메뉴 건너뛰기




Volumn 171, Issue 9, 2005, Pages 1015-1019

Potential difference measurements in the lower airway of children with and without cystic fibrosis

Author keywords

Cystic fibrosis; Ion transport; Potential difference

Indexed keywords

CHLORIDE; ISOPRENALINE; TRANSMEMBRANE CONDUCTANCE REGULATOR;

EID: 20944434002     PISSN: 1073449X     EISSN: None     Source Type: Journal    
DOI: 10.1164/rccm.200408-1116OC     Document Type: Article
Times cited : (33)

References (20)
  • 1
    • 0027162649 scopus 로고
    • Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis
    • Welsh MJ, Smith AE. Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis. Cell 1993;73:1251-1254.
    • (1993) Cell , vol.73 , pp. 1251-1254
    • Welsh, M.J.1    Smith, A.E.2
  • 2
    • 0032433707 scopus 로고    scopus 로고
    • Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
    • Matsui H, Grubb BR, Tarran R, Randell SH, Gatzy JT, Davis CW, Boucher RC. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell 1998;95:1005-1015.
    • (1998) Cell , vol.95 , pp. 1005-1015
    • Matsui, H.1    Grubb, B.R.2    Tarran, R.3    Randell, S.H.4    Gatzy, J.T.5    Davis, C.W.6    Boucher, R.C.7
  • 3
    • 0029010510 scopus 로고
    • Lower respiratory infection and inflammation in infants with newly diagnosed cystic fibrosis
    • Armstrong DS, Grimwood K, Carzino R, Carlin JB, Olinsky A, Phelan PD. Lower respiratory infection and inflammation in infants with newly diagnosed cystic fibrosis. BMJ 1995;310:1571-1572.
    • (1995) BMJ , vol.310 , pp. 1571-1572
    • Armstrong, D.S.1    Grimwood, K.2    Carzino, R.3    Carlin, J.B.4    Olinsky, A.5    Phelan, P.D.6
  • 4
    • 0004240703 scopus 로고
    • CF Foundation. Bethesda, MD: CF Foundation
    • CF Foundation. Patient Registry 1994 Annual Data Report, CF Foundation. Bethesda, MD: CF Foundation; 1995.
    • (1995) Patient Registry 1994 Annual Data Report
  • 6
    • 0034914515 scopus 로고    scopus 로고
    • Therapeutic strategies to correct malfunction of CFTR
    • Lim M, Zeitlin PL. Therapeutic strategies to correct malfunction of CFTR. Paediatr Respir Rev 2001;2:159-164.
    • (2001) Paediatr Respir Rev , vol.2 , pp. 159-164
    • Lim, M.1    Zeitlin, P.L.2
  • 7
    • 0019809960 scopus 로고
    • Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis
    • Knowles M, Gatzy J, Boucher R. Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis. N Engl J Med 1981;305:1489-1495.
    • (1981) N Engl J Med , vol.305 , pp. 1489-1495
    • Knowles, M.1    Gatzy, J.2    Boucher, R.3
  • 8
    • 0028020058 scopus 로고
    • Protocols for in vivo measurement of the ion transport defects in cystic fibrosis nasal epithelium
    • Middleton PG, Geddes DM, Alton EWFW. Protocols for in vivo measurement of the ion transport defects in cystic fibrosis nasal epithelium. Eur Respir J 1994;7:2050-2056.
    • (1994) Eur Respir J , vol.7 , pp. 2050-2056
    • Middleton, P.G.1    Geddes, D.M.2    Alton, E.W.F.W.3
  • 10
    • 0030956949 scopus 로고    scopus 로고
    • Nasal potential difference in cystic fibrosis patients presenting borderline sweat test
    • Delmarco A, Pradal U, Cabrini G, Bonizzato A, Mastella G. Nasal potential difference in cystic fibrosis patients presenting borderline sweat test. Eur Respir J 1997;10:1145-1149.
    • (1997) Eur Respir J , vol.10 , pp. 1145-1149
    • Delmarco, A.1    Pradal, U.2    Cabrini, G.3    Bonizzato, A.4    Mastella, G.5
  • 12
    • 0034073736 scopus 로고    scopus 로고
    • A pilot study of the effect of gentamicin on nasal potential difference measurements in cystic fibrosis patients carrying stop mutations
    • Wilschanski M, Famini C, Blau H, Rivlin J, Augarten A, Avital A, Kerem B, Kerem E. A pilot study of the effect of gentamicin on nasal potential difference measurements in cystic fibrosis patients carrying stop mutations. Am J Respir Crit Care Med 2000;161:860-865.
    • (2000) Am J Respir Crit Care Med , vol.161 , pp. 860-865
    • Wilschanski, M.1    Famini, C.2    Blau, H.3    Rivlin, J.4    Augarten, A.5    Avital, A.6    Kerem, B.7    Kerem, E.8
  • 13
    • 0031889082 scopus 로고    scopus 로고
    • A pilot clinical trial of oral sodium 4-phenylbutyrate (Buphenyl) in deltaF508-homozygous cystic fibrosis patients: Partial restoration of nasal epithelial CFTR function
    • Rubenstein RC, Zeitlin PL. A pilot clinical trial of oral sodium 4-phenylbutyrate (Buphenyl) in deltaF508-homozygous cystic fibrosis patients: partial restoration of nasal epithelial CFTR function. Am J Respir Crit Care Med 1998;157:484-490.
    • (1998) Am J Respir Crit Care Med , vol.157 , pp. 484-490
    • Rubenstein, R.C.1    Zeitlin, P.L.2
  • 14
    • 0033586375 scopus 로고    scopus 로고
    • Cationic lipid-mediated CFTR gene transfer to the lungs and nose of patients with cystic fibrosis: A double-blind placebo-controlled trial
    • Alton EW, Stern M, Parley R, Jaffe A, Chadwick SL, Phillips J, Davies J, Smith SN, Browning J, Davies MG, et al. Cationic lipid-mediated CFTR gene transfer to the lungs and nose of patients with cystic fibrosis: a double-blind placebo-controlled trial. Lancet 1999;353:947-954.
    • (1999) Lancet , vol.353 , pp. 947-954
    • Alton, E.W.1    Stern, M.2    Parley, R.3    Jaffe, A.4    Chadwick, S.L.5    Phillips, J.6    Davies, J.7    Smith, S.N.8    Browning, J.9    Davies, M.G.10
  • 19
    • 0028912888 scopus 로고
    • Normalization of raised sodium absorption and raised calcium-mediated chloride secretion by adenovirus-mediated expression of cystic fibrosis transmembrane conductance regulator in primary human cystic fibrosis airway epithelial cells
    • Johnson LG, Boyles SE, Wilson J, Boucher RC. Normalization of raised sodium absorption and raised calcium-mediated chloride secretion by adenovirus-mediated expression of cystic fibrosis transmembrane conductance regulator in primary human cystic fibrosis airway epithelial cells. J Clin Invest 1995;95:1377-1382.
    • (1995) J Clin Invest , vol.95 , pp. 1377-1382
    • Johnson, L.G.1    Boyles, S.E.2    Wilson, J.3    Boucher, R.C.4
  • 20
    • 0042024949 scopus 로고    scopus 로고
    • Research applications of bronchoscopy
    • Davies J, Payne D. Research applications of bronchoscopy. Paediatr Respir Rev 2003;4:230-236.
    • (2003) Paediatr Respir Rev , vol.4 , pp. 230-236
    • Davies, J.1    Payne, D.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.