메뉴 건너뛰기




Volumn 122, Issue 18, 2004, Pages 698-700

Patients with cystic fibrosis attending at the cystic fibrosis units of Madrid: Cross-sectional study of 387 subjects;Pacientes con fibrosis quística atendidos en las unidades de fibrosis quística de la Comunidad de Madrid: Estudio transversal de 387 casos

Author keywords

Cystic fibrosis; Diabetes mellitus; Lung function; Pancreatic insufficiency; Pseudomonas aeruginosa

Indexed keywords

ADOLESCENT; ADULT; AGED; ANTHROPOMETRY; ARTICLE; BACTERIAL COLONIZATION; BODY MASS; CHILD; CHROMOSOME ANALYSIS; CLINICAL FEATURE; CONTROLLED STUDY; CYSTIC FIBROSIS; DEMOGRAPHY; DIABETES MELLITUS; FEMALE; GENE MUTATION; GENETIC ANALYSIS; HEALTH CARE FACILITY; HOMOZYGOSITY; HUMAN; INFANT; LUNG FUNCTION; MAJOR CLINICAL STUDY; MALE; NUTRITIONAL STATUS; PANCREAS INSUFFICIENCY; PREVALENCE; PSEUDOMONAS AERUGINOSA; REGISTER; SCORING SYSTEM; SPAIN;

EID: 2942538026     PISSN: 00257753     EISSN: None     Source Type: Journal    
DOI: 10.1157/13062169     Document Type: Article
Times cited : (4)

References (22)
  • 2
    • 0024424270 scopus 로고
    • Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
    • Riordan JR, Rommens JM, Kerem B, Alon N, Rozmahel G, Grzelczak Z, et al. Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. Science 1989;245:1066-73.
    • (1989) Science , vol.245 , pp. 1066-1073
    • Riordan, J.R.1    Rommens, J.M.2    Kerem, B.3    Alon, N.4    Rozmahel, G.5    Grzelczak, Z.6
  • 3
    • 0037460729 scopus 로고    scopus 로고
    • Cystic fibrosis
    • Ratjen F, Döring G. Cystic fibrosis. Lancet 2003;361:681-9.
    • (2003) Lancet , vol.361 , pp. 681-689
    • Ratjen, F.1    Döring, G.2
  • 4
    • 0038207591 scopus 로고
    • Standarized lung function testing
    • Quanjer PH. Standarized lung function testing. Eur Respir J 1993;6(Suppl 6):3-102.
    • (1993) Eur Respir J , vol.6 , Issue.SUPPL. 6 , pp. 3-102
    • Quanjer, P.H.1
  • 7
    • 0028299622 scopus 로고
    • Analysis of the CFTR gene confirms the high genetic heterogeneity of the Spanish population: 43 Mutations account for only 78% of CF chromosomes
    • Chillón M, Casals T, Giménez J, Ramos MD, Palacio A, Morral N, et al. Analysis of the CFTR gene confirms the high genetic heterogeneity of the Spanish population: 43 mutations account for only 78% of CF chromosomes. Hum Genet 1994;93:447-51.
    • (1994) Hum Genet , vol.93 , pp. 447-451
    • Chillón, M.1    Casals, T.2    Giménez, J.3    Ramos, M.D.4    Palacio, A.5    Morral, N.6
  • 9
    • 0028033069 scopus 로고
    • Populations variation of common cystic fibrosis mutations
    • Cystic Fibrosis Genetic Analysis Consortium. Populations variation of common cystic fibrosis mutations. Hum Mutat 1994;4:167-77.
    • (1994) Hum Mutat , vol.4 , pp. 167-177
  • 10
    • 0038663174 scopus 로고    scopus 로고
    • Effect of genotype on phenotype and mortality in cystic fibrosis: A retrospective cohort study
    • McKone EF, Emerson SS, Edwards KL, Aitken ML. Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study. Lancet 2003;361:1671-6.
    • (2003) Lancet , vol.361 , pp. 1671-1676
    • McKone, E.F.1    Emerson, S.S.2    Edwards, K.L.3    Aitken, M.L.4
  • 12
    • 0034785481 scopus 로고    scopus 로고
    • Acceleration of lung disease in children with cystic fibrosis after Pseudomonas aeruginosa acquisition
    • Kosorok MR, Zeng L, West SE, Rock MJ, Splaingard ML, Laxova A, et al. Acceleration of lung disease in children with cystic fibrosis after Pseudomonas aeruginosa acquisition. Pediatr Pulmonol 2001;32:277-87.
    • (2001) Pediatr Pulmonol , vol.32 , pp. 277-287
    • Kosorok, M.R.1    Zeng, L.2    West, S.E.3    Rock, M.J.4    Splaingard, M.L.5    Laxova, A.6
  • 13
    • 12244306198 scopus 로고    scopus 로고
    • Risk factors for initial acquisition of Pseudomonas aeruginosa in children with cystic fibrosis identified by newborn screening
    • Maselli JH, Sontang MK, Norris JM, MacKenzie T, Wagener JS, Accurso FJ. Risk factors for initial acquisition of Pseudomonas aeruginosa in children with cystic fibrosis identified by newborn screening. Pediatr Pulmonol 2003;35:257-62.
    • (2003) Pediatr Pulmonol , vol.35 , pp. 257-262
    • Maselli, J.H.1    Sontang, M.K.2    Norris, J.M.3    MacKenzie, T.4    Wagener, J.S.5    Accurso, F.J.6
  • 14
    • 0032135143 scopus 로고    scopus 로고
    • Overproduction of the CFTR R domain leads to increased levels of asialoGM1 and increased Pseudomonas aeruginosa binding by epithelial cells
    • Bryan R, Kube D, Pérez A, Davis P, Prince A. Overproduction of the CFTR R domain leads to increased levels of asialoGM1 and increased Pseudomonas aeruginosa binding by epithelial cells. Am J Respir Cel Mol Biol 1998;19:269-77.
    • (1998) Am J Respir Cel Mol Biol , vol.19 , pp. 269-277
    • Bryan, R.1    Kube, D.2    Pérez, A.3    Davis, P.4    Prince, A.5
  • 15
    • 0028847778 scopus 로고
    • Binding of Pseudomonas aeruginosa to respiratory epithelial cells from patients with various mutations in the cystic fibrosis transmembrane regulator
    • Zar H, Saiman L, Quittell L, Prince A. Binding of Pseudomonas aeruginosa to respiratory epithelial cells from patients with various mutations in the cystic fibrosis transmembrane regulator. J Pediatr 1995;126:230-3.
    • (1995) J Pediatr , vol.126 , pp. 230-233
    • Zar, H.1    Saiman, L.2    Quittell, L.3    Prince, A.4
  • 16
    • 0033827478 scopus 로고    scopus 로고
    • Longitudinal relationship among growth, nutritional status and pulmonary function in children with cystic fibrosis: Analysis of the Cystic Fibrosis Foundation National CF Patient Registry
    • Zemel BS, Jawad AF, FitzSimmons S, Stallings VA. Longitudinal relationship among growth, nutritional status and pulmonary function in children with cystic fibrosis: analysis of the Cystic Fibrosis Foundation National CF Patient Registry. J Pediatr 2000;137:374-80.
    • (2000) J Pediatr , vol.137 , pp. 374-380
    • Zemel, B.S.1    Jawad, A.F.2    FitzSimmons, S.3    Stallings, V.A.4
  • 17
    • 0036311232 scopus 로고    scopus 로고
    • Relationship between nutritional status and lung function in cystic fibrosis: Cross sectional and longitudinal analysis from the German CF quality assurance (CFQA) project
    • Steinkamp G, Wiedemann B, and behalf of the German CFQA Group. Relationship between nutritional status and lung function in cystic fibrosis: cross sectional and longitudinal analysis from the German CF quality assurance (CFQA) project. Thorax 2002;57:596-601.
    • (2002) Thorax , vol.57 , pp. 596-601
    • Steinkamp, G.1    Wiedemann, B.2
  • 18
    • 0036157692 scopus 로고    scopus 로고
    • Association between genetically determined pancreatic status and lung disease in adult cystic fibrosis patients
    • Loubières Y, Grenet D, Simon-Bouy B, Medioni J, Landais P, Férec C, et al. Association between genetically determined pancreatic status and lung disease in adult cystic fibrosis patients. Chest 2002;121:73-8.
    • (2002) Chest , vol.121 , pp. 73-78
    • Loubières, Y.1    Grenet, D.2    Simon-Bouy, B.3    Medioni, J.4    Landais, P.5    Férec, C.6
  • 19
    • 0032775756 scopus 로고    scopus 로고
    • Effect of elective antibiotic therapy on resting energy expenditure and inflammation in cystic fibrosis
    • Burdet L, Hugli O, Aubert JD, Schutz Y, Roulet M, Fitting JW. Effect of elective antibiotic therapy on resting energy expenditure and inflammation in cystic fibrosis. Eur J Pediatr 1999;158:711-6.
    • (1999) Eur J Pediatr , vol.158 , pp. 711-716
    • Burdet, L.1    Hugli, O.2    Aubert, J.D.3    Schutz, Y.4    Roulet, M.5    Fitting, J.W.6
  • 21
    • 0034759112 scopus 로고    scopus 로고
    • Presence of cystic fibrosis-related diabetes mellitus is tightly linked to poor lung function in patients with cystic fibrosis: Data from the European Epidemiologic Registry of Cystic Fibrosis
    • Koch C, Rainisio M, Madessani U, Harms HK, Hodson ME, Mastella G, et al. Presence of cystic fibrosis-related diabetes mellitus is tightly linked to poor lung function in patients with cystic fibrosis: data from the European Epidemiologic Registry of Cystic Fibrosis. Pediatr Pulmonol 2001;32:343-50.
    • (2001) Pediatr Pulmonol , vol.32 , pp. 343-350
    • Koch, C.1    Rainisio, M.2    Madessani, U.3    Harms, H.K.4    Hodson, M.E.5    Mastella, G.6


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.