Klippel-Trenaunay syndrome with small vessel pulmonary arterial hypertension

Thorax

Volumn 60, Issue 11, 2005, Pages 971-973

  Ulrich, S ^a   Fischler, M ^a   Walder, B ^b   Pfammatter, T ^a   Speich, R ^a  

^a UNIVERSITY HOSPITAL ZURICH   (Switzerland)

^b KLINIK HIRSLANDEN   (Switzerland)

Author keywords

[No Author keywords available]

Indexed keywords

ILOPROST; PHENPROCOUMON;

ADULT; ANAMNESIS; ANGIOOSTEOHYPERTROPHY SYNDROME; ARTICLE; CASE REPORT; CLINICAL FEATURE; DRUG TOLERABILITY; HEART HEMODYNAMICS; HUMAN; LABORATORY TEST; LUNG EMBOLISM; MALE; PRIORITY JOURNAL; PULMONARY HYPERTENSION;

HUMANS; HYPERTENSION, PULMONARY; KLIPPEL-TRENAUNAY-WEBER SYNDROME; MALE; MICROCIRCULATION; MIDDLE AGED; PULMONARY EMBOLISM;

EID: 27744513889     PISSN: 00406376     EISSN: None     Source Type: Journal    
DOI: 10.1136/thx.2004.023184     Document Type: Article

References (10)

1. Baskerville PA, Ackroyd JS, Lea TM, et al. The Klippel-Trenaunay syndrome: clinical, radiological and haemodynamic features and management. Br J Surg 1985;72:232-6.
2. Jacob AG, Driscoll DJ, Shaughnessy WJ, et al. Klippel-Trenaunay syndrome: spectrum and management. Mayo Clin Proc 1998;73:28-36.
3. Parkes-Weber F. Haemangiectatic hypertrophy of limbs: congenital phlebarteriectasis and so-called congenital varicose veins. Br J Child Dis 1918;15:13-7.
4. Cohen, MM. Klippel-Trenaunay syndrome: editorial comment. Am J Med Genet 2000;93:171-5.
5. Muluk SC, Ginns LC, Semigran MJ, et al. Klippel-Trenaunay syndrome with multiple pulmonary emboli: an unusual cause of progressive pulmonary dysfunction. J Vasc Surg 1995;21:686-90.
6. Walder B, Kapelanski DP, Auger WR, et al. Successful pulmonary thromboendarterectomy in a patient with Klippel-Trenaunay syndrome. Chest 2000;117:1520-2.
7. Gossage JR, Kanj G. Pulmonary arteriovenous malformations. A state of the art review. Am J Respir Crit Care Med 1998;158:643-61.
8. Eddahibi S, Morrell N, d'Ortho MP, et al. Pathobiology of pulmonary arterial hypertension. Eur Respir J 2002;20:1559-72.
9. Tian XL, Kadaba R, You SA, et al. Identification of an angiogenic factor that when mutated causes susceptibility to Klippel-Trenaunay syndrome. Nature 2004;427:640-5.
10. Chatterjee K, De Marco T, Alpert JS. Pulmonary hypertension: hemodynamic diagnosis and management. Arch Intern Med 2002;162:1925-33.