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Volumn 65, Issue 12, 2005, Pages 1859-1860

Determinants of rapid disease progression in ALS

Author keywords

[No Author keywords available]

Indexed keywords

RNA; SUPEROXIDE DISMUTASE; COPPER ZINC SUPEROXIDE DISMUTASE;

EID: 33645751494     PISSN: 00283878     EISSN: None     Source Type: Journal    
DOI: 10.1212/01.wnl.0000192717.25980.b5     Document Type: Editorial
Times cited : (10)

References (12)
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  • 2
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    • Mutations in Cu/Zn Superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis
    • Rosen DR, Siddique T, Patterson D, et al. Mutations in Cu/Zn Superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis. Nature 1993;362:59-62.
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  • 4
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    • Aggregation and motor neuron toxicity of an ALS-linked SOD1 mutant independent from wild-type SOD1
    • Bruijn LI, Houseweart MK, Kato S, et al. Aggregation and motor neuron toxicity of an ALS-linked SOD1 mutant independent from wild-type SOD1. Science 1998;281:1851-1854.
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  • 5
    • 15844393658 scopus 로고    scopus 로고
    • Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury
    • Reaume AG, Elliott JL, Hoffman EK, et al. Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury. Nat Genet 1996;13:43-47.
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  • 6
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    • Rapid disease progression correlates with instability of mutant SOD1 in familial ALS
    • Sato T, Nakanishi T, Yamamoto Y, et al. Rapid disease progression correlates with instability of mutant SOD1 in familial ALS. Neurology 2005;65:1954-1957.
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    • Sato, T.1    Nakanishi, T.2    Yamamoto, Y.3
  • 7
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    • Silencing mutant SOD1 using RNAi protects against neurodegeneration and extends survival in an ALS model
    • Ralph GS, Radcliffe PA, Day DM, et al. Silencing mutant SOD1 using RNAi protects against neurodegeneration and extends survival in an ALS model. Nat Med 2005;11:429-433.
    • (2005) Nat Med , vol.11 , pp. 429-433
    • Ralph, G.S.1    Radcliffe, P.A.2    Day, D.M.3
  • 8
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    • Wild-type nonneuronal cells extend survival of SOD1 mutant motor neurons in ALS mice
    • Clement AM, Nguyen MD, Roberts EA, et al. Wild-type nonneuronal cells extend survival of SOD1 mutant motor neurons in ALS mice. Science 2003;302:113-117.
    • (2003) Science , vol.302 , pp. 113-117
    • Clement, A.M.1    Nguyen, M.D.2    Roberts, E.A.3
  • 9
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    • Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria
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    • Liu, J.1    Lillo, C.2    Jonsson, P.A.3
  • 10
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    • Amyotrophic lateral sclerosis-associated SOD1 mutant proteins bind and aggregate with Bcl-2 in spinal cord mitochondria
    • Pasinelli P, Belford ME, Lennon N, et al. Amyotrophic lateral sclerosis-associated SOD1 mutant proteins bind and aggregate with Bcl-2 in spinal cord mitochondria. Neuron 2004;43:19-30.
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    • Mutant superoxide dismutase 1 forms aggregates in the brain mitochondrial matrix of amyotrophic lateral sclerosis mice
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* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.