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Volumn 19, Issue 1, 2006, Pages 35-49

Clinical uses of plasma and plasma fractions: Plasma-derived products for hemophilias A and B, and for von Willebrand disease

Author keywords

Hemophilia treatment; Plasma derived factor products; Viral attenuation

Indexed keywords

ACTIVATED PROTHROMBIN COMPLEX; ALPHANATE SD; ALPHANINE SD; AUTOPLEX T; BEBULIN VH; BIOSTATE; BLOOD CLOTTING FACTOR; BLOOD CLOTTING FACTOR 10; BLOOD CLOTTING FACTOR 10A; BLOOD CLOTTING FACTOR 7; BLOOD CLOTTING FACTOR 7A; BLOOD CLOTTING FACTOR 8; BLOOD CLOTTING FACTOR 8 CONCENTRATE; BLOOD CLOTTING FACTOR 9; BLOOD CLOTTING FACTOR 9 COMPLEX; BLOOD CLOTTING FACTOR 9 CONCENTRATE; BLOOD CLOTTING FACTOR 9A; BLOOD CLOTTING FACTOR CONCENTRATE; DESMOPRESSIN ACETATE; FEIBA VH; FRESH FROZEN PLASMA; IMMUNOGLOBULIN; KOATE DVI; KONYNE 80; MONARC M; PROFILNINE SD; PROPLEX T; PROTHROMBIN; PROTHROMBIN A; PROTHROMBIN COMPLEX; RECOMBINANT BLOOD CLOTTING FACTOR 8; RECOMBINANT BLOOD CLOTTING FACTOR 9; VON WILLEBRAND FACTOR; WILFACTIN;

EID: 31044447908     PISSN: 15216926     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.beha.2005.01.031     Document Type: Review
Times cited : (16)

References (75)
  • 1
    • 0036236929 scopus 로고    scopus 로고
    • On the way to virus-safe blood coagulation factor concentrates
    • K. Schimpf On the way to virus-safe blood coagulation factor concentrates Semin Thromb Haemost 28 2002 15-24
    • (2002) Semin Thromb Haemost , vol.28 , pp. 15-24
    • Schimpf, K.1
  • 2
    • 0021715169 scopus 로고
    • Molecular cloning of a cDNA encoding human antihaemophilic factor
    • J.J. Toole J.L. Knopf J.M. Wozney L.A. Sultzman et al. Molecular cloning of a cDNA encoding human antihaemophilic factor Nature 312 1984 342-347
    • (1984) Nature , vol.312 , pp. 342-347
    • Toole, J.J.1    Knopf, J.L.2    Wozney, J.M.3    Sultzman, L.A.4
  • 3
    • 0019957533 scopus 로고
    • Molecular cloning of the gene for human anti-haemophilic factor IX
    • K.H. Choo K.G. Gould D.J. Rees & G.G. Brownlee Molecular cloning of the gene for human anti-haemophilic factor IX Nature 299 5879 1982 178-180
    • (1982) Nature , vol.299 , Issue.5879 , pp. 178-180
    • Choo, K.H.1    Gould, K.G.2    Rees, D.J.3    Brownlee, G.G.4
  • 5
    • 2542560221 scopus 로고    scopus 로고
    • The role of plasma-derived factor VIII/von Willebrand factor concentrates in the treatment of hemophilia A
    • G. Auerswald Th Spranger H.H. Brackmann & The role of plasma-derived factor VIII/von Willebrand factor concentrates in the treatment of hemophilia A Haematologica 88 2003 21-29
    • (2003) Haematologica , vol.88 , pp. 21-29
    • Auerswald, G.1    Spranger, Th.2    Brackmann, H.H.3
  • 6
    • 0028907225 scopus 로고
    • Comparison of the recovery and half-life of a high purity factor IX concentrate with those of a factor IX complex concentrate
    • Factor IX Study Group
    • M.C. Poon L.M. Aledort K. Anderle et al. Comparison of the recovery and half-life of a high purity factor IX concentrate with those of a factor IX complex concentrate. Factor IX Study Group Transfusion 35 1995 319-323
    • (1995) Transfusion , vol.35 , pp. 319-323
    • Poon, M.C.1    Aledort, L.M.2    Anderle, K.3
  • 7
    • 0000147766 scopus 로고    scopus 로고
    • Inhibitor development and substitution therapy in a developing country: Turkey
    • K. Kavakli A. Gringeri R. Bader et al. Inhibitor development and substitution therapy in a developing country: Turkey Haemophilia 4 1998 104-108
    • (1998) Haemophilia , vol.4 , pp. 104-108
    • Kavakli, K.1    Gringeri, A.2    Bader, R.3
  • 8
    • 0035132443 scopus 로고    scopus 로고
    • Choice of factor concentrates for haemophilia: A developing world perspective
    • A. Srivastava Choice of factor concentrates for haemophilia: A developing world perspective Haemophilia 7 2001 117-122
    • (2001) Haemophilia , vol.7 , pp. 117-122
    • Srivastava, A.1
  • 9
    • 0006262868 scopus 로고    scopus 로고
    • Hemophilia A and B
    • J. Lilleyman I. Hann & V. Blanchette (eds) 2nd edn Churchill Livingstone London, UK
    • J.M. Lusher Hemophilia A and B in: J. Lilleyman I. Hann & V. Blanchette (eds) Pedeatric Hematology 2nd edn 1999 Churchill Livingstone London, UK 585-600
    • (1999) Pedeatric Hematology , pp. 585-600
    • Lusher, J.M.1
  • 10
    • 31044443132 scopus 로고
    • The use of continuous infusion of factor concentrates in the treatment of hemophilia
    • R.D. Bona R.A. Weinstein S.T. Weisman et al. The use of continuous infusion of factor concentrates in the treatment of hemophilia Am J Hematol 1990
    • (1990) Am J Hematol
    • Bona, R.D.1    Weinstein, R.A.2    Weisman, S.T.3
  • 11
    • 84992419704 scopus 로고
    • Successful transfusion of blood
    • S. Lane Successful transfusion of blood Lancet 1 1840 185-188
    • (1840) Lancet , vol.1 , pp. 185-188
    • Lane, S.1
  • 12
    • 0000553473 scopus 로고
    • High-potency antihaemophilic factor concentrate prepared from cryoglobulin precipitate
    • J.G. Pool E.J. Gershgold & A.R. Pappenhagen High-potency antihaemophilic factor concentrate prepared from cryoglobulin precipitate Nature 18 203 1964 312
    • (1964) Nature , vol.18 , Issue.203 , pp. 312
    • Pool, J.G.1    Gershgold, E.J.2    Pappenhagen, A.R.3
  • 13
    • 0025872965 scopus 로고
    • The need for recombinant factor VIII: Historical background and rationale
    • M.W. Hilgartner The need for recombinant factor VIII: Historical background and rationale Semin Hematol 28 supplement 1 1991 6-9
    • (1991) Semin Hematol , vol.28 , Issue.SUPPL. 1 , pp. 6-9
    • Hilgartner, M.W.1
  • 14
    • 0034968360 scopus 로고    scopus 로고
    • History of plasma-product safety
    • W.K. Hoots History of plasma-product safety Transfus Med Rev 15 2001 3-10
    • (2001) Transfus Med Rev , vol.15 , pp. 3-10
    • Hoots, W.K.1
  • 15
    • 0027273396 scopus 로고
    • Recent evolution of clotting factor concentrates for hemophilia A and B
    • Transfusion Practices Committee
    • C.K. Kasper & J.M. Lusher Recent evolution of clotting factor concentrates for hemophilia A and B. Transfusion Practices Committee Transfusion 33 1993 422-434
    • (1993) Transfusion , vol.33 , pp. 422-434
    • Kasper, C.K.1    Lusher, J.M.2
  • 16
    • 0036588697 scopus 로고    scopus 로고
    • Evolving perspectives in product safety for haemophilia
    • A. Farrugia Evolving perspectives in product safety for haemophilia Haemophilia 8 2002 236-243
    • (2002) Haemophilia , vol.8 , pp. 236-243
    • Farrugia, A.1
  • 17
    • 31044456760 scopus 로고    scopus 로고
    • Accredo Health Inc. Announces Record Results; Third Quarter Earnings Increase 75%. Accessed 5-2-2004 at
    • Accredo Health Inc. Announces Record Results; Third Quarter Earnings Increase 75%. Accessed 5-2-2004 at http://www.accredohealth.net/ahi/news/ pr010430.html
  • 18
    • 31044432172 scopus 로고    scopus 로고
    • World Federation of Hemophilia Information Update
    • Factor VIII Product Shortage. Accessed on 4-2-04. at
    • Factor VIII Product Shortage. World Federation of Hemophilia Information Update. 2001. Accessed on 4-2-04. at http://www.wfh.org/ Content_Documents/Newsletters/IU_April01_Eng.pdf
    • (2001)
  • 19
    • 0035084947 scopus 로고    scopus 로고
    • Risk factors for infection with HBV and HCV in a large cohort of hemophiliac males
    • J.M. Soucie L.C. Richardson B.E. Evatt et al. Risk factors for infection with HBV and HCV in a large cohort of hemophiliac males Transfusion 41 2001 338-343
    • (2001) Transfusion , vol.41 , pp. 338-343
    • Soucie, J.M.1    Richardson, L.C.2    Evatt, B.E.3
  • 20
    • 0035098164 scopus 로고    scopus 로고
    • Effects of HIV infection on age and cause of death for persons with hemophilia A in the United States
    • T.L. Chorba R.C. Holman M.J. Clarke et al. Effects of HIV infection on age and cause of death for persons with hemophilia A in the United States Am J Hematol 66 2001 229-240
    • (2001) Am J Hematol , vol.66 , pp. 229-240
    • Chorba, T.L.1    Holman, R.C.2    Clarke, M.J.3
  • 21
    • 0026795618 scopus 로고
    • Human immunodeficiency virus infection due to clotting factor concentrates: Results of the Seroconversion Surveillance Project
    • W. Fricke L. Augustyniak D. Lawrence A. Brownstein et al. Human immunodeficiency virus infection due to clotting factor concentrates: results of the Seroconversion Surveillance Project Transfusion 32 1992 707-709
    • (1992) Transfusion , vol.32 , pp. 707-709
    • Fricke, W.1    Augustyniak, L.2    Lawrence, D.3    Brownstein, A.4
  • 22
    • 31044445889 scopus 로고    scopus 로고
    • Human parvovirus B19 is inactivated by pasteurization, a dedicated virus reduction step in the manufacturing procedure of plasma derivatives
    • [abstract]
    • A. Groener S. Mehdi W. Schafer & M. Spyra Human parvovirus B19 is inactivated by pasteurization, a dedicated virus reduction step in the manufacturing procedure of plasma derivatives [abstract] Blood 102 2003 4241
    • (2003) Blood , vol.102 , pp. 4241
    • Groener, A.1    Mehdi, S.2    Schafer, W.3    Spyra, M.4
  • 23
    • 0141785315 scopus 로고    scopus 로고
    • Treatment of hemophilia: Recombinant factor only? No
    • P.M. Mannucci Treatment of hemophilia: Recombinant factor only? No J Thromb Haemost 1 2003 216-217
    • (2003) J Thromb Haemost , vol.1 , pp. 216-217
    • Mannucci, P.M.1
  • 24
    • 0026548917 scopus 로고
    • Incidence of factor VIII and factor IX inhibitors in hemophiliacs
    • S. Ehrenforth W. Kreuz I. Scharrer et al. Incidence of factor VIII and factor IX inhibitors in hemophiliacs Lancet 339 1992 594-598
    • (1992) Lancet , vol.339 , pp. 594-598
    • Ehrenforth, S.1    Kreuz, W.2    Scharrer, I.3
  • 25
    • 9144271882 scopus 로고    scopus 로고
    • Is the incidence and prevalence of inhibitors great with recombinant products? No
    • J.M. Lusher Is the incidence and prevalence of inhibitors great with recombinant products? No J Thromb Heamost 2 2004 863-865
    • (2004) J Thromb Heamost , vol.2 , pp. 863-865
    • Lusher, J.M.1
  • 26
    • 9144233748 scopus 로고    scopus 로고
    • Is the incidence and prevalence of inhibitors greater with recombinant products? Yes
    • L.M. Aledort Is the incidence and prevalence of inhibitors greater with recombinant products? Yes J Thromb Heaemost 2 2004 861-862
    • (2004) J Thromb Heaemost , vol.2 , pp. 861-862
    • Aledort, L.M.1
  • 27
    • 0034913420 scopus 로고    scopus 로고
    • Influence of von Willebrand factor on the reactivity of human factor VIII inhibitors
    • M. Gensana C. Altiesent J.A. Aznar et al. Influence of von Willebrand factor on the reactivity of human factor VIII inhibitors Haemophilia 7 2001 369-374
    • (2001) Haemophilia , vol.7 , pp. 369-374
    • Gensana, M.1    Altiesent, C.2    Aznar, J.A.3
  • 28
    • 0036332175 scopus 로고    scopus 로고
    • Von Willebrand factor modulates factor VIII immunogenicity: Comparative study of different factor VIII concentrates in a hemophilia A mouse model
    • M. Behrmann J. Pasi J.M.R. Saint-Remy et al. Von Willebrand factor modulates factor VIII immunogenicity: Comparative study of different factor VIII concentrates in a hemophilia A mouse model Thromb Haemost 88 2002 221-229
    • (2002) Thromb Haemost , vol.88 , pp. 221-229
    • Behrmann, M.1    Pasi, J.2    Saint-Remy, J.M.R.3
  • 29
    • 0022600698 scopus 로고
    • Structure, function, and molecular defects of factor IX
    • A.R. Thompson Structure, function, and molecular defects of factor IX Blood 67 1986 565-672
    • (1986) Blood , vol.67 , pp. 565-672
    • Thompson, A.R.1
  • 30
    • 0013866962 scopus 로고
    • The potent antihemophilic globulin concentrate derived from a cold insoluble fraction of human plasma: Characterization and further data on preparation and clinical trial
    • E.J. Hershgold J.G. Pool A.R. Pappenhagen & The potent antihemophilic globulin concentrate derived from a cold insoluble fraction of human plasma: Characterization and further data on preparation and clinical trial J Lab Clin Med 67 1966 23-32
    • (1966) J Lab Clin Med , vol.67 , pp. 23-32
    • Hershgold, E.J.1    Pool, J.G.2    Pappenhagen, A.R.3
  • 31
    • 0025862345 scopus 로고
    • Introduction and overview of treatment
    • L.M. Aldort Introduction and overview of treatment Semin Hematol 28 1991 1-2
    • (1991) Semin Hematol , vol.28 , pp. 1-2
    • Aldort, L.M.1
  • 32
    • 0025871335 scopus 로고
    • Thrombogenicity associated with factor IX complex concentrates
    • J.M. Lusher Thrombogenicity associated with factor IX complex concentrates Semin Hematol 28 1991 3-5
    • (1991) Semin Hematol , vol.28 , pp. 3-5
    • Lusher, J.M.1
  • 33
    • 0018097008 scopus 로고
    • Therapy with factor IX concentrate resulting in DIC and thromboembolic phenomena
    • E.W. Campbell S. Neff & A.J. Bowdler Therapy with factor IX concentrate resulting in DIC and thromboembolic phenomena Transfusion 18 1978 94-97
    • (1978) Transfusion , vol.18 , pp. 94-97
    • Campbell, E.W.1    Neff, S.2    Bowdler, A.J.3
  • 34
    • 0015930069 scopus 로고
    • Postoperative thromboses in hemophilia B
    • (letter)
    • C.K. Kasper Postoperative thromboses in hemophilia B (letter) N Eng J Med 289 1973 160
    • (1973) N Eng J Med , vol.289 , pp. 160
    • Kasper, C.K.1
  • 35
    • 0016377858 scopus 로고
    • Thrombogenic materials in prothrombin complex concentrates
    • P.M. Blatt R.L. Lundblad H.S. Kingdon et al. Thrombogenic materials in prothrombin complex concentrates Ann Intern Med 81 1974 766-770
    • (1974) Ann Intern Med , vol.81 , pp. 766-770
    • Blatt, P.M.1    Lundblad, R.L.2    Kingdon, H.S.3
  • 36
    • 0021687466 scopus 로고
    • Coagulation factor IX concentrate: Method of preparation and assessment of potential in vivo thrombogenicity in animal models
    • D. Menache H.E. Behre C.L. Orthner et al. Coagulation factor IX concentrate: Method of preparation and assessment of potential in vivo thrombogenicity in animal models Blood 64 1984 1220-1227
    • (1984) Blood , vol.64 , pp. 1220-1227
    • Menache, D.1    Behre, H.E.2    Orthner, C.L.3
  • 37
  • 38
    • 0025597851 scopus 로고
    • Thrombin generation is not increased in the blood of hemophilia B patients aft the infusion of a purified factor IX concentrate
    • P.M. Mannucci K.A. Bauer A. Gringeri et al. Thrombin generation is not increased in the blood of hemophilia B patients aft the infusion of a purified factor IX concentrate Blood 76 1990 2540-2545
    • (1990) Blood , vol.76 , pp. 2540-2545
    • Mannucci, P.M.1    Bauer, K.A.2    Gringeri, A.3
  • 39
    • 0027411861 scopus 로고
    • Factor IX concentrates for clinical use
    • A.R. Thompson Factor IX concentrates for clinical use Semin Thromb Hemost 19 1993 25-36
    • (1993) Semin Thromb Hemost , vol.19 , pp. 25-36
    • Thompson, A.R.1
  • 40
    • 0027379909 scopus 로고
    • Biochemical and in vivo properties of high purity factor IX concentrates
    • E. Berntorp S. Bjorkman M. Carlsson et al. Biochemical and in vivo properties of high purity factor IX concentrates Thromb Haemost 70 1993 768-773
    • (1993) Thromb Haemost , vol.70 , pp. 768-773
    • Berntorp, E.1    Bjorkman, S.2    Carlsson, M.3
  • 41
    • 31044441933 scopus 로고    scopus 로고
    • Recombinant FIX (rFIX) in the treatment of previously untreated patients with severe or moderately severe hemophilia B
    • Presented at XXIII International Congress of the World Federation of Haemophilia, The Hague, The Netherlands
    • Abshire T, Shapiro A, Gill J et al. Recombinant FIX (rFIX) in the treatment of previously untreated patients with severe or moderately severe hemophilia B. Presented at XXIII International Congress of the World Federation of Haemophilia, The Hague, The Netherlands; 1998.
    • (1998)
    • Abshire, T.1    Shapiro, A.2    Gill, J.3
  • 42
    • 0032756734 scopus 로고    scopus 로고
    • The epidemiology of virus transmission by plasma derivatives: Clinical studies verifying the lack of transmission of hepatitis B and C viruses and HIV type 1
    • E. Tabor The epidemiology of virus transmission by plasma derivatives: clinical studies verifying the lack of transmission of hepatitis B and C viruses and HIV type 1 Transfusion 39 1999 1160-1168
    • (1999) Transfusion , vol.39 , pp. 1160-1168
    • Tabor, E.1
  • 43
    • 0026543642 scopus 로고
    • Solvent/detergent treated plasma: A virus substitute for fresh frozen plasma
    • H.K. Future B. Horowitz R. Bonomo et al. Solvent/detergent treated plasma: A virus substitute for fresh frozen plasma Blood 79 1992 826-831
    • (1992) Blood , vol.79 , pp. 826-831
    • Future, H.K.1    Horowitz, B.2    Bonomo, R.3
  • 44
    • 0025180213 scopus 로고
    • Efficacy and safety of vapor-heated anti-inhibitor complex in hemophilia patients
    • FEIBA Study Group
    • M. Hilgartner L. Aledort A. Andes & J. Gill Efficacy and safety of vapor-heated anti-inhibitor complex in hemophilia patients. FEIBA Study Group Transfusion 30 1990 626-630
    • (1990) Transfusion , vol.30 , pp. 626-630
    • Hilgartner, M.1    Aledort, L.2    Andes, A.3    Gill, J.4
  • 45
    • 0029658954 scopus 로고    scopus 로고
    • Safety and efficacy of monoclonal antibody purified factor IX concentrate in previously untreated patients with hemophilia B
    • A.D. Shapiro M.V. Ragni J.M. Lusher et al. Safety and efficacy of monoclonal antibody purified factor IX concentrate in previously untreated patients with hemophilia B Thromb Haemost 75 1996 30
    • (1996) Thromb Haemost , vol.75 , pp. 30
    • Shapiro, A.D.1    Ragni, M.V.2    Lusher, J.M.3
  • 46
    • 0017659458 scopus 로고
    • Factor IX level in patients with hemophilia B (Christmas disease) following transfusion with concentrates of factor IX fresh frozen plasma
    • N.P. Zauber J. Levin et al. Factor IX level in patients with hemophilia B (Christmas disease) following transfusion with concentrates of factor IX fresh frozen plasma Medicine 56 1977 213-224
    • (1977) Medicine , vol.56 , pp. 213-224
    • Zauber, N.P.1    Levin, J.2
  • 47
    • 0027379909 scopus 로고
    • Biochemical and in vivo properties of high purity factor IX concentrates
    • E. Berntorp S. Bjorkman M. Carrlson et al. Biochemical and in vivo properties of high purity factor IX concentrates Thromb Haemost 70 1993 768-773
    • (1993) Thromb Haemost , vol.70 , pp. 768-773
    • Berntorp, E.1    Bjorkman, S.2    Carrlson, M.3
  • 48
    • 0028907225 scopus 로고
    • Comparison of the recovery and half-life of a high purity factor IX concentrate with those of a factor IX complex concentrate
    • Factor IX Study Group
    • M.C. Poon L.M. Aledort K. Anderle et al. Comparison of the recovery and half-life of a high purity factor IX concentrate with those of a factor IX complex concentrate. Factor IX Study Group Transfusion 35 1995 319-323
    • (1995) Transfusion , vol.35 , pp. 319-323
    • Poon, M.C.1    Aledort, L.M.2    Anderle, K.3
  • 49
    • 0026747195 scopus 로고
    • Coagulation factor IX. Successful surgical experience with purified factor IX concentrate
    • J.C. Goldsmith C.K. Kasper P.M. Blatt et al. Coagulation factor IX. Successful surgical experience with purified factor IX concentrate Am J Hematol 40 1992 210-215
    • (1992) Am J Hematol , vol.40 , pp. 210-215
    • Goldsmith, J.C.1    Kasper, C.K.2    Blatt, P.M.3
  • 50
    • 0035119994 scopus 로고    scopus 로고
    • The future of plasma-derived clotting factor concentrates
    • W.K. Hoots The future of plasma-derived clotting factor concentrates Haemophilia 7 2001 4-9
    • (2001) Haemophilia , vol.7 , pp. 4-9
    • Hoots, W.K.1
  • 51
    • 0038779279 scopus 로고    scopus 로고
    • Prophylaxis in factor IX deficiency product and patient variation
    • & Study Mononine Group
    • C.T. Kisker A. Eisberg & B. Schwartz Mononine Study Group Prophylaxis in factor IX deficiency product and patient variation Haemophilia 9 2003 279-284
    • (2003) Haemophilia , vol.9 , pp. 279-284
    • Kisker, C.T.1    Eisberg, A.2    Schwartz, B.3
  • 53
    • 28744448726 scopus 로고    scopus 로고
    • Recombinant versus plasma-derived factor IX in the treatment of hemophilia B: Proceedings of a meeting held in June 2003
    • P. Mathew & C. Altisent Recombinant versus plasma-derived factor IX in the treatment of hemophilia B: Proceedings of a meeting held in June 2003 Blood Coagul Fibrin 15 2004 S1-S3
    • (2004) Blood Coagul Fibrin , vol.15
    • Mathew, P.1    Altisent, C.2
  • 54
    • 0023164845 scopus 로고
    • Epidemiological investigation of the prevalence of von Willebrand disease
    • F. Rodeghiero G. Castaman & E. Dini Epidemiological investigation of the prevalence of von Willebrand disease Blood 69 1987 454-459
    • (1987) Blood , vol.69 , pp. 454-459
    • Rodeghiero, F.1    Castaman, G.2    Dini, E.3
  • 55
    • 0027458101 scopus 로고
    • Prevalence of von Willebrand disease in children: A multi-ethnic study
    • E.J. Werner E.H. Boxson E.L. Tucker et al. Prevalence of von Willebrand disease in children: A multi-ethnic study J Pediatr 123 1993 893-898
    • (1993) J Pediatr , vol.123 , pp. 893-898
    • Werner, E.J.1    Boxson, E.H.2    Tucker, E.L.3
  • 57
    • 0017754787 scopus 로고
    • Stabilization of factor VIII in plasma by the von Willebrand factor: Studies on posttransfusion and dissociated factor VIII and in patients with von Willebrand's Disease
    • H.J. Weiss I.I. Sussman & L.W. Hoyer Stabilization of factor VIII in plasma by the von Willebrand factor: Studies on posttransfusion and dissociated factor VIII and in patients with von Willebrand's Disease J Clin Invest 60 1977 390-404
    • (1977) J Clin Invest , vol.60 , pp. 390-404
    • Weiss, H.J.1    Sussman, I.I.2    Hoyer, L.W.3
  • 58
    • 3943048700 scopus 로고    scopus 로고
    • Treatment of von Willebrand's Disease
    • Manuucci PM. Treatment of von Willebrand's Disease. N Engl J Med 351;7:683-94.
    • N Engl J Med , vol.351 , Issue.7 , pp. 683-694
    • Manuucci, P.M.1
  • 59
    • 0028201807 scopus 로고
    • A revised classification of von Willebrand disease
    • J.E. Sadler A revised classification of von Willebrand disease Thromb Haemost 71 1994 520-525
    • (1994) Thromb Haemost , vol.71 , pp. 520-525
    • Sadler, J.E.1
  • 61
    • 0014123936 scopus 로고
    • Correction of the hemostatic defects in von Willebrand's Disease
    • H.A. Perkins Correction of the hemostatic defects in von Willebrand's Disease Blood 30 1967 375-380
    • (1967) Blood , vol.30 , pp. 375-380
    • Perkins, H.A.1
  • 62
    • 10744230522 scopus 로고    scopus 로고
    • Successful treatment of urgent bleeding in von Willebrand disease with FVIII/VWF concentrate (Humate-P): Use of ristocetin factor assay (VWF:RCo) to measure potency and to guide therapy
    • C.J. Gill B.M. Ewenstein A.R. Thompson et al. Successful treatment of urgent bleeding in von Willebrand disease with FVIII/VWF concentrate (Humate-P): Use of ristocetin factor assay (VWF:RCo) to measure potency and to guide therapy Haemophilia 9 2003 688-695
    • (2003) Haemophilia , vol.9 , pp. 688-695
    • Gill, C.J.1    Ewenstein, B.M.2    Thompson, A.R.3
  • 63
    • 10744220312 scopus 로고    scopus 로고
    • Successful treatment for patients with von Willebrand disease undergoing urgent surgery using factor VIII/VWF concentrate (Humate-P)
    • A.R. Thompson J.C. Gill B.M. Ewenstein et al. Successful treatment for patients with von Willebrand disease undergoing urgent surgery using factor VIII/VWF concentrate (Humate-P) Haemophilia 10 2004 42-51
    • (2004) Haemophilia , vol.10 , pp. 42-51
    • Thompson, A.R.1    Gill, J.C.2    Ewenstein, B.M.3
  • 64
    • 0037079717 scopus 로고    scopus 로고
    • Treatment of von Willebrand disease with a high-purity factor VIII/von Willebrand factor concentrate: A prospective, multicenter study
    • P.M. Mannucci j. Chediak W. Hanna et al. Treatment of von Willebrand disease with a high-purity factor VIII/von Willebrand factor concentrate: A prospective, multicenter study Blood 99 2002 450-456
    • (2002) Blood , vol.99 , pp. 450-456
    • Mannucci, P.M.1    Chediak, J.2    Hanna, W.3
  • 66
    • 0024357699 scopus 로고
    • Absence of anti-human immunodeficiency virus type I and 2 seroconversion after the treatment of hemophilia and von Willebrand disease with pasteurized factor VIII concentrate
    • K. Schimpf H.H. Brackmann W. Kreuz et al. Absence of anti-human immunodeficiency virus type I and 2 seroconversion after the treatment of hemophilia and von Willebrand disease with pasteurized factor VIII concentrate N Engl J Med 26 321 1989 1148-1152
    • (1989) N Engl J Med , vol.26 , Issue.321 , pp. 1148-1152
    • Schimpf, K.1    Brackmann, H.H.2    Kreuz, W.3
  • 67
    • 0024353189 scopus 로고
    • In vitro and in vivo characterization of a high-purity solvent/ detergent-treated factor VIII concentrate: Evidence for its therapeutic efficacy in von Willebrand disease
    • C. Mazurier C. De Romeuf A. Parquet-Gernez & M. Goudemand In vitro and in vivo characterization of a high-purity solvent/detergent-treated factor VIII concentrate: Evidence for its therapeutic efficacy in von Willebrand disease Eur J Haematol 43 1989 7-14
    • (1989) Eur J Haematol , vol.43 , pp. 7-14
    • Mazurier, C.1    De Romeuf, C.2    Parquet-Gernez, A.3    Goudemand, M.4
  • 68
    • 0030736701 scopus 로고    scopus 로고
    • In vivo characterization of recombinant von Willebrand factor in dogs with von Willebrand disease
    • P. Turecek H. Gritsch L. Pichler et al. In vivo characterization of recombinant von Willebrand factor in dogs with von Willebrand disease Blood 90 1997 3555-3567
    • (1997) Blood , vol.90 , pp. 3555-3567
    • Turecek, P.1    Gritsch, H.2    Pichler, L.3
  • 69
    • 0023157798 scopus 로고
    • Absence of hepatitis after treatment with a pasteurized factor VIII concentrate in patients with hemophilia and no previous transfusions
    • K. Schimpf P.M. Mannucci W. Kreutz et al. Absence of hepatitis after treatment with a pasteurized factor VIII concentrate in patients with hemophilia and no previous transfusions N Eng J Med 316 1987 918-922
    • (1987) N Eng J Med , vol.316 , pp. 918-922
    • Schimpf, K.1    Mannucci, P.M.2    Kreutz, W.3
  • 70
    • 0037079717 scopus 로고    scopus 로고
    • Treatment of von Willebrand disease with a high-purity factor VIII/von Willebrand factor concentrate: A prospective, multicenter study
    • P.M. Mannucci J. Chediak W. Hanna et al. Treatment of von Willebrand disease with a high-purity factor VIII/von Willebrand factor concentrate: A prospective, multicenter study Blood 99 2002 450-456
    • (2002) Blood , vol.99 , pp. 450-456
    • Mannucci, P.M.1    Chediak, J.2    Hanna, W.3
  • 71
    • 0028010958 scopus 로고
    • The use of intermediate and high purity factor VIII products in the treatment of von Willebrand disease
    • W.T. Hanna R.D. Bona C.E. Zimmerman et al. The use of intermediate and high purity factor VIII products in the treatment of von Willebrand disease Thromb Haemost 71 1994 173-179
    • (1994) Thromb Haemost , vol.71 , pp. 173-179
    • Hanna, W.T.1    Bona, R.D.2    Zimmerman, C.E.3
  • 72
    • 0036120805 scopus 로고    scopus 로고
    • A comparative mulit-laboratory assessment of three factor VIII/von Willebrand factor concentrates
    • E.J. Favaloro M. Bukuva T. Martinelli et al. A comparative mulit-laboratory assessment of three factor VIII/von Willebrand factor concentrates Thromb Haemost 87 2002 466-476
    • (2002) Thromb Haemost , vol.87 , pp. 466-476
    • Favaloro, E.J.1    Bukuva, M.2    Martinelli, T.3
  • 73
    • 0026567524 scopus 로고
    • Clinical and biological evaluation in von Willebrand's disease of a von Willebrand factor concentrate wit low factor VIII activity
    • J. Goudemand C. Mazurier A. Marey et al. Clinical and biological evaluation in von Willebrand's disease of a von Willebrand factor concentrate wit low factor VIII activity Br J Haematol 80 1992 21-221
    • (1992) Br J Haematol , vol.80 , pp. 21-221
    • Goudemand, J.1    Mazurier, C.2    Marey, A.3
  • 74
    • 0031774616 scopus 로고    scopus 로고
    • Clinical management of patients with von Willebrand's disease with VHP VWF concentrate: The French experience
    • J. Goudemand C. Negrier N. Onnoughene & Y. Sultan Clinical management of patients with von Willebrand's disease with VHP VWF concentrate: The French experience Haemophilia 4 1998 48-52
    • (1998) Haemophilia , vol.4 , pp. 48-52
    • Goudemand, J.1    Negrier, C.2    Onnoughene, N.3    Sultan, Y.4
  • 75
    • 31044443656 scopus 로고    scopus 로고
    • Aventis Behring. Humate-P package insert; July
    • Aventis Behring. Humate-P package insert; July, 2000.
    • (2000)


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