Pulmonary involvement by Niemann-Pick disease. A report of six cases

Histopathology

Volumn 48, Issue 5, 2006, Pages 596-603

  Nicholson, A G ^a   Florio, R ^a   Hansell, D M ^a   Du Bois, R M ^a   Wells, A U ^a   Hughes, P ^b   Ramadan, H K ^c   Mackinlay, C I ^c   Brambilla, E ^d   Ferretti, G R ^d   Erichsen, A ^e   Malone, M ^f   Lantuejoul, S ^d  

^a ROYAL BROMPTON HOSPITAL   (United Kingdom)

^b DERRIFORD HOSPITAL   (United Kingdom)

^c GREAT WESTERN HOSPITAL   (United Kingdom)

^d HÔPITAL MICHALLON   (France)

^e ULLEVÅL UNIVERSITY HOSPITAL   (Norway)

^f GREAT ORMOND STREET HOSPITAL   (United Kingdom)

Author keywords

Inborn error of metabolism; Lipid pneumonia; Lung; Niemann Pick disease

Indexed keywords

ACUTE RESPIRATORY FAILURE; ADULT; ADULTHOOD; ARTICLE; ASPIRATION PNEUMONIA; CELL VACUOLE; CLINICAL ARTICLE; CLINICAL FEATURE; COMPUTER ASSISTED TOMOGRAPHY; CORRELATION COEFFICIENT; DIAGNOSTIC IMAGING; DISEASE CLASSIFICATION; ELECTRON MICROSCOPY; FEMALE; HISTOLOGY; HUMAN; HUMAN TISSUE; INBORN ERROR OF METABOLISM; LAMELLAR BODY; LUNG BIOPSY; LUNG FIBROSIS; LUNG INTERSTITIUM; LUNG LAVAGE; LYSOSOME; MACROPHAGE; MALE; MORBIDITY; NIEMANN PICK DISEASE; PRIORITY JOURNAL;

EID: 33645395564     PISSN: 03090167     EISSN: 13652559     Source Type: Journal    
DOI: 10.1111/j.1365-2559.2006.02355.x     Document Type: Article

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