Biliary atresia associated with a fatty acid oxidation defect

Journal of Pediatric Gastroenterology and Nutrition

Volumn 35, Issue 5, 2002, Pages 624-628

  Matthews, Randolph P ^a   Russo, Pierre ^b   Berry, Gerard T ^c   Piccoli, David A ^a   Rand, Elizabeth B ^a  

^a Fred/Suzanne Biesecker Liver Ctr   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c CHILDREN'S NATIONAL MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ARTICLE; BILE DUCT ATRESIA; BILE DUCT OBSTRUCTION; CASE REPORT; DISEASE ASSOCIATION; FATTY ACID OXIDATION; FEMALE; GENE MUTATION; HUMAN; INTRAHEPATIC CHOLESTASIS; LIVER BIOPSY; LIVER TRANSPLANTATION; PORTOENTEROSTOMY; PRESCHOOL CHILD; PRIORITY JOURNAL; SYMPTOMATOLOGY; ENZYMOLOGY; INFANT; LIVER; LIVER CIRRHOSIS; MALE; METABOLISM; NEWBORN; OXIDATION REDUCTION REACTION; PATHOLOGY;

3 HYDROXYACYL COENZYME A DEHYDROGENASE; FATTY ACID;

3-HYDROXYACYL COA DEHYDROGENASES; BILIARY ATRESIA; FATTY ACIDS; HUMANS; INFANT; INFANT, NEWBORN; LIVER; LIVER CIRRHOSIS; LIVER TRANSPLANTATION; MALE; OXIDATION-REDUCTION; PORTOENTEROSTOMY, HEPATIC;

EID: 1842843281     PISSN: 02772116     EISSN: None     Source Type: Journal    
DOI: 10.1097/00005176-200211000-00007     Document Type: Article

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