The metabolism of glycosaminoglycans is impaired in prion diseases

Neurobiology of Disease

Volumn 20, Issue 3, 2005, Pages 738-743

  Mayer Sonnenfeld, Tehila ^a   Zeigler, Marsha ^a   Halimi, Michele ^a   Dayan, Yael ^a   Herzog, Christian ^b   Lasmezas, Corinne I ^b   Gabizon, Ruth ^a  

^a HADASSAH HEBREW UNIVERSITY MEDICAL CENTER   (Israel)

^b INSTITUT DE RADIOPROTECTION ET DE SÛRETÉ NUCLÉAIRE   (France)

Author keywords

Glycosaminoglycans; Metabolism; Prion diseases

Indexed keywords

GLYCOSAMINOGLYCAN; HEPARAN SULFATE;

ANIMAL TISSUE; ARTICLE; CLINICAL ARTICLE; CONTROLLED STUDY; HUMAN; LYSOSOME; LYSOSOME STORAGE DISEASE; METABOLISM; MOUSE; NERVE DEGENERATION; NONHUMAN; PRION DISEASE; PRIORITY JOURNAL; URINALYSIS;

ANIMALS; BRAIN; CREUTZFELDT-JAKOB SYNDROME; CRICETINAE; DISEASE MODELS, ANIMAL; ENZYME ACTIVATION; GLYCOSAMINOGLYCANS; HEXOSAMINIDASES; HUMANS; LYSOSOMES; MALE; MICE; MICE, KNOCKOUT; NEURONS; PRION DISEASES; PRPC PROTEINS; PRPSC PROTEINS; SCRAPIE; SHEEP; UP-REGULATION;

EID: 27744465417     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nbd.2005.05.009     Document Type: Article

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