Treatment of glycogenosis type V with ketogenic diet [1]

Annals of Neurology

Volumn 58, Issue 2, 2005, Pages 341-

  Busch, Verena ^a   Gempel, Klaus ^b   Hack, Alexandra ^a   Müller, Klaus ^c   Vorgerd, Matthias ^c   Lochmüller, Hanns ^d   Baumeister, Friedrich A M ^a  

^a TECHNICAL UNIVERSITY OF MUNICH   (Germany)

^b Klinikum Schwabing   (Germany)

^c RUHR UNIVERSITY BOCHUM   (Germany)

^d LUDWIG MAXIMILIANS UNIVERSITY   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYL COENZYME A; GLYCOGEN PHOSPHORYLASE; KETONE BODY;

ADULT; CASE REPORT; CITRIC ACID CYCLE; ELECTROMYOGRAPHY; EXERCISE TOLERANCE; FATIGUE; GLYCOGEN STORAGE DISEASE TYPE 5; GLYCOGEN SYNTHESIS; HUMAN; KETOGENIC DIET; LETTER; MALE; MYALGIA; MYOGLOBINURIA; PHOSPHORUS NUCLEAR MAGNETIC RESONANCE; PRIORITY JOURNAL;

EID: 23244460225     PISSN: 03645134     EISSN: None     Source Type: Journal    
DOI: 10.1002/ana.20565     Document Type: Letter

References (5)

1. Quinlivan R, Beynon RJ. Pharmacological and nutritional treatment for McArdle's disease (Glycogen Storage Disease type V). Cochrane Database Syst Rev 2004;3:CD003458.
2. Cahill GF Jr. Starvation in man. N Engl J Med 1970;282: 668-675.
3. Vorgerd M, Zange J, Kley R, et al. Effect of high dose creatine therapy on symptoms of exercise intolerance in McArdle disease: double blind, placebo-controlled crossover study. Arch Neurol 2002;59:97-101.
4. MacLean D, Vissing J, Vissing SF, et al. Oral branched-chain amino acids do not improve exercise capacity in McArdle disease. Neurology 1998;51:1456-1459.
5. Vissing J, Haller RG. The effect of oral sucrose on exercise tolerance in patients with McArdle's disease. N Engl J Med 2003;349:2503-2509.