Genetic disorders of surfactant homeostasis

Biology of the Neonate

Volumn 87, Issue 4, 2005, Pages 283-287

  Whitsett, Jeffrey A ^a,b   Wert, Susan E ^a   Xu, Yan ^a  

^a UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

^b CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

Author keywords

Hereditary lung disease; Lamellar bodies; Pulmonary; Respiratory distress syndrome; Surfactant proteins

Indexed keywords

ABC TRANSPORTER; ABC TRANSPORTER A3; ADENOSINE TRIPHOSPHATE; LIPID; LUNG SURFACTANT; MUTANT PROTEIN; PHOSPHOLIPID DERIVATIVE; SURFACTANT PROTEIN B; SURFACTANT PROTEIN C; THYROID TRANSCRIPTION FACTOR 1; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG;

ACUTE DISEASE; ADAPTATION; BREATHING; CHRONIC LUNG DISEASE; CONFERENCE PAPER; GENETIC DISORDER; GENETIC TRANSCRIPTION; HOMEOSTASIS; HUMAN; HYDROPHOBICITY; LAMELLAR BODY; LIPOGENESIS; LUNG ALVEOLUS; LUNG ALVEOLUS EPITHELIUM; LUNG BLOOD FLOW; LUNG INTERSTITIUM; MUTATION; NEONATAL RESPIRATORY DISTRESS SYNDROME; NEWBORN DISEASE; PREGNANCY; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FAMILY; PROTEIN FUNCTION; PROTEIN SYNTHESIS; PROTEIN SYNTHESIS REGULATION; REGULATORY MECHANISM; RESPIRATORY EPITHELIUM; SECRETION; SURFACE TENSION; THIRD TRIMESTER PREGNANCY; TISSUE DIFFERENTIATION;

ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; DNA-BINDING PROTEINS; GENE EXPRESSION REGULATION; HEPATOCYTE NUCLEAR FACTOR 3-BETA; HUMANS; INFANT, NEWBORN; MICE; MUTATION; NUCLEAR PROTEINS; PEPTIDES; PULMONARY SURFACTANT-ASSOCIATED PROTEIN B; PULMONARY SURFACTANT-ASSOCIATED PROTEIN C; RESPIRATORY DISTRESS SYNDROME, NEWBORN; TRANSCRIPTION FACTORS;

VERTEBRATA;

EID: 23244452988     PISSN: 00063126     EISSN: None     Source Type: Journal    
DOI: 10.1159/000084875     Document Type: Conference Paper

References (21)

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