Effects of chemical chaperones on partially retarded NaCl cotransporter mutants associated with Gitelman's syndrome in a mouse cortical collecting duct cell line

Nephrology Dialysis Transplantation

Volumn 19, Issue 5, 2004, Pages 1069-1076

  de Jong, Joke C ^a   Willems, Peter H G M ^a   Goossens, Monique ^a   Vandewalle, Alain ^b   van den Heuvel, Lambertus P W J ^a   Knoers, Nine V A M ^a   Bindels, René J M ^a  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^b INSERM   (France)

Author keywords

mpk CCD; NCC; Thiazide

Indexed keywords

4 PHENYLBUTYRIC ACID; CHAPERONE; COTRANSPORTER; DIMETHYL SULFOXIDE; GLYCEROL; SODIUM CHLORIDE; THAPSIGARGIN;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CELL LINE; CELL POLARITY; CHLORIDE TRANSPORT; CONTROLLED STUDY; GENE MUTATION; GITELMAN SYNDROME; IMMUNOBLOTTING; IMMUNOHISTOCHEMISTRY; KIDNEY COLLECTING TUBULE; MOLECULAR WEIGHT; MOUSE; NONHUMAN; PRIORITY JOURNAL; SODIUM ABSORPTION; SODIUM TRANSPORT; XENOPUS LAEVIS;

ANIMALS; DISEASE MODELS, ANIMAL; FEMALE; GENETIC VECTORS; HUMANS; KIDNEY DISEASES; MICE; MICE, TRANSGENIC; MOLECULAR CHAPERONES; MUTAGENESIS, SITE-DIRECTED; MUTATION; OOCYTES; RECOMBINANT PROTEINS; SODIUM; SODIUM CHLORIDE SYMPORTERS; SYMPORTERS; SYNDROME; TRANSFECTION; XENOPUS LAEVIS;

EID: 2442598041     PISSN: 09310509     EISSN: None     Source Type: Journal    
DOI: 10.1093/ndt/gfg474     Document Type: Article

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