Quantification of glutaric and 3-hydroxyglutaric acids in urine of glutaric acidemia type I patients by HPLC with intramolecular excimer-forming fluorescence derivatization

Clinica Chimica Acta

Volumn 359, Issue 1-2, 2005, Pages 179-188

  Al Dirbashi, Osama Y ^a   Jacob, Minnie ^a   Al Amoudi, Mohammed ^a   Al Kahtani, Khalid ^a   Al Odaib, Ahmed ^a   El Badaoui, Fahad ^a   Rashed, Mohamed S ^a  

^a KING FAISAL SPECIALIST HOSPITAL AND RESEARCH CENTER   (Saudi Arabia)

Author keywords

3 Hydroxyglutaric acid; Excimer forming fluorescence; Glutaric acid; Glutaric aciduria

Indexed keywords

1 PYRENEBUTYRIC HYDRAZIDE; 3 HYDROXYGLUTARIC ACID; CARBON; GLUTARIC ACID; HYDRAZIDE DERIVATIVE; UNCLASSIFIED DRUG;

ANALYTIC METHOD; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; FLUORESCENCE; FLUOROMETRY; GLUTARIC ACIDEMIA TYPE 1; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; INFANT; INFORMATION CENTER; LABORATORY; METHODOLOGY; PRIORITY JOURNAL; PROSPECTIVE STUDY; QUANTITATIVE ANALYSIS; REPRODUCIBILITY; RETROSPECTIVE STUDY; SEPARATION TECHNIQUE; SYMPTOM; URINALYSIS;

CASE-CONTROL STUDIES; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; GLUTARATES; HUMANS; METABOLISM, INBORN ERRORS; REFERENCE STANDARDS; REPRODUCIBILITY OF RESULTS; SENSITIVITY AND SPECIFICITY; SPECTROMETRY, FLUORESCENCE;

EID: 23644433504     PISSN: 00098981     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.cccn.2005.03.048     Document Type: Article

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