Current treatment and prognosis in children with functionally univentricular hearts

Archives of Disease in Childhood

Volumn 90, Issue 7, 2005, Pages 757-762

  Kaulitz, R ^a   Hofbeck, M ^a  

^a UNIVERSITY HOSPITAL TÜBINGEN   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ANASTOMOSIS; CARDIOPULMONARY INSUFFICIENCY; COGNITIVE DEFECT; CONGENITAL HEART MALFORMATION; CYANOSIS; FOLLOW UP; FONTAN PROCEDURE; HEART ARRHYTHMIA; HEART SINGLE VENTRICLE; HEART TRANSPLANTATION; HEMODYNAMICS; HUMAN; LIVER DYSFUNCTION; PATIENT SELECTION; PRIORITY JOURNAL; PROGNOSIS; PROTEIN LOSING GASTROENTEROPATHY; REVIEW; SURGICAL TECHNIQUE; THROMBOEMBOLISM;

FONTAN PROCEDURE; HEART BYPASS, RIGHT; HEART DEFECTS, CONGENITAL; HEART VENTRICLES; HUMANS; INFANT, NEWBORN; PROGNOSIS; TREATMENT OUTCOME;

EID: 21544471269     PISSN: 00039888     EISSN: 14682044     Source Type: Journal    
DOI: 10.1136/adc.2003.034090     Document Type: Review

References (58)

1. Driscoll DJ, Offord K, Feldt R, et al. Five- to fifteen-year follow-up after Fontan operation. Circulation 1992;85:469-96.
2. Azakie A, Merklinger SL, Williams WG, et al. Improving outcomes of the Fontan operation in children with atrial isomerism and heterotaxy syndromes. Ann Thorac Surg 2001;72:1636-40.
3. Stamm C, Friehs I, Duebener LF, et al. Improving results of the modified Fontan operation in patients with heterotaxy syndrome. Ann Thorac Surg 2002;74:1967-77.
4. Jonas RA, Lang P, Hansen D, et al. First stage palliation of hypoplastic left heart syndrome: the importance of coarctation and shunt size. J Thorac Cardiovasc Surg 1986;92:6-13.
5. Sono S, Kawada M, Yoshida H, et al. Norwood procedure in hypoplastic left heart syndrome. Jpn J Thorac Cardiovasc Surg 1998;46:1311-16.
6. Fontan F, Kirklin KW, Fernandez G, et al. Outcome after a "perfect" Fontan operation. Circulation 1990;81:1520-36.
7. Maitiau A, Geva T, Colon SD, et al. Bulboventricular foramen size in infants with double inlet left ventricle or tricuspid atresia with transposed great arteries. J Am Coll Cordial 1992;19:142-8.
8. Norwood WI, Jacobs ML. Fontan's operation in two stages. Am J Surg 1993;166:548-51.
9. Jacobs ML, Rychik J, Rome JJ, et al. Early reduction of the volume work of the single ventricle: the hemi-Fontan operation. Ann Thorac Surg 1996;62:456-61.
10. Fontan F, Baudet E. Surgical repair of tricuspid atresia. Thorax 1971;26:240-8.
11. Björk VO, Olin CL, Bjarke BB, et al. Right atrial-right ventricular anastomosis for correction of tricuspid atresia. J Thorac Cardiovasc Surg 1979;77:452-8.
12. Kreutzer G, Galindez E, Bono H, et al. An operation for the correction of tricuspid atresia. J Thorac Cardiovasc Surg 1973;66:613-21.
13. DeLevol MR, Kliner P, Gewillig M, et al. Total cavopulmonary connection: a logical alternative to atriopulmonary connection for complex Fontan operations. J Thoracic Cardiovasc Surg 1988;96:682-95.
14. Jonas RA, Castaneda AR. Modified Fontan procedure: atrial baffle and systemic venous to pulmonary artery anastomotic techniques. J Cardiac Surg 1988;3:91-6.
15. Stamm G, Friehs I, Mayer JE, et al. Long-term results of the lateral tunnel Fontan operation. J Thorac Cardiovasc Surg 2001;121:28-41.
16. Gentles TL, Mayer JE, Gavreau K, et al. Fontan operation in five hundred consecutive patients: factors influencing early and late outcome. J Thorac Cardiovasc Surg 1997;114:376-91.
17. Hoshimota K, Kurosawa H, Tanaka K, et al. Total cavopulmonary connection without the use of prosthetic material: technical considerations and hemodynamic consequences. J Thorac CaroWasc Surg 1995;110:625-32.
18. Choussat P, Fontan F, Besso P, et al. Selection criteria for Fontan's operation. In: Andersen R, Shineborne E, eds. Pediatric cardiology. New York: Churchill-Livingstone, 1977:559-60.
19. Bridges ND, Mayer JE, Lock JE, et al. Effect of baffle fenestration on outcome of the modified Fontan operation. Circulation 1992;86:1762-9.
20. Sommer RJ, Recto M, Golinko R, et al. Transcatheter coil occlusion of surgical fenestration after Fontan operation. Circulation 1996;94:249-52.
21. Lloyd TR, Rydberg A, Ludomirsky A, et al. Late fenestration closure in the hypoplastic left heart syndrome: comparison of hemodynamic changes. Am Heart J 1998;136:302-6.
22. Kopf GS, Kleinman CS, Hijazi ZM, et al. Fenestrated Fontan operation with delayed transcatheter closure of atrial septal defect. J Thorac Cardiovasc Surg 1992;103:1039-48.
23. Woods RK, Dyamenahalli U, Duncan BW, et al. Comparison of extracardiac Fontan techniques: pedicled pericardial tunnel versus conduit reconstruction. J Thorac Cardiovasc Surg 2003;125:465-71.
24. Azakie A, McCrindle BW, Van Arsdell G, et al. Extracardiac conduit versus lateral tunnel cavopulmonary connections at a single institution: impact on outcomes. J Thorac Cardiovasc Surg 2001;122:1219-28.
25. Shirai LK, Rosenthal DN, Reitz BA, et al. Arrhythmias and thromboembolic complications after the extracardiac Fontan operation. J Thorac Cardiovasc Surg 1998;115:499-505.
26. Vouhe PR. Fontan completion: intracardiac tunnel or extracardiac conduit? Thorac Cardiovasc Surg 2001;49:27-9.
27. Kawashima Y, Kitamura S, Matsuda H, et al. Total cavopulmonary shunt operation in complex cardiac anomalies: a new operation. J Thorac Cardiovasc Surg 1984;87:74-81.
28. Srivastava D, Preminger T, Lock JE, et al. Hepatic venous blood and the development of pulmonary arteriovenous malformations in congenital heart disease. Circulation 1995;92:1217-22.
29. Cohen Ml, Wernovsky G, Vetter VL, et al. Sinus node function after a systematically staged Fontan procedure. Circulation 1998;98(suppl II):352-8.
30. Fishberger SB, Wernovsky G, Gentles T, et al. Factors that influence the development of atrial flutter after the Fontan operation. J Thorac Cardiovasc Surg 1997;113:80-6.
31. Manning PB, Mayer JE, Wernovsky G, et al. Staged operation to Fontan increases the incidence of sinoatrial node dysfunction. J Thorac Cardiovasc Surg 1996;111:833-40.
32. Durongpisikul K, Porter C, Cetta F, et al. Predictors of early- and late-onset supraventricular tachyarrhythmias after Fontan operation. Circulation 1998;98:1099-1107.
33. Balling G, Vogt M, Kaemmerer H, et al. Intracardiac thrombus formation after the Fontan operation. J Thoarc Cardiovasc Surg 2000;119:745-52.
34. Fyfe DA, Kline CH, Sade RM, et al. Transesophageal echocardiography detects thrombus formation not identified by transthoracic echocardiography after the Fontan operation. S Am Coll Cardiol 1991;18:1733-7.
35. Rauch R, Ries M, Hofbeck M, et al. Hemostatic changes following the modified Fontan operation (total cavopulmonary connection). Thromh Haemost 2000;83:678-82.
36. Kaulitz R, Luhmer I, Bergmann F, et al. Sequelae after modified Fontan operation: postoperative haemodynamics and organ function. Heart 1997;58:154-9.
37. Odegaard C, McGowan FX, Zurakowski D, et al. Procoagulant and anticoagulant factor abnormalities following the Fontan procedure: increased factor VIII may predispose to thrombosis. J Thorac Cordiovasc Surg 2003;125:1260-7.
38. Jahangiri M, Shore D, Kakkar V, et al. Coagulation factor abnormalities after the Fontan procedure and its modifications. J Thorac Cardiovasc Surg 1997;113:989-92.
39. Coon PD, Rychik J, Novella RT, et al. Thrombus formation after the Fontan operation. Ann Thorac Surg 2001;71:1990-4.
40. Feldt RH, Driscoll DJ, Offord KP, et al. Protein-losing enteropathy after the Fontan operation. J Thorac Cardiovasc Surg 1996;112:672-80.
41. Mertens L, Hagler DJ, Sauer U, et al. Protein-losing enteropathy after the Fontan operation: an international multicenter study. J Thorac Cardiovasc Surg 1998;115:1063-73.
42. Chakrabarti S, Keeton BR, Salmon AP, et al. Acquired combined immunodeficiency associated with protein losing enteropathy complicating Fonton operation. Heart 2003;89:1130-1.
43. Freedom RM, Hamilton R, Yoo S, et al. The Fontan procedure: analysis of cohorts and late complications. Cardiol Young 2000;10:307-31.
44. Narkewicz M, Sondheimer HM, Ziegler JW, et al. Hepatic dysfunction following the Fontan procedure. J Pediatr Gastroenterol Nutr 2003;36:352-7.
45. Gatzoulis MA, Shinebourne EA, Redington AN, et al. Increasing cyanosis early after cavopulmonary connection caused by abnormal systemic venous channels. Br Heart J 1995;73:182-6.
46. McElhinney DB, Reddy M, Tworetzky W, et al. Incidence and implications of systemic to pulmonary collaterals after bidirectional cavopulmonary anastomosis. Ann Thorac Surg 2000;69:1222-8.
47. Stumper O, Wright JGC, Sadiq M, et al. Late systemic desaturation after total cavopulmonary shunt operations. Br Heart J 1995;74:282-6.
48. Kaulitz R, Ziemer G, Paul Th, et al. Fontan-type procedures: residual lesions and late interventions. Ann Thorac Surg 2002;74:778-85.
49. Shah MJ, Rychik J, Fogel MA, et al. Pulmonary AV malformations after superior cavopulmonary connection: resolution after inclusion of hepatic veins in the pulmonary circulation. Ann Thorac Surg 1997;63:960-3.
50. Lamour JM, Hsu DT, Kichuk MR, et al. Regression of pulmonary arteriovenous malformations following heart transplantation. Pediatr Transpl 2000;4:280-4.
51. Knight WB, Mee RBB. A cure for pulmonary arteriovenous fistulas? Ann Thorac Surg 1995;59:999-1001.
52. Fredriksen PM, Therrien J, Veldtman G, et al. Lung function and aerobic capacity in adult patients following modified Fontan procedure. Heart 2001;85:295-9.
53. Durongpisikul K, Driscoll DJ, Mahoney DW, et al. Cardiorespiratory response to exercise after modified Fontan operation: determinants of performance. J Am Coll Cordiol 1997;29:785-90.
54. Goldberg CS, Schwarte EM, Brunberg JA, et al. Neurodevelopmental outcome of patients after the Fontan operation: a comparison between children with hypoplastic left heart syndrome and other functional single ventricle lesions. J Pediatr 2000;137:646-52.
55. Wernosky G, Stiles KM, Gauvreau K, et al. Cognitive development after the Fontan operation. Circulation 2000;102:883-9.
56. Mahle WT, Clancy RR, Moss EM, et al. Neurodevelopmental outcome and lifestyle assessment in school-aged and adolescent children with hypoplastic left heart syndrome. Pediatrics 2000;105:1082-9.
57. Michielon G, Parisi F, Squitieri C, et al. Orthotopic heart transplantation for congenital heart disease: an alternative for high-risk Fontan candidates? Circulation 2003;108(suppl I):II140-9.
58. Knott-Craig CJ, Danielson GK, Schaff HV, et al. The modified Fontan operation. J Thorac Cardiovosc Surg 1995;109:1237-43.