Formation of the enzyme complex in mitochondria is required for function of trifunctional β-oxidation protein

Biochemical and Biophysical Research Communications

Volumn 219, Issue 3, 1996, Pages 773-777

  Orii, Kenji E ^a,b   Aoyama, Toshifumi ^b   Souri, Masayoshi ^b   Jiang, Ling Ling ^b   Orii, Koji O ^a,b   Hayashi, Shuhei ^c   Yamaguchi, Seiji ^d   Kondo, Naomi ^a   Orii, Tadao ^a,e   Hashimoto, Takashi ^b  

^a GIFU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b SHINSHU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^c FUKUI PREFECTURAL HOSPITAL   (Japan)

^d SHIMANE UNIVERSITY   (Japan)

^e Chubu Women's College   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

CELL PROTEIN; MULTIENZYME COMPLEX;

ARTICLE; CASE REPORT; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; HUMAN; HUMAN CELL; MALE; MITOCHONDRION; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN STABILITY; PROTEIN SYNTHESIS; PROTEIN TRANSPORT;

EID: 17044446991     PISSN: 0006291X     EISSN: None     Source Type: Journal    
DOI: 10.1006/bbrc.1996.0309     Document Type: Article

References (12)

1. Uchida, Y., Izai, K., Orii, T., and Hashimoto, T. (1992) J. Biol. Chem. 267, 1034-1041.
2. Carpenter, K., Pollitt, R. J., and Middleton, B. (1992) Biochem. Biophys. Res. Commun. 183, 443-448.
3. Kamijo, T., Aoyama, T., Miyazaki, J., and Hashimoto, T. (1993) J. Biol. Chem. 268, 26452-26460.
4. Wanders, R. J. A., Duran, M., IJlst, L., de Jager, J. P., van Gennip, A. H., Jakobs, C., Dorland, L., and van Sprang, F. J. (1989) Lancet ii, 52-53.
5. Kamijo, T., Wanders, R. J. A., Saudubray, J. M., Aoyama, T., Komiyama, A., and Hashimoto, T. (1994) J. Clin. Invest. 93, 1740-1747.
6. Jackson, S., Singh Kler, R., Bartlett, K., Briggs, A., Bindoff, K. A., Pourfarzam, M., Gardner-Medwin, D., and Turnbull, D. M. (1992) J. Clin. Invest. 90, 1219-1225.
7. Wanders, R. J. A., IJlst, L., Poggi, F., Bonnefont, J. P., Munnich, A., Brivet, M., Rabier, D., and Saudubray, J. M. (1992) Biochem. Biophys. Res. Commun. 188, 1139-1145.
8. IJlst, L., Wanders, R. L. A., Ushikubo, S., Kamijo, T., and Hashimoto, T. (1994) Biochim. Biophys. Acta 1215, 347-350.
9. Osumi, T., and Hashimoto, T. (1979) Biochim. Biophys. Acta 574, 258-267.
10. Furuta, S., Miyazawa, S., Osumi, T., Hashimoto, T., and Ui, N. (1980) J. Biochem. 88, 1059-1070.
11. Aoyama, T., Souri, M., Ushikubo, S., Kamijo, T., Yamaguchi, S., Kelly, R. I., Rhead, W. J., Uetake, K., Tanaka, K., and Hashimoto, T. (1995) J. Clin. Invest. 95, 2465-2473.
12. Aoyama, T., Ueno, I., Kamijo, T., and Hashimoto, T. (1994) J. Biol. Chem. 269, 19088-19094.