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Volumn 28, Issue 5, 2005, Pages 665-672

A new protein substitute for adolescents and adults with maple syrup urine disease (MSUD)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; ISOLEUCINE; LEUCINE; PROTEIN; PROTEIN DERIVATIVE; TRACE ELEMENT; VALINE;

EID: 25144472161     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-005-0061-6     Document Type: Article
Times cited : (6)

References (10)
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    • 6798541
    • Clow CL, Reade TM, Scriver CR (1981) Outcome of early and long-term management of classical maple syrup urine disease. Pediatrics 68 (6): 856-862. 6798541
    • (1981) Pediatrics , vol.68 , Issue.6 , pp. 856-862
    • Clow, C.L.1    Reade, T.M.2    Scriver, C.R.3
  • 2
    • 25144520104 scopus 로고    scopus 로고
    • Disorders of amino acid metabolism, organic acidaemias and urea cycle defects
    • V Shaw M Lawson eds. 2nd edn. Blackwell Science London
    • M Dixon 2001 Disorders of amino acid metabolism, organic acidaemias and urea cycle defects In: V Shaw M Lawson eds. Clinical Paediatric Dietetics 2nd edn. Blackwell Science London 253-262
    • (2001) Clinical Paediatric Dietetics , pp. 253-262
    • Dixon, M.1
  • 3
    • 0025847951 scopus 로고
    • Intellectual outcome in children with maple syrup urine disease
    • 2066858
    • Kaplan P, Mazur A, Field M (1991) Intellectual outcome in children with maple syrup urine disease. J Pediatr 119 (1 pt 1): 46-50. 2066858
    • (1991) J. Pediatr. , vol.119 , Issue.1 PART 1 , pp. 46-50
    • Kaplan, P.1    Mazur, A.2    Field, M.3
  • 4
    • 2942568160 scopus 로고    scopus 로고
    • A new, low volume protein substitute for teenagers and adults with phenylketonuria
    • 10.1023/B:BOLI.0000028784.11080.9b
    • MacDonald A, Lilburn M, Cochrane B (2004) A new, low volume protein substitute for teenagers and adults with phenylketonuria. J Inherit Metab Dis 27 (2): 127-135. 10.1023/B:BOLI.0000028784.11080.9b
    • (2004) J. Inherit. Metab. Dis. , vol.27 , Issue.2 , pp. 127-135
    • MacDonald, A.1    Lilburn, M.2    Cochrane, B.3
  • 5
    • 0036264313 scopus 로고    scopus 로고
    • Diagnosis and treatment of maple syrup disease: A study of 36 patients
    • 10.1542/peds.109.6.999
    • Morton D, Strauss KA, Robinson DL, Puffenberger EG, Kelley RI (2002) Diagnosis and treatment of maple syrup disease: A study of 36 patients. Pediatrics 109 (6): 1008. 10.1542/peds.109.6.999
    • (2002) Pediatrics , vol.109 , Issue.6 , pp. 100
    • Morton, D.1    Strauss, K.A.2    Robinson, D.L.3    Puffenberger, E.G.4    Kelley, R.I.5
  • 6
    • 15444361371 scopus 로고    scopus 로고
    • Maple syrup urine disease
    • WL Nyhan OT Ozand eds. 1st edn. Chapman and Hall Medical London
    • WL Nyhan OT Ozand 1998 Maple syrup urine disease In: WL Nyhan OT Ozand eds. Atlas of Metabolic Diseases 1st edn. Chapman and Hall Medical London 138-146
    • (1998) Atlas of Metabolic Diseases , pp. 138-146
    • Nyhan, W.L.1    Ozand, O.T.2
  • 7
    • 0012199060 scopus 로고    scopus 로고
    • Branched-chain organic acidurias
    • J Fernandes JM Saudubray G Van den Berghe eds. 3rd revised edn Springer-Verlag Heidelberg
    • H Ogier de Baulny JM Saudubray 2000 Branched-chain organic acidurias In: J Fernandes JM Saudubray G Van den Berghe eds. Inborn Metabolic Diseases: Diagnosis and Treatment 3rd revised edn Springer-Verlag Heidelberg 197-212
    • (2000) Inborn Metabolic Diseases: Diagnosis and Treatment , pp. 197-212
    • Ogier de Baulny, H.1    Saudubray, J.M.2
  • 8
    • 0027533685 scopus 로고
    • Recommendations on the dietary management of phenylketonuria
    • 8466250 Medical Research Council Working Party on Phenylketonuria
    • Smith I, Cockburn F, Brenton DP, et al (1993) Medical Research Council Working Party on Phenylketonuria. Recommendations on the dietary management of phenylketonuria. Arch Dis Child 68: 426-427. 8466250
    • (1993) Arch. Dis. Child. , vol.68 , pp. 426-427
    • Smith, I.1    Cockburn, F.2    Brenton, D.P.3
  • 9
    • 84995046159 scopus 로고
    • Treatment outcome of maple syrup urine disease
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    • Snyderman SE (1988) Treatment outcome of maple syrup urine disease. Acta Paediatr Jpn 30 (4): 417-424. 3150230
    • (1988) Acta Paediatr. Jpn. , vol.30 , Issue.4 , pp. 417-424
    • Snyderman, S.E.1
  • 10
    • 25144443526 scopus 로고    scopus 로고
    • Specialist dietitian-metabolic disease
    • Great Ormond Street Hospital for Children NHS Trust, in SHS Inborn Error Review Series No. 10
    • Van Wyk K (2000) Specialist dietitian-metabolic disease. Maple Syrup Urine Disease - Practical Dietary Management. Great Ormond Street Hospital for Children NHS Trust, in SHS Inborn Error Review Series No. 10
    • (2000) Maple Syrup Urine Disease - Practical Dietary Management
    • Van Wyk, K.1


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.