Swallowing dysfunction in 101 patients with nephropathic cystinosis: Benefit of long-term cysteamine therapy

Medicine

Volumn 84, Issue 3, 2005, Pages 137-146

  Sonies, Barbara C ^a   Almajid, Phaedra ^a   Kleta, Robert ^a   Bernardini, Isa ^a   Gahl, William A ^a,b  

^a NATIONAL INSTITUTES OF HEALTH   (United States)

^b NATIONAL HUMAN GENOME RESEARCH INSTITUTE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MERCAPTAMINE;

ADOLESCENT; ADULT; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CHILD; CONTROLLED STUDY; DISEASE SEVERITY; DYSPHAGIA; ECHOGRAPHY; ESOPHAGUS; FACE MUSCLE; FEMALE; FLUOROSCOPY; HUMAN; LIP; LYSOSOME STORAGE DISEASE; MAJOR CLINICAL STUDY; MALE; MOUTH; MUSCLE ATROPHY; NEPHROPATHIC CYSTINOSIS; PATIENT COMPLIANCE; PHARYNX; PRIORITY JOURNAL; TONGUE; VOCALIZATION;

ADOLESCENT; ADULT; AGE FACTORS; CHILD; CYSTEAMINE; CYSTINOSIS; DEGLUTITION DISORDERS; FEMALE; GLYCOPROTEINS; HUMANS; MALE; MEMBRANE PROTEINS; MEMBRANE TRANSPORT PROTEINS; MIDDLE AGED; MUTATION; SEVERITY OF ILLNESS INDEX;

EID: 18744364173     PISSN: 00257974     EISSN: None     Source Type: Journal    
DOI: 10.1097/01.md.0000164204.00159.d4     Document Type: Article

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