Severity of Osteogenesis Imperfecta and Structure of a Collagen-like Peptide Modeling a Lethal Mutation Site

Biochemistry

Volumn 43, Issue 18, 2004, Pages 5314-5323

  Radmer, Randall J ^a   Klein, Teri E ^a  

^a STANFORD UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN; COMPUTER SIMULATION; HYDROGEN BONDS; MOLECULAR DYNAMICS; MOLECULAR STRUCTURE;

MUTATIONS; STRUCTURAL DISRUPTION;

BIOCHEMISTRY;

ALANINE; ARGININE; ASPARAGINE; ASPARTIC ACID; COLLAGEN DERIVATIVE; COLLAGEN TYPE 1; GLUTAMIC ACID; GLUTAMINE; HISTIDINE; HYDROXYPROLINE; LEUCINE; LYSINE; METHIONINE; PHENYLALANINE; PROLINE; SERINE; THREONINE; VALINE;

ARTICLE; CORRELATION ANALYSIS; DISEASE SEVERITY; GENE MUTATION; HYDROGEN BOND; MOLECULAR DYNAMICS; OSTEOGENESIS IMPERFECTA; PATHOGENESIS; PHENOTYPE; POINT MUTATION; PRIORITY JOURNAL; PROTEIN FUNCTION; PROTEIN STRUCTURE; SIMULATION; STRUCTURE ANALYSIS; THERMOSTABILITY;

AMINO ACID SEQUENCE; AMINO ACID SUBSTITUTION; COLLAGEN; COLLAGEN TYPE I; COMPUTER SIMULATION; GENES, LETHAL; GLYCINE; HUMANS; HYDROGEN BONDING; HYDROGEN-ION CONCENTRATION; HYDROXYPROLINE; MODELS, MOLECULAR; MOLECULAR SEQUENCE DATA; OSTEOGENESIS IMPERFECTA; PEPTIDES; PREDICTIVE VALUE OF TESTS; PROLINE; SEVERITY OF ILLNESS INDEX;

EID: 2442492118     PISSN: 00062960     EISSN: None     Source Type: Journal    
DOI: 10.1021/bi035676w     Document Type: Article

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