Congenital adrenal hyperplasia in adulthood: Do men need to continue treatment?

Hormone Research

Volumn 64, Issue SUPPL. 2, 2005, Pages 71-73

  Mönig, Heiner ^a,b   Sippell, Wolfgang ^a  

^a UNIVERSITY OF KIEL   (Germany)

^b UNIVERSITY HOSPITAL SCHLESWIG HOLSTEIN   (Germany)

Author keywords

Adult male; Congenital adrenal hyperplasia; Continuous treatment

Indexed keywords

CORTICOTROPIN; FLUDROCORTISONE; GLUCOCORTICOID; HYDROCORTISONE; MINERALOCORTICOID;

ADRENAL CORTEX INSUFFICIENCY; ADRENAL INSUFFICIENCY; ADRENAL TUMOR; CLINICAL FEATURE; CONFERENCE PAPER; CONGENITAL ADRENAL HYPERPLASIA; DISEASE COURSE; GONAD FUNCTION; HORMONE DETERMINATION; HORMONE SUBSTITUTION; HUMAN; INCIDENCE; MALE INFERTILITY; PRACTICE GUIDELINE; PRIORITY JOURNAL; RISK FACTOR; SEX DIFFERENCE;

ADRENAL GLAND NEOPLASMS; ADRENAL HYPERPLASIA, CONGENITAL; ADRENAL INSUFFICIENCY; ADULT; CHILD; FLUDROCORTISONE; HUMANS; HYDROCORTISONE; HYPERTROPHY; INFANT; INFERTILITY, MALE; MALE; TESTIS;

EID: 27944458513     PISSN: 03010163     EISSN: None     Source Type: Journal    
DOI: 10.1159/000087758     Document Type: Conference Paper

References (17)

1. White PC, Speiser PW: Congenital adrenal hyperplasia due to 21-hydroxylase deficiency. Endocr Rev 2000;21:245-291.
2. Partsch CJ, Sippell WG, MacKenzie IZ, Aynsley-Green A: The steroid hormonal milieu of the undisturbed human fetus and mother at 16-20 weeks gestation. J Clin Endocrinol Metab 1991;73:969-974.
3. Kovacs J, Votava F, Heinze G, Solyom J, Lebl J, Pribilincova Z, Frisch H, Battelino T, Waldhauser F, Middle European Workshop on Paediatric Endocrinology-Congenital Adrenal Hyperplasia Study Group: Lessons from 30 years of clinical diagnosis and treatment of congenital adrenal hyperplasia in five middle European countries. J Clin Endocrinol Metab 2001;86:2958-2964.
4. Kruse B, Riepe FG, Krone N, Bosinski HA, Kloehn S, Partsch CJ, Sippell WG, Mönig H: Congenital adrenal hyperplasia - how to improve the transition from adolescence to adult life. Exp Clin Endocrinol Diabetes 2004;112:343-355.
5. Clayton PE, Miller WL, Oberfield SE, Ritzén EM, Sippell WG, Speiser PW: Consensus statement on 21-hydroxylase deficiency from the Lawson Wilkins Pediatric Endocrine Society and the European Society for Paediatric Endocrinology. J Clin Endocrinol Metab 2002;87:4048-4053.
6. Clayton PE, Miller WL, Oberfield SE, Ritzén EM, Sippell WG, Speiser PW, ESPE/LWPES CAH Working Group: Consensus Statement on 21-hydroxylase deficiency from the European Society for Paediatric Endocrinology and the Lawson Wilkins Pediatric Endocrine Society. Horm Res 2002;58:188-195.
7. Bonaccorsi AC, Adler I, Figueiredo JG: Male infertility due to congenital adrenal hyperplasia: testicular biopsy findings, hormonal evaluation, and therapeutic results in three patients. Fertil Steril 1987;47:664-670.
8. Stewart J: A fertile male with untreated congenital adrenal hyperplasia. Acta Endocrinol Suppl 1960;51:661.
9. Chrousos GP, Loriaux DL, Sherins RJ, Cutler GB Jr: Unilateral testicular enlargement resulting from inapparent 21-hydroxylase deficiency. J Urol 1981;126:127-128.
10. Stikkelbroeck NM, Otten BJ, Pasic A, Jager GJ, Sweep CG, Noordam K, Hermus AR: High prevalence of testicular adrenal rest tumors, impaired spermatogenesis, and Leydig cell failure in adolescent and adult males with congenital adrenal hyperplasia. J Clin Endocrinol Metab 2001;86:5721-5728.
11. Stikkelbroeck NM, Hermus AR, Suliman HM, Jager GJ, Otten BJ: Asymptomatic testicular adrenal rest tumours in adolescent and adult males with congenital adrenal hyperplasia: Basal and follow-up investigation after 2.6 years. J Pediatr Endocrinol Metab 2004;17:645-653.
12. Rich MA, Keating MA: Leydig cell tumors associated with congenital adrenal hyperplasia. Urol Clin North Am 2000;27:519-528.
13. Cabrera MS, Vogiatzi MG, New MI: Long term outcome in adult males with classic congenital adrenal hyperplasia. J Clin Endocrinol Metab 2001;86:3070-3078.
14. Jaresch S, Kornely E, Kley HK, Schlaghecke R: Adrenal incidentaloma and patients with homozygous or heterozygous congenital adrenal hyperplasia. J Clin Endocrinol Metab 1992;74:685-689.
15. Lightner ES, Levine LS: The adrenal incidentaloma. A pediatric perspective. Am J Dis Child 1993;147:1274-1276.
16. Bornstein SR, Stratakis CA, Chrousos GP: Adrenocortical tumors: recent advances in basic concepts and clinical management. Ann Intern Med 1999;130:759-771.
17. Riepe FG, Krone N, Viemann M, Partsch CJ, Sippell WG: Management of congenital adrenal hyperplasia: results of the ESPE questionnaire. Horm Res 2002;58:196-205.