Unmasked adult-onset urea cycle disorders in the critical care setting

Critical Care Clinics

Volumn 21, Issue 4 SUPPL., 2005, Pages

  Summar, Marshall L ^a,c   Barr, Frederick ^b,c   Dawling, Sheila ^c   Smith, Wendy ^d,e   Lee, Brendan ^f   Singh, Rani H ^g   Rhead, William J ^h   King, Lisa Sniderman ⁱ   Christman, Brian W ^c,g  

^a VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b MONROE CARELL JR CHILDREN S HOSPITAL AT VANDERBILT   (United States)

^c VANDERBILT UNIVERSITY MEDICAL CENTER   (United States)

^d Barbara Bush Children's Hospital   (United States)

^e Maine Pediatric Specialty Group   (United States)

^f BAYLOR COLLEGE OF MEDICINE   (United States)

^g EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

^h MEDICAL COLLEGE OF WISCONSIN   (United States)

ⁱ UNIVERSITY OF WASHINGTON   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMMONIA; ANTICONVULSIVE AGENT; ARGININE; ARYLBUTYRIC ACID DERIVATIVE; BENZOIC ACID; CITRULLINE; INSULIN; NORADRENALIN; ORNITHINE CARBAMOYLTRANSFERASE; PHENYLACETIC ACID DERIVATIVE;

ADULT; AMMONIA BLOOD LEVEL; ANAMNESIS; CASE REPORT; CLINICAL FEATURE; COMA; CONFERENCE PAPER; DISEASE COURSE; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; EPILEPTIC STATE; FEMALE; FOLLOW UP; HEMODIALYSIS; HUMAN; HYPERAMMONEMIA; HYPOTENSION; INTENSIVE CARE; LABORATORY TEST; MALE; METABOLIC DISORDER; PHYSICAL EXAMINATION; PRIORITY JOURNAL; PROTEIN RESTRICTION; UREA CYCLE; UREA CYCLE DISORDER;

ADULT; AGE OF ONSET; BRAIN DISEASES, METABOLIC, INBORN; CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE; CRITICAL ILLNESS; EMERGENCIES; FEMALE; HUMANS; HYPERAMMONEMIA; MALE; MIDDLE AGED; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; PRECIPITATING FACTORS; UREA;

EID: 26844529765     PISSN: 07490704     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ccc.2005.05.002     Document Type: Conference Paper

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