOCLONAL ANTIBODY; T LYMPHOCYTE RECEPTOR ALPHA CHAIN; T LYMPHOCYTE RECEPTOR BETA CHAIN;

APOPTOSIS; ARTICLE; AUTOIMMUNE DISEASE; AUTOIMMUNE HEMOLYTIC ANEMIA; CASE REPORT; CD4+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CELL MATURATION; CHILD; CLINICAL FEATURE; COOMBS TEST; DYSERYTHROPOIESIS; ERYTHROBLAST; GENE MUTATION; HEMOLYTIC ANEMIA; HETEROZYGOSITY; HUMAN; LYMPHOPROLIFERATIVE DISEASE; NEUTROPENIA; PROTEIN DEFICIENCY; THROMBOCYTOPENIA;

ANEMIA, DYSERYTHROPOIETIC, CONGENITAL; ANEMIA, HEMOLYTIC, AUTOIMMUNE; ANTIGENS, CD95; APOPTOSIS; CHILD, PRESCHOOL; HEPATOMEGALY; HUMANS; INFANT; MALE; MUTATION; SPLENOMEGALY;

EID: 33645889969     PISSN: 0929693X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.arcped.2006.01.012     Document Type: Article

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