Hemolytic crisis with fulminant hepatic failure in Wilson disease without consanguinity

Pediatrics International

Volumn 46, Issue 6, 2004, Pages 726-729

  Kitazawa, Junichi ^a,g   Kaizuka, Michiko ^a   Kasai, Mikio ^a   Noda, Yasuko ^a   Takahashi, Yoshihiro ^b   Terui, Kiminori ^b   Narumi, Shunji ^b   Hakamada, Kenichi ^b   Sasaki, Mutsuo ^b   Kamata, Yoshimasa ^b   Endo, Tetsuya ^c   Nomachi, Shosuke ^d   Saikai, Toyohiro ^e   Mizoguchi, Yoshikazu ^f   Kinebuchi, Miyuki ^f   Ito, Etsuro ^b   Matsuura, Akihiro ^f  

^a National Hospital Organization   (Japan)

^b HIROSAKI UNIVERSITY   (Japan)

^c HEALTH SCIENCES UNIVERSITY OF HOKKAIDO   (Japan)

^d Sapporo City Institute of Public Health   (Japan)

^e SAPPORO MEDICAL UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^f FUJITA HEALTH UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^g Hirosaki City Hospital   (Japan)

Author keywords

Hemolytic crisis; Iron metabolism; Liver transplantation; R778L and A874V mutations in ATP7B; Wilsonian fulminant hepatitis

Indexed keywords

ACUTE CHOLECYSTITIS; ADOLESCENT; ARTICLE; CASE REPORT; CLINICAL FEATURE; CONSANGUINITY; DISEASE COURSE; DISSEMINATED INTRAVASCULAR CLOTTING; FEMALE; HEMOLYSIS; HUMAN; LABORATORY TEST; LIVER CIRRHOSIS; LIVER DYSFUNCTION; LIVER FAILURE; LIVER TRANSPLANTATION; PRIORITY JOURNAL; WILSON DISEASE; WILSONIAN FULMINANT HEPATITIS;

ADOLESCENT; ANEMIA, HEMOLYTIC; CONSANGUINITY; FEMALE; FOLLOW-UP STUDIES; HEPATIC ENCEPHALOPATHY; HEPATOLENTICULAR DEGENERATION; HUMANS; JAPAN; LIVER FAILURE, ACUTE; LIVER TRANSPLANTATION; LIVING DONORS; RISK ASSESSMENT; TREATMENT OUTCOME;

EID: 19944428316     PISSN: 13288067     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1442-200x.2004.01993.x     Document Type: Article

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